A Study of Repotrectinib in Pediatric and Young Adult Subjects Harboring ALK, ROS1, OR NTRK1-3 Alterations

NCT ID: NCT04094610

Last Updated: 2025-11-19

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

75 participants

Study Classification

INTERVENTIONAL

Study Start Date

2020-03-12

Study Completion Date

2027-09-30

Brief Summary

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Phase 1 will evaluate the safety and tolerability at different dose levels of repotrectinib in pediatric and young adult subjects with advanced or metastatic malignancies harboring anaplastic lymphoma kinase (ALK), receptor tyrosine kinase encoded by the gene ROS1 (ROS1), or neurotrophic receptor kinase genes encoding TRK kinase family (NTRK1-3) alterations to estimate the Maximum Tolerated Dose (MTD) or Maximum Administered Dose (MAD) and select the Pediatric Recommended Phase 2 Dose (RP2D).

Phase 2 will determine the anti-tumor activity of repotrectinib in pediatric and young adult subjects with advanced or metastatic malignancies harboring ROS1 or NTRK1-3 alterations.

Detailed Description

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Enrollment of subjects into Phase 1 will proceed concurrently by age as follows:

* Subjects \<12 years old will initially be enrolled in the Phase 1 part to determine the pediatric RP2D for this age group; once the pediatric RP2D is determined, subjects age \<12 years old may be enrolled into the Phase 2 part of the study.
* Subjects 12 to 25 years old will be directly enrolled into the Phase 2 part concurrent with Phase 1 enrollment.

Phase 1:

Approximately 12 pediatric subjects with locally advanced or metastatic solid tumors, including a primary central nervous system (CNS) tumor, or anaplastic large cell lymphoma (ALCL), with disease progression or who are non-responsive or intolerant to available therapies and for which no standard or available curative therapy exists.

Phase 2:

Subjects will be enrolled in one of 3 cohorts as follows:

Cohort 1: approximately 10-20 subjects with solid tumors characterized by NTRK fusion, TRK tyrosine kinase inhibitor (TKI)-naïve, and centrally confirmed measurable disease at baseline.

Cohort 2: approximately 23 subjects with solid tumors characterized by NTRK fusion, TRK TKI-pretreated, and centrally confirmed measurable disease at baseline.

Cohort 3: approximately 20 subjects with solid tumors or ALCL characterized by other ALK/ROS1/NTRK alterations or NTRK fusions without centrally confirmed measurable disease not otherwise eligible for Cohort 1 or 2. As of the current protocol amendment, only patients with ROS1 alterations will be enrolled to this cohort.

Conditions

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Locally Advanced Solid Tumors Metastatic Solid Tumors Lymphoma Primary CNS Tumors

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Repotrectinib (TPX-0005)

Phase 1

Oral repotrectinib (TPX-0005):

Safety and tolerability at different dose levels

Phase 2

Oral repotrectinib (TPX-0005): 3 cohorts

Cohort 1: TKI-naive NTRK fusion Cohort 2: Prior TKI NTRK fusion Cohort 3: ROS1 gene fusions or other ROS1 aberrations

Group Type EXPERIMENTAL

Oral repotrectinib (TPX-0005)

Intervention Type DRUG

Oral repotrectinib (TPX-0005)

Interventions

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Oral repotrectinib (TPX-0005)

Oral repotrectinib (TPX-0005)

Intervention Type DRUG

Other Intervention Names

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Oral repotrectinib (TPX-0005) capsules Oral repotrectinib (TPX-0005) oral suspension repotrectinib

Eligibility Criteria

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Inclusion Criteria

1. Documented genetic ROS1 point mutation, fusion, or amplification or NTRK1-3 fusion as identified by local testing in a Clinical Laboratory Improvement Amendments (CLIA) laboratory in the US or equivalently accredited diagnostic lab outside the United States (US) is required.
2. Phase 1: Age \<12 years; Phase 2: Age 12- 25 years
3. Prior cytotoxic chemotherapy is allowed.
4. Prior immunotherapy is allowed.
5. Resolution of all acute toxic effects (excluding alopecia) of any prior anti-cancer therapy to National Cancer Institute Common Terminology Criteria for Adverse Events (NCI CTCAE) Version 4.03 Grade less than or equal to 1.
6. All subjects must have measurable disease by RECIST v1.1 or Response Assessment in Neuro-Oncology (RANO) criteria at time of enrollment.
7. Subjects with a primary CNS tumor or CNS metastases must be neurologically stable on a stable or decreasing dose of steroids for at least 7 days prior to enrollment.
8. Subjects must have a Lansky (\< 16 years) or Karnofsky (≥ 16 years) score of at least 50.
9. Life expectancy greater than or equal to 12 weeks, in the investigator's opinion.
10. Adequate hematologic, renal and hepatic function.



* Cohort 1: Subjects with NTRK fusion gene positive (NTRK+) advanced solid tumors (including primary CNS tumors), that are tropomyosin receptor kinase (TRK) TKI naïve;
* Cohort 2: subjects with NTRK+ advanced solid tumors (including primary CNS tumors), that are TRK TKI pre-treated;
* Cohort 3: subjects with advanced solid tumors with ROS1 gene fusions or other ROS1 aberrations (including amplifications and point mutations) with measurable disease.
2. Subjects in Cohorts 1 and 2 must have prospectively confirmed measurable disease by BICR prior to enrollment.

Exclusion Criteria

1. Subjects with neuroblastoma with only bone marrow disease evaluable by bone marrow aspiration only.
2. Major surgery within 14 days (2 weeks) of start of repotrectinib treatment. Central venous access (Broviac, Mediport, etc.) placement does not meet criteria for major surgery.
3. Known active infections requiring ongoing treatment (bacterial, fungal, viral including HIV positivity).
4. Gastrointestinal disease (e.g., Crohn's disease, ulcerative colitis, or short gut syndrome) or other malabsorption syndromes that would impact drug absorption.
5. Any of the following cardiac criteria:

* Mean resting corrected QT interval (ECG interval measured from the onset of the QRS complex to the end of the T wave) for heart rate (QTc) \> 480 msec obtained from three ECGs, using the screening clinic ECG machine-derived QTc value
* Any clinically important abnormalities in rhythm, conduction, or morphology of resting ECG (e.g., complete left bundle branch block, third degree heart block, second degree heart block, PR interval \> 250 msec)
* Any factors that increase the risk of QTc prolongation or risk of arrhythmic events such as heart failure, congenital long QT syndrome, family history of long QT syndrome, or any concomitant medication known to prolong the QT interval
6. Peripheral neuropathy of CTCAE ≥grade 2.
7. Subjects being treated with or anticipating the need for treatment with strong CYP3A4 inhibitors or inducers.
8. Any potential allergies to repotrectinib and/or its excipients.
Maximum Eligible Age

25 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Turning Point Therapeutics, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Bristol-Myers Squibb

Role: STUDY_DIRECTOR

Bristol-Myers Squibb

Locations

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Children's Hospital Los Angeles

Los Angeles, California, United States

Site Status RECRUITING

University of California at Los Angeles

Los Angeles, California, United States

Site Status RECRUITING

Children's Hospital Colorado - Anschutz Medical Campus

Aurora, Colorado, United States

Site Status RECRUITING

Local Institution - 2105

Orlando, Florida, United States

Site Status COMPLETED

Local Institution - 2120

Orlando, Florida, United States

Site Status COMPLETED

Children's Healthcare of Atlanta - Egleston Hospital

Atlanta, Georgia, United States

Site Status RECRUITING

Maine Medical Center

Scarborough, Maine, United States

Site Status RECRUITING

Dana Farber Cancer Institute.

Boston, Massachusetts, United States

Site Status RECRUITING

Washington University School of Medicine in St. Louis

St Louis, Missouri, United States

Site Status RECRUITING

Local Institution - 2110

New Brunswick, New Jersey, United States

Site Status COMPLETED

Local Institution - 2102

New York, New York, United States

Site Status COMPLETED

Levine Children's Hospital- Pediatric Neuro-Oncology

Charlotte, North Carolina, United States

Site Status RECRUITING

Local Institution - 2112

Cleveland, Ohio, United States

Site Status COMPLETED

Local Institution - 2114

Hershey, Pennsylvania, United States

Site Status COMPLETED

Children's Hospital of Philadelphia-Center for Childhood Cancer Research

Philadelphia, Pennsylvania, United States

Site Status RECRUITING

St. Jude Children's Research Hospital

Memphis, Tennessee, United States

Site Status RECRUITING

The University of Texas Southwestern Medical Center - Harold C Simmons Comprehensive Cancer Center

Dallas, Texas, United States

Site Status RECRUITING

Baylor College of Medicine

Houston, Texas, United States

Site Status RECRUITING

Local Institution - 2104

Houston, Texas, United States

Site Status COMPLETED

Children's Hospital of Richmond at VCU

Richmond, Virginia, United States

Site Status WITHDRAWN

Local Institution - 6104

Randwick, New South Wales, Australia

Site Status RECRUITING

Local Institution - 6103

Westmead, New South Wales, Australia

Site Status COMPLETED

Children's Health Queensland Hospital and Health Service

South Brisbane, Queensland, Australia

Site Status RECRUITING

Perth Childrens Hospital

Nedlands, Western Australia, Australia

Site Status RECRUITING

University Of Calgary

Calgary, Alberta, Canada

Site Status RECRUITING

Stollery Children'S Hospital

Edmonton, Alberta, Canada

Site Status RECRUITING

Children'S Hospital Of Eastern Ontario

Ottawa, Ontario, Canada

Site Status RECRUITING

St Justine Hospital

Montreal, Quebec, Canada

Site Status RECRUITING

Rigshospitalet - Glostrup

Copenhagen, , Denmark

Site Status RECRUITING

Local Institution - 6111

Lyon, Rhone, France

Site Status NOT_YET_RECRUITING

Centre Hospitalier Universitaire D'Angers

Angers, , France

Site Status RECRUITING

Centre Hospitalier Universitaire de Bordeaux - Groupe Hospitalier Pellegrin

Bordeaux, , France

Site Status RECRUITING

Institut d Hematologie et d Oncologie Pediatriques

Lyon, , France

Site Status RECRUITING

Hôpitaux Universitaires de Marseille Timone

Marseille, , France

Site Status RECRUITING

Local Institution - 6110

Marseille, , France

Site Status NOT_YET_RECRUITING

Local Institution - 6112

Nantes, , France

Site Status NOT_YET_RECRUITING

Local Institution - 6109

Paris, , France

Site Status NOT_YET_RECRUITING

Institut Gustave-Roussy

Villejuif, , France

Site Status RECRUITING

Local Institution - 6108

Villejuif, , France

Site Status NOT_YET_RECRUITING

Fondazione IRCCS - Istituto Nazionale dei Tumori

Milan, , Italy

Site Status RECRUITING

Local Institution - 6113

Padua, , Italy

Site Status WITHDRAWN

Local Institution - 4302

Rome, , Italy

Site Status NOT_YET_RECRUITING

Local Institution - 6114

Torino, , Italy

Site Status WITHDRAWN

National University Hospital

Singapore, , Singapore

Site Status RECRUITING

KK Women's and Children's Hospital

Singapore, , Singapore

Site Status RECRUITING

Local Institution - 6303

Seoul, Seodaemun-gu, South Korea

Site Status COMPLETED

Seoul National University Hospital

Seoul, , South Korea

Site Status RECRUITING

Asan Medical Center

Seoul, , South Korea

Site Status RECRUITING

Local Institution - 6304

Seoul, , South Korea

Site Status COMPLETED

Hospital Sant Joan De Deu

Esplugues de Llobregat, Barcelona, Spain

Site Status RECRUITING

Clínica Universidad de navarra

Pamplona, Navarre, Spain

Site Status RECRUITING

Local Institution - 6105

Barcelona, , Spain

Site Status NOT_YET_RECRUITING

Hospital Universitari Vall d'Hebron

Barcelona, , Spain

Site Status RECRUITING

Hospital Infantil Universitario Nino Jesus

Madrid, , Spain

Site Status RECRUITING

Local Institution - 6106

Madrid, , Spain

Site Status NOT_YET_RECRUITING

Clinica Universidad de Navarra

Madrid, , Spain

Site Status RECRUITING

HM Sanchinarro University Hospital

Madrid, , Spain

Site Status RECRUITING

Hospital Universitario Virgen del Rocio

Seville, , Spain

Site Status RECRUITING

Hospital Universitario Y Politecnico La Fe

Valencia, , Spain

Site Status RECRUITING

Local Institution - 6107

Valencia, , Spain

Site Status NOT_YET_RECRUITING

National Taiwan University Hospital

Taipei, , Taiwan

Site Status RECRUITING

Taipei Medical University Hospital

Taipei, , Taiwan

Site Status RECRUITING

Alder Hey Children's NHS Foundation Trust

Liverpool, England, United Kingdom

Site Status RECRUITING

Local Institution - 4403

Birmingham, , United Kingdom

Site Status COMPLETED

University Hospital of Wales

Cardiff, , United Kingdom

Site Status RECRUITING

Royal Hosp. for Children

Glasgow, , United Kingdom

Site Status RECRUITING

The Royal Marsden NHS Foundation Trust

London, , United Kingdom

Site Status RECRUITING

Great Ormond Street Hospital For Children NHS Foundation Trust

London, , United Kingdom

Site Status RECRUITING

Countries

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United States Australia Canada Denmark France Italy Singapore South Korea Spain Taiwan United Kingdom

Central Contacts

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BMS Study Connect Contact Center www.BMSStudyConnect.com

Role: CONTACT

855-907-3286

First line of the email MUST contain the NCT# and Site #.

Role: CONTACT

Facility Contacts

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Leo Mascarenhas, Site 2111

Role: primary

323-361-5418

Noah Federman, Site 2109

Role: primary

310-206-7625

Margaret Macy, Site 2108

Role: primary

720-777-8856

Tobey Macdonald, Site 2119

Role: primary

000-000-0000

Stanley Chaleff, Site 2115

Role: primary

207-396-7565

Steven Dubois, Site 2106

Role: primary

415-476-3831

Andrew Cluster, Site 2113

Role: primary

443-745-4180

Chad Jacobsen, Site 2121

Role: primary

000-000-0000

Theodore Laetsch, Site 2117

Role: primary

267-425-5544

Alberto Pappo, Site 2103

Role: primary

901-595-3300

Tanya Carens Watt, Site 2101

Role: primary

Matthew McEvoy, Site 2118

Role: primary

Site 6104

Role: primary

Timothy Hassall, Site 6102

Role: primary

61730681111

Nick Gottardo, Site 6101

Role: primary

Victor Lewis, Site 2202

Role: primary

14039557203

Sunil desai, Site 2201

Role: primary

17802485415

Lesleigh Abbott, Site 2203

Role: primary

61373776002370

Sebastien Perreault, Site 2205

Role: primary

4384958893

Karsten Nysom, Site 4901

Role: primary

4535450809

Site 6111

Role: primary

Emilie De Carli, Site 4203

Role: primary

0241353863

Stephane Ducassou, Site 4201

Role: primary

0557820438

Nadege Corradini, Site 4204

Role: primary

33478782642

Nicolas Andre, Site 4205

Role: primary

33491386821

Site 6110

Role: primary

Site 6112

Role: primary

Site 6109

Role: primary

Samuel Abbou, Site 4202

Role: primary

142114211

Site 6108

Role: primary

Michela Casanova, Site 4301

Role: primary

390223902593

Site 4302

Role: primary

Allen Yeoh, Site 6401

Role: primary

67724406

Shui Yen Soh, Site 6402

Role: primary

6563941045

Hyoung Jin Kang, Site 6301

Role: primary

82220723304

Kyung Nam Koh, Site 6302

Role: primary

+82230105994

Alicia Castaneda Heredia, Site 4106

Role: primary

34932532100

Elena Panizo Morgado, Site 4102

Role: primary

34913531920

Site 6105

Role: primary

Maria Paula Perez Albert, Site 4103

Role: primary

Alvaro Lassaletta, Site 4105

Role: primary

+34915035938

Site 6106

Role: primary

Elena Panizo Morgado, Site 4101

Role: primary

34913531920

Marta Osuna Marco, Site 4104

Role: primary

34917089935

Jose Luis Moreno, Site 4108

Role: primary

955012000

Antonio Juan Ribelles, Site 4107

Role: primary

961244190

Site 6107

Role: primary

Shiann-Tarng Jou, Site 6202

Role: primary

886223123456x71716

Yen-Lin Liu, Site 6201

Role: primary

886970749572

Lisa Howell, Site 4404

Role: primary

+441512933679

Madeleine Adams, Site 4401

Role: primary

02920742107

Milind Ronghe, Site 4406

Role: primary

Linley Marchall, Site 4405

Role: primary

209156161

Elwira Szychot, Site 4402

Role: primary

447849760509

References

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Wachter F, Al-Ibraheemi A, Trissal MC, Hollowell M, DuBois SG, Collins NB, Church AJ, Janeway KA. Molecular Characterization of Inflammatory Tumors Facilitates Initiation of Effective Therapy. Pediatrics. 2021 Dec 1;148(6):e2021050990. doi: 10.1542/peds.2021-050990.

Reference Type DERIVED
PMID: 34814185 (View on PubMed)

Related Links

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Other Identifiers

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CA127-1029

Identifier Type: OTHER

Identifier Source: secondary_id

TPX-0005-07

Identifier Type: OTHER

Identifier Source: secondary_id

CA127-1029

Identifier Type: -

Identifier Source: org_study_id

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