Efficacy and Safety of IgPro10 in Adults With Systemic Sclerosis (SSc)

NCT ID: NCT04138485

Last Updated: 2020-11-17

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

WITHDRAWN

Clinical Phase

PHASE2

Study Classification

INTERVENTIONAL

Study Start Date

2019-12-20

Study Completion Date

2020-09-16

Brief Summary

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This randomized, multicenter, double-blind (DB), placebo controlled, phase 2 study will evaluate the efficacy and safety of IgPro10. The DB Treatment Period will be followed by a 24-week Open-label (OL) Treatment Period.

Eligible subjects will be randomized at Baseline in a 2:1 ratio of treatment IgPro10 or placebo in the DB Treatment Period. All subjects who enter OL Treatment Period will receive IgPro10.

Detailed Description

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Conditions

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Diffuse Cutaneous Systemic Sclerosis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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IgPro10

10% liquid formulation of human immunoglobulin for intravenous use

Group Type EXPERIMENTAL

IgPro10

Intervention Type BIOLOGICAL

10% liquid formulation of human immunoglobulin for IVIG

Placebo

0.5% human albumin solution stabilized with 250 mmol/L L-proline

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type BIOLOGICAL

0.5% human albumin solution stabilized with 250 mmol/L L-proline

Interventions

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IgPro10

10% liquid formulation of human immunoglobulin for IVIG

Intervention Type BIOLOGICAL

Placebo

0.5% human albumin solution stabilized with 250 mmol/L L-proline

Intervention Type BIOLOGICAL

Other Intervention Names

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Human normal immunoglobulin Albumin

Eligibility Criteria

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Inclusion Criteria

* 1\. Age ≥18 years (male or female) at time of providing written informed consent
* Documented diagnosis of SSc according to ACR / EULAR criteria 2013
* mRSS ≥ 15 and ≤ 45
* Disease duration ≤ 5 years defined as the time from the first non-Raynaud's phenomenon manifestation
* Subjects within first 18 months of disease duration from first non-Raynaud's phenomenon manifestation.

Exclusion Criteria

* Primary rheumatic autoimmune disease other than dcSSc, including but not limited to rheumatoid arthritis, systemic lupus erythematosus, mixed connective tissue disorder, polymyositis, and dermatomyositis, as determined by the investigator Note: Subjects with fibromyalgia, secondary Sjogren's syndrome, and scleroderma-associated myopathy or myositis at Screening are not excluded
* Positive anti-centromere autoantibodies at Screening
* Evidence of severe chronic kidney disease with estimated glomerular filtration rate \< 45 mL/min/1.73 m2 (as calculated by the Chronic Kidney Disease Epidemiology Collaboration equation) or receiving dialysis. Additionally, subjects with current confirmed diagnosis of diabetes mellitus and requiring medication, with eGFR \< 90 mL/min/1.73m2 will be excluded from the study.
* History of documented thrombotic episode eg, PE, DVT, myocardial infarction, thromboembolic stroke at any time Note: past superficial thrombophlebitis more than two years from Screening is not exclusionary
* Documented thrombophilic abnormalities including blood hyperviscosity, protein S or protein C deficiency, anti-thrombin-3 deficiency, plasminogen deficiency, antiphospholipid syndrome, Factor V Leiden mutation, dysfibrinogenemia, or prothrombin G20210A mutation
* Greater than 3 specified current risk factors for TEEs (documented and currents conditions): atrial fibrillation, coronary disease, diabetes mellitus, dyslipidemia, hypertension, obesity (Body Mass Index ≥ 30 kg/m2), recent significant trauma, and immobility (wheelchair-bound or bedridden)
* Ongoing active serious infection at Screening (including, but not limited to, pneumonia, bacteremia/septicemia, osteomyelitis/septic arthritis, bacterial meningitis, or visceral abscess)
* Malignancy in the past 2 years, except for non-melanoma skin cancer, cervical carcinoma in situ, or other in situ cancer if it has been excised and treated within in the past year
* Known hypoalbuminemia, protein-losing enteropathies, and any proteinuria (defined by total urine protein concentration \> 0.2 g/L)
* Known IgA deficiency or serum IgA level \< 5% lower limit of normal
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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CSL Behring

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Study Director

Role: STUDY_DIRECTOR

CSL Behring

Locations

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Mayo Clinic Arizona - Scottsdale

Scottsdale, Arizona, United States

Site Status

Pacific Arthritis Care Center

Los Angeles, California, United States

Site Status

University of California

Los Angeles, California, United States

Site Status

Stanford University Medical Center

Palo Alto, California, United States

Site Status

University of Colorado

Aurora, Colorado, United States

Site Status

Lombardi Cancer Center-Georgetown University

Washington D.C., District of Columbia, United States

Site Status

Alliance for Multispecialty Research

Wichita, Kansas, United States

Site Status

Heartland Research Associates, LLC

Wichita, Kansas, United States

Site Status

Louisiana State University Health Sciences Center

Shreveport, Louisiana, United States

Site Status

John Hopkins Bayview Medical Center

Baltimore, Maryland, United States

Site Status

Boston University Amyloidosis Center

Boston, Massachusetts, United States

Site Status

University of Michigan Health System

Ann Arbor, Michigan, United States

Site Status

Rutgers Clinical Research Center

New Brunswick, New Jersey, United States

Site Status

Northwell Health

Great Neck, New York, United States

Site Status

Hospital For Special Surgery

New York, New York, United States

Site Status

Cleveland Clinic - Taussig Cancer Center

Cleveland, Ohio, United States

Site Status

Altoona Center For Research

Duncansville, Pennsylvania, United States

Site Status

University of Pennsylvania - Perelman Center

Philadelphia, Pennsylvania, United States

Site Status

Medical University of South Carolina

Charleston, South Carolina, United States

Site Status

The University Of Texas Medical School At Houston (Utms)

Houston, Texas, United States

Site Status

APRILLUS Asistencia e Investigacion Clinica

Buenos Aires, , Argentina

Site Status

Hospital Militar Central

Buenos Aires, , Argentina

Site Status

Hospital Italiano de Buenos Aires

Buenos Aires, , Argentina

Site Status

Sanatorio Parque S.A y Consultorios Externos Asociados

Rosario, , Argentina

Site Status

John Hunter Hospital / Autoimmune Resource and Research Centre

New Lambton Heights, New South Wales, Australia

Site Status

PARC Clinical Research

Adelaide, South Australia, Australia

Site Status

UZ Gent

Ghent, , Belgium

Site Status

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

Leuven, , Belgium

Site Status

Mount Sinai Hospital, The Rebecca Macdonald Centre For Arthritis

Toronto, , Canada

Site Status

CHU de Caen

Caen, , France

Site Status

CHRU de Lille Hopital Huriez

Lille, , France

Site Status

Internal Medicine, Nantes University Hospital

Nantes, , France

Site Status

Assistance Publique - Hopitaux de Paris (AP-HP)

Paris, , France

Site Status

CHU de Rennes-Hopital Sud

Rennes, , France

Site Status

Centre Hospitalier Universitaire de Rouen-Hopital

Rouen, , France

Site Status

CHU Hautepierre

Strasbourg, , France

Site Status

Kerckhoff Klinik GmbH, Abteilung für Rheumatologie und Klinische Immunologie Rheumatologie

Bad Nauheim, , Germany

Site Status

Charite - Universitaetsmedizin Berlin - Campus Charite Mitte

Berlin, , Germany

Site Status

Universitaetsmedizin Berlin - Campus Charite Mitte (CCM)

Berlin, , Germany

Site Status

University Hospital of Cologne

Cologne, , Germany

Site Status

Universitaetsklinikum Freiburg- Klinik fuer Rheumatologie und Klinische Immunologie

Freiburg im Breisgau, , Germany

Site Status

Universitaetsmedizin der Johannes Gutenberg

Mainz, , Germany

Site Status

University Hospital Of Tuebingen

Tübingen, , Germany

Site Status

Universitaetsklinikum Ulm

Ulm, , Germany

Site Status

Hospital St. Josef

Wuppertal, , Germany

Site Status

Universita degli Study di Ancona

Ancona, , Italy

Site Status

Universita Degli Studi Di Bari Aldo Moro

Bari, , Italy

Site Status

Universita degli Studi Di Brescia

Brescia, , Italy

Site Status

Universita degli Studi Firenze

Florence, , Italy

Site Status

UOC Immunoreumatologia

L’Aquila, , Italy

Site Status

Azienda Ospedaliera Gaetano Pini

Milan, , Italy

Site Status

Modena University

Modena, , Italy

Site Status

Universita degli Studi di Napoli Federico II

Napoli, , Italy

Site Status

IRCCS Policlinico San Matteo

Pavia, , Italy

Site Status

Dip.to Med. Sperimentale -Polic.Umberto I -Univ. La Sapienza

Rome, , Italy

Site Status

Centro Integral en Reumatologia, SA de CV

Guadalajara, , Mexico

Site Status

Centro De Estudios De Investigation Basica Y Clinica S.C

Jalisco, , Mexico

Site Status

Cliditer, S.A. DE C.V.

Mexico City, , Mexico

Site Status

Centro de Investigacion y Tratamiento Reumatologico S.C.

Mexico City, , Mexico

Site Status

Instituto Nacional De Ciencias Medicas Y Nutricion

México, , Mexico

Site Status

Centro de Alta Especialidad en Reumatologia

San Luis Potosí City, , Mexico

Site Status

Uniwersytecki Szpital Kliniczny W Bialymstoku

Bialystok, , Poland

Site Status

University Clinical Centre, Medical University of Gdansk

Gdansk, , Poland

Site Status

Samodzielny Publiczny Szpital Kliniczny

Katowice, , Poland

Site Status

Klinika Dermatologii Szpital im. Dzieciątka Jezus

Warsaw, , Poland

Site Status

Klinika i Poliklinika Układowych Chorób Tkanki Łącznej Narodowy Instytut Geriatrii, Reumatologii i Rehabilitacji

Warsaw, , Poland

Site Status

Complejo Hospitalario Universitario A Coruna

A Coruña, , Spain

Site Status

Hospital Universitari Materno Infantil Vall Dhebron

Barcelona, , Spain

Site Status

Hospital de la Santa Creu i Sant Pau

Barcelona, , Spain

Site Status

Hospital General Universitario Gregorio Maranon

Madrid, , Spain

Site Status

Hospital Univ 12 de Octubre

Madrid, , Spain

Site Status

Hospital Infanta Luisa Quirónsalud

Seville, , Spain

Site Status

Hospital Universitari Dr.Peset

Valencia, , Spain

Site Status

Cantonal Hospital St. Gallen - Klinik fuer Rheumatologie

Sankt Gallen, , Switzerland

Site Status

Countess of Chester Hospital

Chester, , United Kingdom

Site Status

Chapel Allerton Hospital

Leeds, , United Kingdom

Site Status

Royal Free Hospital-Royal Free London NHS Foundation Trust

London, , United Kingdom

Site Status

Countries

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United States Argentina Australia Belgium Canada France Germany Italy Mexico Poland Spain Switzerland United Kingdom

Other Identifiers

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2019-000906-31

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

IgPro10_2001

Identifier Type: -

Identifier Source: org_study_id