Genotypic Influences on Network Progression in Parkinson's Disease

NCT ID: NCT04228172

Last Updated: 2025-12-18

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Total Enrollment

32 participants

Study Classification

OBSERVATIONAL

Study Start Date

2020-02-24

Study Completion Date

2026-02-01

Brief Summary

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In this longitudinal study, the investigators will follow Parkinson's disease (PD) patients with and without glucocerebrosidase (GBA) mutations. The investigators hypothesize that the rate of increase in brain network activity over time (network progression rate) is faster in patients with GBA gene mutations.

Detailed Description

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Parkinson's disease (PD) patients with mutations in the glucocerebrosidase gene (GBA) tend to have a more aggressive disease course. GBA may therefore provide a target for disease modifying therapies in mutation carriers. Using positron emission tomography (PET) and magnetic resonance imaging (MRI) brain imaging to measure network progression rates in mutation carriers will allow for the assessment of the potential disease modifying effects of new anti-GBA therapies.

The investigators will also determine whether magnetic resonance imaging (MRI) network methods, which are less invasive and more broadly available than positron emission tomography (PET), produce comparable network progression measurements in individual patients. These determinations will be critical for the design of clinical trials of new disease-modifying drugs.

Conditions

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Parkinson's Disease

Keywords

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GBA genetic progression PD glucocerebrosidase

Study Design

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Observational Model Type

CASE_CONTROL

Study Time Perspective

PROSPECTIVE

Study Groups

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Parkinson's disease (PD) glucocerebrosidase (GBA) carriers

Parkinson's disease subjects with GBA mutation

DNA/GeneticTesting

Intervention Type GENETIC

Subjects will be tested for GBA and LRRK2 mutation status at baseline.

FDG PET scan

Intervention Type RADIATION

18F-Fluoro-2-deoxy-glucose (FDG) PET scan is a nuclear medicine test that measures glucose metabolism (energy) in your brain at baseline and 18 months later.

MRI scan

Intervention Type OTHER

Magnetic Resonance Imaging (MRI) is a noninvasive scan which produces detailed pictures of the brain using a magnetic field. In addition, a special type of MRI, called resting state functional MRI (rs-fMRI), will measure and map brain activity. Conducted at baseline and 18 months later.

Clinical and neuropsychological assessments

Intervention Type OTHER

Investigator will evaluate subjects according to the Movement Disorder Society-Unified Parkinson's Disease Rating Scale (MDS-UPDRS), the standard clinical tool used to measure the severity and progression of PD. Neuropsychological evaluation will assess how one's brain functions (via pencil and paper testing), which indirectly yields information about the structural and functional integrity of the brain. Conducted at baseline and 18 months later.

Parkinson's disease (PD) non glucocerebrosidase (GBA) carriers

Parkinson's disease subjects without GBA mutation

DNA/GeneticTesting

Intervention Type GENETIC

Subjects will be tested for GBA and LRRK2 mutation status at baseline.

FDG PET scan

Intervention Type RADIATION

18F-Fluoro-2-deoxy-glucose (FDG) PET scan is a nuclear medicine test that measures glucose metabolism (energy) in your brain at baseline and 18 months later.

MRI scan

Intervention Type OTHER

Magnetic Resonance Imaging (MRI) is a noninvasive scan which produces detailed pictures of the brain using a magnetic field. In addition, a special type of MRI, called resting state functional MRI (rs-fMRI), will measure and map brain activity. Conducted at baseline and 18 months later.

Clinical and neuropsychological assessments

Intervention Type OTHER

Investigator will evaluate subjects according to the Movement Disorder Society-Unified Parkinson's Disease Rating Scale (MDS-UPDRS), the standard clinical tool used to measure the severity and progression of PD. Neuropsychological evaluation will assess how one's brain functions (via pencil and paper testing), which indirectly yields information about the structural and functional integrity of the brain. Conducted at baseline and 18 months later.

Interventions

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DNA/GeneticTesting

Subjects will be tested for GBA and LRRK2 mutation status at baseline.

Intervention Type GENETIC

FDG PET scan

18F-Fluoro-2-deoxy-glucose (FDG) PET scan is a nuclear medicine test that measures glucose metabolism (energy) in your brain at baseline and 18 months later.

Intervention Type RADIATION

MRI scan

Magnetic Resonance Imaging (MRI) is a noninvasive scan which produces detailed pictures of the brain using a magnetic field. In addition, a special type of MRI, called resting state functional MRI (rs-fMRI), will measure and map brain activity. Conducted at baseline and 18 months later.

Intervention Type OTHER

Clinical and neuropsychological assessments

Investigator will evaluate subjects according to the Movement Disorder Society-Unified Parkinson's Disease Rating Scale (MDS-UPDRS), the standard clinical tool used to measure the severity and progression of PD. Neuropsychological evaluation will assess how one's brain functions (via pencil and paper testing), which indirectly yields information about the structural and functional integrity of the brain. Conducted at baseline and 18 months later.

Intervention Type OTHER

Eligibility Criteria

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Inclusion Criteria

* Diagnosis of PD made according to United Kingdom (UK) Parkinson's Disease Society Brain Bank Criteria
* Ability to provide written informed consent
* Age 40-75
* Stable dose of antiparkinsonian medication for \>1 month prior to study entry

Exclusion Criteria

* Subjects with pathogenic mutations in LRRK2 related PD mutations (subjects with variants of uncertain significance (VUS) are eligible
* History of known causative factors such as encephalitis or neuroleptic treatment
* Patients with dementia (defined as Mini-Mental Status Exam score \<24 or a Telephone Interview for Cognitive Status score \<26)
* Atypical parkinsonian features including oculomotor abnormalities, incontinence, ataxia, sensory loss, or pyramidal signs
* Known structural brain lesions
* Patients with history of stroke, head injury, high intracranial pressure or severe headaches
* Psychiatric disorder, including a history of major depression in the past 36 months
* Pregnant or breastfeeding women (female subjects of child-bearing potential will be screened for pregnancy before imaging).
Minimum Eligible Age

40 Years

Maximum Eligible Age

75 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Michael J. Fox Foundation for Parkinson's Research

OTHER

Sponsor Role collaborator

The Silverstein Foundation for Parkinson's with GBA

UNKNOWN

Sponsor Role collaborator

Northwell Health

OTHER

Sponsor Role lead

Responsible Party

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David Eidelberg

Professor & Head, Feinstein Center for Neurosciences, Feinstein Institutes for Medical Research

Responsibility Role PRINCIPAL_INVESTIGATOR

Principal Investigators

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David Eidelberg, MD

Role: PRINCIPAL_INVESTIGATOR

Head, Center for Neurosciences

Locations

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Feinstein Institutes for Medical Research

Manhasset, New York, United States

Site Status

Countries

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United States

References

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Other Identifiers

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MJFF grant 16325

Identifier Type: -

Identifier Source: org_study_id