First in Human Study to Test the Safety and Preliminary Efficacy of PPSGG in Patients With Anti-MAG Neuropathy

NCT ID: NCT04568174

Last Updated: 2021-10-15

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

TERMINATED

Clinical Phase

PHASE1/PHASE2

Total Enrollment

1 participants

Study Classification

INTERVENTIONAL

Study Start Date

2020-11-17

Study Completion Date

2021-09-23

Brief Summary

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In this study, the new drug called PPSGG (PN-1007) will be tested. Preliminary studies conducted in animals suggest PPSGG (PN-1007) might be a good treatment for reducing levels of anti-MAG antibodies in patients with anti-MAG neuropathy.

This is the first research of PPSGG (PN-1007) in people and its main purpose is to test its safety and acceptability in patients. In this study it will be examined how the drug is changed by and removed from the body and checked for signs that the drug may be truly effective against anti-MAG neuropathy. PPSGG (PN-1007) will be tested at several different doses.

Detailed Description

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PPSGG (PN-1007) is intended to bind anti-MAG IgM autoantibodies, the underlying cause of anti-MAG neuropathy, in a highly selective manner, resulting in their neutralization and removal from the circulation. This allows specific targeting of anti-MAG IgM in the circulation and circumvents unspecific immunosuppression associated with current treatment strategies.

This is a Phase I/IIa, First in Human (FiH), multicenter, single and multiple ascending dose escalation trial of PPSGG (PN-1007), an antibody scavenger of pathogenic anti-MAG immunoglobulin M (IgM) autoantibodies for treatment of anti-MAG neuropathy. The aim of the study is to assess the safety and tolerability, pharmacokinetics (PK), pharmacodynamics (PD), and preliminary efficacy of PPSGG (PN-1007) in a SAD and a MAD phase in an adaptive trial in anti-MAG neuropathy patients.

Conditions

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Anti-MAG Neuropathy

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Single Group in SAD and parallel in MAD
Primary Study Purpose

TREATMENT

Blinding Strategy

TRIPLE

Participants Investigators Outcome Assessors
The SAD phase is open label and MAD is randomized, dose escalation, double blind (patient and investigator blinded), placebo-controlled

Study Groups

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PPSGG

sterile liquid, one 1-hour infusion in SAD and multiple infusions in MAD. In SAD multiple cohorts being tested. Dosage and regime in MAD to be defined based on SAD outcome.

Group Type ACTIVE_COMPARATOR

PPSGG

Intervention Type DRUG

an antibody scavenger of pathogenic anti-MAG immunoglobulin M (IgM) autoantibodies

Placebo

standard PBS solution, pH 7.4, composed of disodium hydrogen phosphate dodecahydrate, potassium dihydrogen phosphate, sodium chloride, and water for injection

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

A standard PBS solution, pH 7.4, composed of disodium hydrogen phosphate dodecahydrate, potassium dihydrogen phosphate, sodium chloride, and water for injection

Interventions

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PPSGG

an antibody scavenger of pathogenic anti-MAG immunoglobulin M (IgM) autoantibodies

Intervention Type DRUG

Placebo

A standard PBS solution, pH 7.4, composed of disodium hydrogen phosphate dodecahydrate, potassium dihydrogen phosphate, sodium chloride, and water for injection

Intervention Type DRUG

Other Intervention Names

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PN-1007

Eligibility Criteria

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Inclusion Criteria

* Patients with a confirmed diagnosis of monoclonal IgM associated with MGUS with anti-MAG activity (titer of \> 10'000 BTU) and demyelinating neuropathy defined by electrophysiological criteria according to EFNS/PNS PDN guideline, 2010.
* Clear clinical signs of disability
* Adequate hepatic and renal function

Exclusion Criteria

* Patients with total serum IgM levels \>30 g.
* Hematological malignancy, prior malignancy of any organ system (except BCC)
* Prior immunosuppression: No IVIG in previous 3 months, no previous cyclophosphamide or biologicals in prior 6 months.
* Other neurological, neuromuscular, rheumatologic or orthopedic condition with significant impact on the capabilities of walk preventing evaluation of neurological scores
Minimum Eligible Age

18 Years

Maximum Eligible Age

80 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Polyneuron Pharmaceuticals AG

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Hedvika Lazar

Role: STUDY_CHAIR

Polyneuron Pharmaceuticals AG

Locations

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Service de Neurologie Centre de Référence Neuropathies Périphériques Rares, CHU Limoges

Limoges, , France

Site Status

Referral centre for neuromuscular diseases and ALS, hôpital La Timone

Marseille, , France

Site Status

Département de Neurologie Pôle Neurosciences Centre de Référence des Neuropathies Amyloïdes Familiales et autres Neuropathies Périphériques Rares Centre Hospitalier Universitaire de Bicêtre

Paris, , France

Site Status

UMC Utrecht Cancer Center

Utrecht, , Netherlands

Site Status

Barcelona

Barcelona, , Spain

Site Status

Lausanne

Lausanne, , Switzerland

Site Status

National hospital for neurology and neurosurgery, Queen London

London, , United Kingdom

Site Status

Countries

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France Netherlands Spain Switzerland United Kingdom

Other Identifiers

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PN-1007-001

Identifier Type: -

Identifier Source: org_study_id