Global Safety and Efficacy Registration Study of Crinecerfont in Pediatric Participants With Classic Congenital Adrenal Hyperplasia (CAHtalyst Pediatric Study)

NCT ID: NCT04806451

Last Updated: 2025-02-05

Study Results

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Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

103 participants

Study Classification

INTERVENTIONAL

Study Start Date

2021-06-25

Study Completion Date

2027-08-31

Brief Summary

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This is a Phase 3 study to evaluate the efficacy, safety, and tolerability of crinecerfont versus placebo administered for 28 weeks in approximately 81 pediatric participants with classic congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. The study consists of a 28-week double blind, placebo-controlled period, followed by 24 weeks of open-label treatment with crinecerfont. Subsequently, participants may elect to participate in the open-label extension (OLE) period. The duration of participation in the study is approximately 14 months for the core study and will be a variable amount of time per participant for the OLE (estimated to be approximately 3 years).

Detailed Description

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Conditions

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Congenital Adrenal Hyperplasia

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

TRIPLE

Participants Caregivers Investigators

Study Groups

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Crinecerfont

Crinecerfont solution or capsule, administered orally, twice daily for 28 weeks during the placebo-controlled treatment period, followed by active treatment with crinecerfont for at least 24 weeks.

Group Type EXPERIMENTAL

Crinecerfont

Intervention Type DRUG

CRF type 1 receptor antagonist

Placebo

Placebo solution or capsule, administered orally, twice daily for 28 weeks, followed by active treatment with crinecerfont for at least 24 weeks.

Group Type PLACEBO_COMPARATOR

Crinecerfont

Intervention Type DRUG

CRF type 1 receptor antagonist

Placebo

Intervention Type DRUG

Non-active dosage form

Interventions

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Crinecerfont

CRF type 1 receptor antagonist

Intervention Type DRUG

Placebo

Non-active dosage form

Intervention Type DRUG

Other Intervention Names

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NBI-74788 Crenessity

Eligibility Criteria

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Inclusion Criteria

* Be willing and able to adhere to the study procedures, including all requirements at the study center, and return for the follow-up visit.
* Have a medically confirmed diagnosis of classic CAH due to 21-hydroxylase deficiency.
* Be on a stable steroid regimen.
* Have elevated androgen levels.
* Participants of childbearing potential must be abstinent or agree to use appropriate birth control during the study.

Exclusion Criteria

* Have a diagnosis of any of the other forms of classic CAH.
* Have a history of bilateral adrenalectomy, hypopituitarism, or other condition requiring chronic glucocorticoid therapy.
* Have a clinically significant unstable medical condition or chronic disease other than CAH.
* Have a history of cancer unless considered to be cured.
* Have a known history of clinically significant arrhythmia or abnormalities on electrocardiogram (ECG).
* Have a known hypersensitivity to any corticotropin-releasing hormone antagonist.
* Have received an investigational drug within 30 days before initial screening or plan to use an investigational drug (other than the study drug) during the study.
* Have current substance dependence or substance (drug) or alcohol abuse.
* Have had a significant blood loss or donated blood or blood products within 8 weeks prior to the study.
Minimum Eligible Age

2 Years

Maximum Eligible Age

17 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Neurocrine Biosciences

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Clinical Development Lead

Role: STUDY_DIRECTOR

Neurocrine Biosciences

Locations

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Neurocrine Clinical Site

Birmingham, Alabama, United States

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Los Angeles, California, United States

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Orange, California, United States

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San Diego, California, United States

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San Francisco, California, United States

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Aurora, Colorado, United States

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Hartford, Connecticut, United States

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Washington D.C., District of Columbia, United States

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Atlanta, Georgia, United States

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Indianapolis, Indiana, United States

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Boston, Massachusetts, United States

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Ann Arbor, Michigan, United States

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Minneapolis, Minnesota, United States

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St Louis, Missouri, United States

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New Hyde Park, New York, United States

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New York, New York, United States

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Oklahoma City, Oklahoma, United States

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Tulsa, Oklahoma, United States

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Philadelphia, Pennsylvania, United States

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Pittsburgh, Pennsylvania, United States

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Dallas, Texas, United States

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Seattle, Washington, United States

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Brussels, , Belgium

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Ghent, , Belgium

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Edmonton, Alberta, Canada

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Vancouver, British Columbia, Canada

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Montreal, Quebec, Canada

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Angers, , France

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Bordeau, , France

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Le Kremlin-Bicêtre, , France

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Paris, , France

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Paris, , France

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Berlin, , Germany

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Heidelberg, , Germany

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Magdeburg, , Germany

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Athens, , Greece

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Athens, , Greece

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Bologna, , Italy

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Milan, , Italy

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Napoli, , Italy

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Roma, , Italy

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Gdansk, , Poland

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Rzeszów, , Poland

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Barcelona, , Spain

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Neurocrine Clinical Site

Seville, , Spain

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Neurocrine Clinical Site

London, , United Kingdom

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Countries

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United States Belgium Canada France Germany Greece Italy Poland Spain United Kingdom

References

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Sarafoglou K, Kim MS, Lodish M, Felner EI, Martinerie L, Nokoff NJ, Clemente M, Fechner PY, Vogiatzi MG, Speiser PW, Auchus RJ, Rosales GBG, Roberts E, Jeha GS, Farber RH, Chan JL; CAHtalyst Pediatric Trial Investigators. Phase 3 Trial of Crinecerfont in Pediatric Congenital Adrenal Hyperplasia. N Engl J Med. 2024 Aug 8;391(6):493-503. doi: 10.1056/NEJMoa2404655. Epub 2024 Jun 2.

Reference Type DERIVED
PMID: 38828945 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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2020-004381-19

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

2023-509170-33-00

Identifier Type: CTIS

Identifier Source: secondary_id

NBI-74788-CAH2006

Identifier Type: -

Identifier Source: org_study_id

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