Efficacy and Safety of Odevixibat in Children With Biliary Atresia Who Have Undergone a Kasai HPE (BOLD)

NCT ID: NCT04336722

Last Updated: 2025-12-30

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

Get a concise snapshot of the trial, including recruitment status, study phase, enrollment targets, and key timeline milestones.

Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE3

Total Enrollment

254 participants

Study Classification

INTERVENTIONAL

Study Start Date

2020-07-08

Study Completion Date

2026-06-26

Brief Summary

Review the sponsor-provided synopsis that highlights what the study is about and why it is being conducted.

Double-blind, randomized, placebo-controlled, Phase 3 study to investigate the efficacy and safety of odevixibat compared to placebo in children with biliary atresia who have undergone a Kasai hepatoportoenterostomy.

Detailed Description

Dive into the extended narrative that explains the scientific background, objectives, and procedures in greater depth.

Up to 70 sites will be initiated for this study in North America, Europe, Middle East, and Asia Pacific.

Conditions

See the medical conditions and disease areas that this research is targeting or investigating.

Biliary Atresia

Keywords

Explore important study keywords that can help with search, categorization, and topic discovery.

Kasai

Study Design

Understand how the trial is structured, including allocation methods, masking strategies, primary purpose, and other design elements.

Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

TRIPLE

Participants Caregivers Investigators

Study Groups

Review each arm or cohort in the study, along with the interventions and objectives associated with them.

Odevixibat (A4250)

Capsules for oral administration once daily for 104 weeks.

Group Type EXPERIMENTAL

Odevixibat

Intervention Type DRUG

Odevixibat is a small molecule and selective inhibitor of IBAT.

Placebo

Capsules for oral administration (to match active) once daily for 104 weeks.

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Placebo identical in appearance to experimental drug (odevixibat).

Interventions

Learn about the drugs, procedures, or behavioral strategies being tested and how they are applied within this trial.

Odevixibat

Odevixibat is a small molecule and selective inhibitor of IBAT.

Intervention Type DRUG

Placebo

Placebo identical in appearance to experimental drug (odevixibat).

Intervention Type DRUG

Eligibility Criteria

Check the participation requirements, including inclusion and exclusion rules, age limits, and whether healthy volunteers are accepted.

Inclusion Criteria

* A male or female patient with a clinical diagnosis of BA
* Age at Kasai HPE ≤90 days
* Eligible to start study treatment within 3 weeks post-Kasai HPE

Exclusion Criteria

* Patients with intractable ascites
* Ileal resection surgery
* ALT ≥10× upper limit of normal (ULN) at screening
* Patients reliant only on total parenteral nutrition, or not able to take study medication orally, at randomization
* Acute ascending cholangitis (patients may be randomized after resolution of acute ascending cholangitis)
* Choledochal cystic disease
* INR \>1.6 (the patient may be treated with Vitamin K intravenously; sample may be redrawn and if INR is ≤1.6 at resampling the patient may be randomized)
* Any other conditions or abnormalities, including congenital abnormalities, major cardiac surgery, hepatic, biliary, or GI disease which, in the opinion of the Investigator or Medical Monitor, may compromise the safety of the patient, the integrity of study results, or patient compliance with study requirements
* Weight \<3.5kg at randomization
Maximum Eligible Age

111 Days

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

Meet the organizations funding or collaborating on the study and learn about their roles.

Albireo, an Ipsen Company

INDUSTRY

Sponsor Role lead

Responsible Party

Identify the individual or organization who holds primary responsibility for the study information submitted to regulators.

Responsibility Role SPONSOR

Principal Investigators

Learn about the lead researchers overseeing the trial and their institutional affiliations.

Ipsen Medical Director

Role: STUDY_DIRECTOR

Ipsen

Locations

Explore where the study is taking place and check the recruitment status at each participating site.

Children's Hospital Los Angeles

Los Angeles, California, United States

Site Status

Stanford Children's Health

Palo Alto, California, United States

Site Status

Rady Children's Hospital

San Diego, California, United States

Site Status

UCSF Benioff Children's Hospital San Francisco

San Francisco, California, United States

Site Status

Children's Hospital Colorado

Aurora, Colorado, United States

Site Status

Nemours/Alfred I. duPont Hospital for Children

Wilmington, Delaware, United States

Site Status

Children's National Medical Center

Washington D.C., District of Columbia, United States

Site Status

University of Miami

Miami, Florida, United States

Site Status

Children's Healthcare of Atlanta - Emory University School of Medicine

Atlanta, Georgia, United States

Site Status

Ann & Robert H. Lurie Children's Hospital

Chicago, Illinois, United States

Site Status

Indiana University school of Medicine

Indianapolis, Indiana, United States

Site Status

Johns Hopkins Children's Center

Baltimore, Maryland, United States

Site Status

Boston Children's Hospital

Boston, Massachusetts, United States

Site Status

University of Michigan Children's Hospital

Ann Arbor, Michigan, United States

Site Status

Children's Mercy Hospital

Kansas City, Missouri, United States

Site Status

Washington University in St. Louis

St Louis, Missouri, United States

Site Status

NYU Grossman school of Medicine

New York, New York, United States

Site Status

Icahn School of Medicine at Mount Sinai

New York, New York, United States

Site Status

NewYork-Presbyterian Morgan Stanley Children's Hospital

New York, New York, United States

Site Status

The Children's Hospital at Montefiore

The Bronx, New York, United States

Site Status

Cincinnati Children's Hospital

Cincinnati, Ohio, United States

Site Status

Cleveland Clinic

Cleveland, Ohio, United States

Site Status

Oregon Health & Science University

Portland, Oregon, United States

Site Status

The Children´s Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

UPMC Children's Hospital of Pittsburgh

Pittsburgh, Pennsylvania, United States

Site Status

UT Southwestern Medical Center

Dallas, Texas, United States

Site Status

University of Utah

Salt Lake City, Utah, United States

Site Status

Seattle Children's Hospital

Seattle, Washington, United States

Site Status

Medical College of Wisconsin

Milwaukee, Wisconsin, United States

Site Status

Royal Children's Hospital

Parkville, , Australia

Site Status

The Children´s Hospital at Westmead

Sydney, , Australia

Site Status

UZ Gent

Ghent, , Belgium

Site Status

CHU Sainte-Justine

Montreal, , Canada

Site Status

The Hospital for Sick Children

Toronto, , Canada

Site Status

Guangzhou Women and Children's Medical Center

Guangzhou, Guangdong, China

Site Status

Children's Hospital of Fudan University

Shanghai, , China

Site Status

Hôpital Femme Mère Enfant

Bron, , France

Site Status

Bicêtre Hospital

Le Kremlin-Bicêtre, , France

Site Status

Jeanne de Flandre Hospital

Lille, , France

Site Status

Necker University Hospital - Enfants malades

Paris, , France

Site Status

Charité - Universitätsmedizin Berlin

Berlin, , Germany

Site Status

University Medical Center Hamburg-Eppendorf UKE

Hamburg, , Germany

Site Status

Hannover Medical School

Hanover, , Germany

Site Status

University Children´s Hospital Tuebingen

Tübingen, , Germany

Site Status

Semmelweis Egyetem I.sz Gyermekgyógyászati Klinika

Budapest, , Hungary

Site Status

Schneider Children´s Medical Center of Israel

Petah Tikva, , Israel

Site Status

ASST Papa Giovanni XXIII

Bergamo, , Italy

Site Status

Meyer Children´s University Hospital

Florence, , Italy

Site Status

University Hospital of Padova

Padua, , Italy

Site Status

ISMETT - Istituto Mediterraneo per i Trapianti e Terapie ad Alta Specializzazione

Palermo, , Italy

Site Status

Ospedale Pediatrico Bambino Gesù

Roma, , Italy

Site Status

Regina Margherita Children´s Hospital

Turin, , Italy

Site Status

Hospital Raja Perempuan Zainab II

Kota Bharu, , Malaysia

Site Status

University of Malaya Medical Centre

Kuala Lumpur, , Malaysia

Site Status

University Medical Center Groningen

Groningen, , Netherlands

Site Status

Starship Child Health

Auckland, , New Zealand

Site Status

Instytut Pomnik-Centrum Zdrowia Dziecka

Warsaw, , Poland

Site Status

Samsung Medical Center

Seoul, , South Korea

Site Status

Seoul National University Children's Hospital

Seoul, , South Korea

Site Status

Hospital Universitari Vall d'Hebron

Barcelona, , Spain

Site Status

National Taiwan University Hospital

Taipei, , Taiwan

Site Status

Hacettepe University Ihsan Dogramaci Childrens Hospital

Ankara, , Turkey (Türkiye)

Site Status

Akdeniz University Medical Faculty

Antalya, , Turkey (Türkiye)

Site Status

Istanbul University, Istanbul Medical Faculty

Istanbul, , Turkey (Türkiye)

Site Status

Birmingham Women´s and Children´s Hospital

Birmingham, , United Kingdom

Site Status

Leeds General Infirmary

Leeds, , United Kingdom

Site Status

Countries

Review the countries where the study has at least one active or historical site.

United States Australia Belgium Canada China France Germany Hungary Israel Italy Malaysia Netherlands New Zealand Poland South Korea Spain Taiwan Turkey (Türkiye) United Kingdom

Other Identifiers

Review additional registry numbers or institutional identifiers associated with this trial.

2019-003807-37

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

2024-512086-14-00

Identifier Type: CTIS

Identifier Source: secondary_id

A4250-011

Identifier Type: -

Identifier Source: org_study_id