Open-label Extension Study to Evaluate the Long-term Safety and Tolerability of Aficamten in Adults With HCM

NCT ID: NCT04848506

Last Updated: 2025-11-13

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ENROLLING_BY_INVITATION

Clinical Phase

PHASE2/PHASE3

Total Enrollment

900 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-05-06

Study Completion Date

2028-03-31

Brief Summary

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The purpose of this study is to collect long-term safety and tolerability data for aficamten.

Detailed Description

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Conditions

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Symptomatic Hypertrophic Cardiomyopathy (HCM)

Keywords

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Obstructive Hypertrophic Cardiomyopathy oHCM CK-3773274 CK-274 Non obstructive hypertrophic cardiomyopathy nHCM HCM Hypertrophic cardiomyopathy Aficamten REDWOOD-OLE CY 6022 FOREST-HCM Forest

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Aficamten up to 20 mg

Patients in this arm take daily dose of aficamten. Each patient will start at the lowest prespecified dose and titrate up to their maximum tolerated dose.

Group Type EXPERIMENTAL

Aficamten (5 - 20 mg)

Intervention Type DRUG

Aficamten tablets administered orally. During titration phase, clinic visits will occur approximately every 2-6 weeks. In the maintenance phase clinic visits will occur every 24 weeks, with safety check-in occurring every 12 weeks between visits by phone or, if desirable, in the clinic.

Interventions

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Aficamten (5 - 20 mg)

Aficamten tablets administered orally. During titration phase, clinic visits will occur approximately every 2-6 weeks. In the maintenance phase clinic visits will occur every 24 weeks, with safety check-in occurring every 12 weeks between visits by phone or, if desirable, in the clinic.

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Completion of a Cytokinetics trial investigating aficamten
* LVEF ≥ 55% at the Screening Visit

Exclusion Criteria

* Has received treatment with mavacamten: (a) within 56 days prior to dosing and (b) has not received approval for participation from the Medical Monitor.
* Has participated in another investigational device or drug study or received an investigational device or drug \< 1 month (or 5 half-lives for drugs, whichever is longer) prior to screening. Other investigational procedures while participating in this study are not permitted.
* Since completion of a previous trial of aficamten has:

* Developed new-onset paroxysmal or permanent atrial fibrillation requiring rhythm restoring treatment (eg, direct-current cardioversion, ablation procedure, or antiarrhythmic therapy) \< 30 days prior to screening. Patient may re-screen for CY 6022 after 30 days if heart rate (HR) \< 100 bpm and/or rhythm is stable \> 30 days
* Undergone septal reduction therapy (surgical myectomy or transcatheter alcohol ablation)
* Had a confirmed LVEF \< 40% with an associated dose interruption during participation in a prior study with aficamten
* History of implantable ICD placement within 30 days prior to screening.
Minimum Eligible Age

18 Years

Maximum Eligible Age

85 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Cytokinetics

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Cytokinetics, MD

Role: STUDY_DIRECTOR

Cytokinetics

Locations

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Alaska Heart and Vascular Institute

Anchorage, Alaska, United States

Site Status

Mayo Clinic Building - Phoenix

Phoenix, Arizona, United States

Site Status

UC San Diego Health - Sulpizio Cardiovascular Center

La Jolla, California, United States

Site Status

Cedar-Sinai Medical Center

Los Angeles, California, United States

Site Status

Cedars-Sinai Medical Center (Smidt Heart Institute)

Los Angeles, California, United States

Site Status

UCSF Medical Center

San Francisco, California, United States

Site Status

Yale New Haven Hospital

New Haven, Connecticut, United States

Site Status

MedStar Washington Hospital Center

Washington D.C., District of Columbia, United States

Site Status

Holy Cross Hospital / Cardiology Associates

Fort Lauderdale, Florida, United States

Site Status

Emory Clinic

Atlanta, Georgia, United States

Site Status

Piedmont Fayette Hospital

Fayetteville, Georgia, United States

Site Status

Northwestern University

Evanston, Illinois, United States

Site Status

Massachusetts General Hospital

Boston, Massachusetts, United States

Site Status

Brigham and Women's Hospital

Boston, Massachusetts, United States

Site Status

Lahey Hospital & Medical Center

Burlington, Massachusetts, United States

Site Status

Michigan Medicine - University of Michigan

Ann Arbor, Michigan, United States

Site Status

University of Michigan Health System (UMHS) - University Hospital (University of Michigan Medical Center)

Ann Arbor, Michigan, United States

Site Status

Henry Ford Hospital

Detroit, Michigan, United States

Site Status

Saint Luke's Hospital of Kansas City

Kansas City, Missouri, United States

Site Status

Morristown Medical Center

Morristown, New Jersey, United States

Site Status

Northwell Health North Shore University Hospital

Manhasset, New York, United States

Site Status

NYU Langone Health

New York, New York, United States

Site Status

Weill Cornell Medicine

New York, New York, United States

Site Status

Mount Sinai Hospital

New York, New York, United States

Site Status

Columbia University Medical Center/New York Presbyterian Hospital

New York, New York, United States

Site Status

Westchester Medical Center

Valhalla, New York, United States

Site Status

Sanger Heart & Vascular Institute - HCM Clinic

Charlotte, North Carolina, United States

Site Status

Duke Cardiology at Southpoint

Durham, North Carolina, United States

Site Status

The Linder Research Center at The Christ Hospital

Cincinnati, Ohio, United States

Site Status

Cleveland Clinic

Cleveland, Ohio, United States

Site Status

Ascension St. John Clinical Research Institute

Tulsa, Oklahoma, United States

Site Status

Providence St. Vincent Medical Center

Portland, Oregon, United States

Site Status

Oregon Health & Science University

Portland, Oregon, United States

Site Status

Hospital of the University of Pennsylvania (University of Pennsylvania School of Medicine)

Philadelphia, Pennsylvania, United States

Site Status

UPMC Presbyterian

Pittsburgh, Pennsylvania, United States

Site Status

Medical University of South Carolina

Charleston, South Carolina, United States

Site Status

Ascension Saint Thomas Heart West

Nashville, Tennessee, United States

Site Status

Vanderbilt University Medical Center

Nashville, Tennessee, United States

Site Status

The University of Texas Southwestern Medical Center at Dallas

Dallas, Texas, United States

Site Status

CHI St. Luke's Health Baylor College of Medicine Medical Center

Houston, Texas, United States

Site Status

Houston Methodist Hospital

Houston, Texas, United States

Site Status

Intermountain Medical Center

Murray, Utah, United States

Site Status

University of Utah Health

Salt Lake City, Utah, United States

Site Status

University of Virginia Health System University Hospital

Charlottesville, Virginia, United States

Site Status

Inova Health Care Services

Falls Church, Virginia, United States

Site Status

Instituto Dante Pazzanese de Cardiologia

São Paulo, , Brazil

Site Status

Institut universitaire de cardiologie et de pneumologie de Quebec-Universite Laval

Québec, Quebec, Canada

Site Status

Il. Interni klinika kardiologie a angiologie

Prague, , Czechia

Site Status

Department of Cardiology Aalborg University Hospital

Aalborg, , Denmark

Site Status

Department of Cardiology Aarhus University Hospital

Aarhus, , Denmark

Site Status

The Heart Center, Department of Cardiology

Copenhagen, , Denmark

Site Status

Copenhagen University Hospital

Copenhagen, , Denmark

Site Status

Hopital de la Timone Service de cardiologie

Marseille, , France

Site Status

CHU de Nantes Institut Du Thorax et du systeme nerveux Clinique Cardiologique et des Maladies Vasculaires

Nantes, , France

Site Status

Hopital Lariboisiere

Paris, , France

Site Status

Hopital Europeen Georges Pompidou

Paris, , France

Site Status

Hopital cardiologique de Haut-Leveque

Pessac, , France

Site Status

Centre hospitalier universitaire (CHU) de Rennes-Hopital Pontchaillou

Rennes, , France

Site Status

Charite-Universitaetsmedizin Berlin

Berlin, , Germany

Site Status

Universitaetsklinikum Essen

Essen, , Germany

Site Status

Universitaetsmedizin Goettingen Klinik fur Kardiologie und Pneumologie

Goettigen, , Germany

Site Status

Universitaesklinkum Heidelberg

Heidelberg, , Germany

Site Status

Universitaetsklinikum Jena

Jena, , Germany

Site Status

Universitaetskinikum Wuerzburg Deutsches Zentrum fur Herzinsuffzienz Wurzburg (DZHI) Comprehensive Heart Failure Center (CHFC)

Würzburg, , Germany

Site Status

Semmelweis Egyetem Varosmajori Sziv es Ergyogyaszati Klinika

Budapest, , Hungary

Site Status

The Barzilai University Medical Center

Ashkelon, , Israel

Site Status

Hadassah Medical Center- Ein Kerem

Jerusalem, , Israel

Site Status

The Chaim Sheba Medical Center

Ramat Gan, , Israel

Site Status

Ziv Medical Center

Safed, , Israel

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Unit Cardiomiopatie, Dipartimento Cardio ToracoVascolare

Florence, , Italy

Site Status

Fondazione toscana Gabriele Monesterio per la ricarca medica Dipartimento Cardiotoracico UOC Cardiologia e Medicina Cardiovasculare Ospedale San Cataldo

Pisa, , Italy

Site Status

Dipartimento di Medicina Clinica e Molecolare Universita Sapienza di Roma Unita di Terapia Intensiva Cardiologica Azienda Ospedaliero Universitaria Sant'Andrea

Roma, , Italy

Site Status

Maastricht University Medical Center (MUMC)

Maastricht, , Netherlands

Site Status

Erasmus Medical Center Department of Cardiology

Rotterdam, , Netherlands

Site Status

Kardio Brynow S.C.

Katowice, , Poland

Site Status

Narodowy Instytut Kardiologii Stefana Kardynala Wyszynskiego - Panstwowy Instytut Badawczy Centrum Zaburzen Rytmu Serca

Warsaw, , Poland

Site Status

Centro Hospitalar Do Baixo Vouga, EPE Cardiology Department

Aveiro, , Portugal

Site Status

Hospital da Luz

Lisbon, , Portugal

Site Status

Complejo Hospitalario Universitario A Coruna

A Coruña, , Spain

Site Status

Hospital Clinic Barcelona

Barcelona, , Spain

Site Status

Hospital Universitario Puerta de Hierro Majadahonda

Madrid, , Spain

Site Status

Hospital Clinico Universitario Virgen de la Arrixaca

Madrid, , Spain

Site Status

Hospital Universitario Son Llatzer

Palma, , Spain

Site Status

Hospital Universitario de Salamanca

Salamanca, , Spain

Site Status

Hospital Universitario Virgen Macarena-merge

Seville, , Spain

Site Status

Hospital Universitario Virgen del Rocío

Seville, , Spain

Site Status

Queen Elizabeth Hospital Birmingham University Hospitals Birmingham NHS Foundation Trust

Birmingham, , United Kingdom

Site Status

Glasgow Clinical Research Facility Neuroscience Institute

Glasgow, , United Kingdom

Site Status

Liverpool Heart and Chest Hospital

Liverpool, , United Kingdom

Site Status

St Bartholomew's Hospital

London, , United Kingdom

Site Status

St George's University Hospitals NHS Foundation Trust

London, , United Kingdom

Site Status

Royal Brompton Hospital

London, , United Kingdom

Site Status

Oxford Centre for Clinical Magnetic Resonance Research (OCMR) Division of Cardiovascular Medicine Radcliffe Department of Medicine University of Oxford

Oxford, , United Kingdom

Site Status

Countries

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United States Brazil Canada Czechia Denmark France Germany Hungary Israel Italy Netherlands Poland Portugal Spain United Kingdom

References

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Saberi S, Abraham TP, Choudhury L, Barriales-Villa R, Elliott PM, Nassif ME, Oreziak A, Owens AT, Tower-Rader A, Rader F, Garcia-Pavia P, Olivotto I, Coats CJ, Fifer MA, Sherrid MV, Solomon SD, Watkins H, Heitner SB, Jacoby DL, Kupfer S, Malik FI, Melloni C, Meng L, Wei J, Maron MS, Masri A; FOREST-HCM Steering Committee and Investigators. Aficamten Treatment for Symptomatic Obstructive Hypertrophic Cardiomyopathy: 48-Week Results From FOREST-HCM. JACC Heart Fail. 2025 Aug;13(8):102496. doi: 10.1016/j.jchf.2025.03.040. Epub 2025 Jun 19.

Reference Type DERIVED
PMID: 40540987 (View on PubMed)

Masri A, Maron MS, Abraham TP, Nassif ME, Barriales-Villa R, Bilen O, Coats CJ, Elliott P, Garcia-Pavia P, Massera D, Olivotto I, Oreziak A, Owens AT, Saberi S, Solomon SD, Tower-Rader A, Heitner SB, Jacoby DL, Melloni C, Wei J, Sherrid MV; REDWOOD-HCM, SEQUOIA-HCM, and FOREST-HCM Investigators. Concomitant Aficamten and Disopyramide in Symptomatic Obstructive Hypertrophic Cardiomyopathy. JACC Heart Fail. 2025 Apr 2:102441. doi: 10.1016/j.jchf.2025.03.008. Online ahead of print.

Reference Type DERIVED
PMID: 40285763 (View on PubMed)

Masri A, Choudhury L, Barriales-Villa R, Elliott P, Maron MS, Nassif ME, Oreziak A, Owens AT, Saberi S, Tower-Rader A, Rader F, Garcia-Pavia P, Olivotto I, Nagueh SF, Wang A, Heitner SB, Jacoby DL, Kupfer S, Malik FI, Melloni C, Meng L, Wei J, Sherrid MV, Abraham TP; FOREST-HCM Investigators. Standard-of-Care Medication Withdrawal in Patients With Obstructive Hypertrophic Cardiomyopathy Receiving Aficamten in FOREST-HCM. J Am Coll Cardiol. 2024 Nov 5;84(19):1839-1849. doi: 10.1016/j.jacc.2024.09.002.

Reference Type DERIVED
PMID: 39477631 (View on PubMed)

Other Identifiers

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2020-003571-17

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

2023-508963-58-00

Identifier Type: OTHER

Identifier Source: secondary_id

CY 6022

Identifier Type: -

Identifier Source: org_study_id