A Study of Pegcetacoplan in Pediatric Patients With Paroxysmal Nocturnal Hemoglobinuria (PNH)

NCT ID: NCT04901936

Last Updated: 2025-06-11

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE2

Total Enrollment

12 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-02-04

Study Completion Date

2028-12-31

Brief Summary

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The purpose of this study is to evaluate the safety, effectiveness, and biological activity (how the investigational medication is processed by the body) of pegcetacoplan in 12-17 year-olds (adolescents) who have paroxysmal nocturnal hemoglobinuria (PNH).

Detailed Description

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This is an open-label study to evaluate pegcetacoplan in people with PNH who are 12-17 years old. The study will consist of a 4-week screening period followed by a 16-week treatment period. Participants switching from a C5 inhibitor will have an additional 4 week run-in period between the screening and treatment periods. At the completion of the study treatment period, participants will either enter a long-term extension period or a 2-month follow-up period.

All eligible study participants will receive pegcetacoplan, administered via subcutaneous infusion twice a week at home. The subcutaneous infusion requires two small needles to be inserted into the fatty layer of tissue under the skin and the investigational medication will flow into the body. Study participants and/or caregivers will be trained on home administration of pegcetacoplan.

Conditions

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Paroxysmal Nocturnal Hemoglobinuria (PNH) Paroxysmal Hemoglobinuria

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Pegcetacoplan

Group Type EXPERIMENTAL

Pegcetacoplan

Intervention Type DRUG

Complement (C3) inhibitor

Interventions

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Pegcetacoplan

Complement (C3) inhibitor

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Are 12-17 years old at the time of screening
* Weigh at least 20 kg (approx. 44 lbs)
* Have the diagnosis of PNH, confirmed by high-sensitivity flow cytometry (granulocyte or monocyte clone \>10%)
* EITHER:

* Not being treated with an approved complement inhibitor (eculizumab or ravulizumab) prior to start of pegcetacoplan dosing, AND have hemolytic anemia. Hemolytic anemia is defined as hemoglobin (Hb) less than the lower limit of normal (Hb \< LLN) and LDH \>1.5 times the upper limit of normal (ULN); OR
* Currently receiving treatment with an approved complement inhibitor (eculizumab or ravulizumab) AND have evidence of ongoing anemia. Ongoing anemia is defined as Hb \< LLN and ARC \> ULN
* Have a platelet count \>75,000/mm3 and an absolute neutrophil count \>1000/mm3

Exclusion Criteria

* Are an adult, 18 years of age or older, with PNH
* Known or suspected hereditary fructose intolerance (HFI)
* History of hereditary complement deficiency, bone marrow transplant, or meningococcal disease (meningitis, bacteremia or septicemia)
* Females who are pregnant or breastfeeding
Minimum Eligible Age

12 Years

Maximum Eligible Age

17 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Apellis Pharmaceuticals, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Children's Hospital of Atlanta

Atlanta, Georgia, United States

Site Status RECRUITING

Motol University Hospital

Prague, , Czechia

Site Status COMPLETED

Robert-Debré Hospital Paris

Paris, , France

Site Status NOT_YET_RECRUITING

Hospital Ampang

Ampang, , Malaysia

Site Status RECRUITING

Radboud University Hospital Nijmegen

Nijmegen, , Netherlands

Site Status COMPLETED

University Medical Center Utrecht

Utrecht, , Netherlands

Site Status RECRUITING

University Children's Hospital

Belgrade, , Serbia

Site Status RECRUITING

University Hospital Vall d'Hebron

Barcelona, , Spain

Site Status RECRUITING

University Hospital 12 de Octubre

Madrid, , Spain

Site Status RECRUITING

Phramongkutklao Hospital and College of Medicine

Bangkok, , Thailand

Site Status RECRUITING

Maharaj Nakorn Chiang Mai hospital

Chiang Mai, , Thailand

Site Status RECRUITING

St. Mary's Hospital

London, , United Kingdom

Site Status RECRUITING

Countries

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United States Czechia France Malaysia Netherlands Serbia Spain Thailand United Kingdom

Central Contacts

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Apellis Clinical Trial Information Line

Role: CONTACT

1-833-284-6361 (833-CT Info-1)

Other Identifiers

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APL2-PNH-209

Identifier Type: -

Identifier Source: org_study_id

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