A Study of Etavopivat in Patients With Thalassemia or Sickle Cell Disease

NCT ID: NCT04987489

Last Updated: 2025-12-16

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

53 participants

Study Classification

INTERVENTIONAL

Study Start Date

2022-03-28

Study Completion Date

2025-09-24

Brief Summary

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This clinical trial is a Phase 2 study that will evaluate the safety and clinical activity of etavopivat in patients with thalassemia or sickle cell disease and test how well etavopivat works to lower the number of red blood cell transfusions required and increase hemoglobin.

Detailed Description

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Etavopivat is a potent, selective, orally bioavailable, small-molecule activator of pyruvate kinase red blood cell (PKR) being developed by Forma Therapeutics, Inc and is intended for use as a treatment for patients with sickle cell disease (SCD) or other inherited hemoglobinopathies or refractory anemias. This study is a multicenter, Phase 2, open-label, multiple-cohort study examining the safety and efficacy of etavopivat for the treatment of patients, age 12 to 65 years, with SCD or thalassemia. Three treatment cohorts based on the patients hemoglobinopathy (SCD or thalassemia) and transfusion requirements will be evaluated.

Conditions

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Sickle Cell Disease Thalassemia

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Etavopivat 400 mg daily - SCD with transfusions

Patients with sickle cell disease on chronic red blood cell transfusions

Group Type EXPERIMENTAL

Etavopivat tablets

Intervention Type DRUG

Etavopivat 400 mg once daily

Etavopivat 400 mg daily - Thalassemia with transfusions

Patients with thalassemia on chronic red blood cell transfusions

Group Type EXPERIMENTAL

Etavopivat tablets

Intervention Type DRUG

Etavopivat 400 mg once daily

Etavopivat 400 mg daily - Thalassemia

Patients with thalassemia not on chronic red blood cell transfusions

Group Type EXPERIMENTAL

Etavopivat tablets

Intervention Type DRUG

Etavopivat 400 mg once daily

Interventions

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Etavopivat tablets

Etavopivat 400 mg once daily

Intervention Type DRUG

Other Intervention Names

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FT-4202

Eligibility Criteria

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Inclusion Criteria

* Provision of consent
* Female patients of childbearing potential must use acceptable methods of contraception, male patients are willing to use barrier methods of contraception

Cohort A (Sickle Cell Disease Transfusion Cohort)

* Confirmed diagnosis of sickle cell disease
* Chronically red blood cell transfused (sample or exchange \[manual or via electrophoresis\]) for primary stroke prevention or due to previous stroke. Chronic red blood cell transfusion is defined as: ≥ 6 red blood cell units in the previous 24 weeks before the first dose of study treatment and no transfusion-free period for \> 35 days during that period
* At least 24 months of chronic monthly red blood cell transfusions for secondary stroke prevention/treatment of primary stroke (initial completed overt clinical stroke with documented infarction on brain computed tomography \[CT\] or magnetic resonance imaging \[MRI\])
* Prior to screening OR at least 12 months of chronic RBC transfusions for primary stroke prevention (abnormal TCD) prior to screening
* Documented adequate monthly transfusions with average HbS ≤ 45% (the upper limit of the established academic community standard) for the previous 12 weeks of red blood cell transfusions before the first dose of study treatment

Cohort B (Thalassemia Transfusion Cohort)

* Documented diagnosis of β-thalassemia, Hemoglobin E/ β-thalassemia or Hemoglobin H (α-thalassemia), or other thalassemia variant
* Chronically transfused, defined as: ≥ 6 red blood cell units in the previous 24 weeks before the first dose of study treatment and no transfusion-free period for \> 35 days during that period

Cohort C (Thalassemia Non-transfused Cohort)

* Documented diagnosis of β-thalassemia, Hemoglobin E/ β-thalassemia or Hemoglobin H (α-thalassemia), or other thalassemia variant
* Hemoglobin ≤ 10 g/dL

Exclusion Criteria

* Female who is breast feeding or pregnant
* Hepatic dysfunction characterized by:

* Alanine aminotransferase (ALT) \> 4.0 × upper limit of normal (ULN)
* Direct bilirubin \> 3.0 × ULN
* History of cirrhosis
* Known human immunodeficiency virus (HIV) positivity
* Active hepatitis B or hepatitis C infection
* Severe renal dysfunction or on chronic dialysis
* History of malignancy within the past 2 years prior to treatment Day 1 requiring systemic chemotherapy and/or radiation.

* Patients with malignancy considered surgically cured are eligible (eg, non- melanoma skin cancer, cancer of the cervix in-situ, ductal carcinoma in situ \[Stage 1\], Grade 1 endometrial cancer)
* History of unstable or deteriorating cardiac or pulmonary disease within 6 months prior to consent including but not limited to the following:

* Unstable angina pectoris or myocardial infarction or elective coronary intervention
* Congestive heart failure requiring hospitalization
* Uncontrolled clinically significant arrhythmias
* Symptomatic pulmonary hypertension
Minimum Eligible Age

12 Years

Maximum Eligible Age

65 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Forma Therapeutics, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Clinical Transparency (dept. 2834)

Role: STUDY_DIRECTOR

Novo Nordisk A/S

Locations

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TOI Clinical Research

Cerritos, California, United States

Site Status

[Legal] Children's Hospital Los Angeles

Los Angeles, California, United States

Site Status

University of Californ LA-UCLA

Los Angeles, California, United States

Site Status

UCSF Oakland Benioff ChildHosp

Oakland, California, United States

Site Status

[Legal] Children's Hospital of Orange County on behalf of CHOC Children's Hospital of Orange County

Orange, California, United States

Site Status

UCI Health

Orange, California, United States

Site Status

Children's National Health Hospital

Washington D.C., District of Columbia, United States

Site Status

Children's Hospital of Atlanta

Atlanta, Georgia, United States

Site Status

[Legal] Dr. Vince Clinical Research, LLC and Dr. Vince Clinical Research, P.A.

Detroit, Michigan, United States

Site Status

Weill Medical College of Cornell University

New York, New York, United States

Site Status

Duke University

Durham, North Carolina, United States

Site Status

East Carolina University

Greenville, North Carolina, United States

Site Status

[Legal] Children's Hospital Medical Center dba Cincinnati Children's

Cincinnati, Ohio, United States

Site Status

Children's Hosptl Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

Master Centre for Canada

Mississauga, Ontario, Canada

Site Status

The Hospital for Sick Children

Toronto, Ontario, Canada

Site Status

University Health Network - Toronto General Hospital

Toronto, Ontario, Canada

Site Status

CHU Sainte-Justine Mother and Child University Hospital

Montreal, Quebec, Canada

Site Status

Cairo University

Cairo, , Egypt

Site Status

Abu El-Reesh El-Mounira Children University Hospital

Cairo, Egypt, , Egypt

Site Status

Galliera Hospital Centro Anemie Congenite

Genova, , Italy

Site Status

Fondazione IRCSS Ca' Granda Ospedale Maggiore Policlinico

Milan, , Italy

Site Status

A.O.U. Università Studi della Campania "Luigi Vanvitelli"

Naples, , Italy

Site Status

AORN A. Cardarelli

Napoli, , Italy

Site Status

Chronic Care Center

Baabda, , Lebanon

Site Status

Hospital Nini

Tripoli, , Lebanon

Site Status

Sandwell and West Birmingham NHS Trust SCAT/ haematology

Birmingham, , United Kingdom

Site Status

Barts Health NHS Trust - The Royal London Hospital

London, , United Kingdom

Site Status

University College Hospital - University College London Hospitals NHS Foundation Trust

London, , United Kingdom

Site Status

Kings College London

London, , United Kingdom

Site Status

Hammersmith Hospital - London

London, , United Kingdom

Site Status

Manchester University NHS Foundation Trust

Manchester, , United Kingdom

Site Status

Countries

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United States Canada Egypt Italy Lebanon United Kingdom

Other Identifiers

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4202-HEM-201

Identifier Type: -

Identifier Source: org_study_id