A Gene Transfer Study for Late-Onset Pompe Disease (RESOLUTE)

NCT ID: NCT04093349

Last Updated: 2024-11-27

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

4 participants

Study Classification

INTERVENTIONAL

Study Start Date

2020-10-01

Study Completion Date

2032-04-30

Brief Summary

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The purpose of this study is to evaluate the safety, tolerability, and efficacy of a single intravenous infusion of SPK-3006 in adults with clinically moderate, late-onset Pompe disease receiving enzyme replacement therapy (ERT). Participants will be treated in sequential, dose-level cohorts.

Detailed Description

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Conditions

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Pompe Disease Pompe Disease (Late-onset) Glycogen Storage Disease Type 2 Glycogen Storage Disease Type II LOPD Lysosomal Storage Diseases Acid Maltase Deficiency

Study Design

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Allocation Method

NA

Intervention Model

SEQUENTIAL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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SPK-3006

All participants who meet the eligibility criteria will receive a single intravenous (i.v.) administration of SPK-3006.

Group Type EXPERIMENTAL

SPK-3006

Intervention Type GENETIC

adeno-associated viral (AAV) vector

Interventions

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SPK-3006

adeno-associated viral (AAV) vector

Intervention Type GENETIC

Eligibility Criteria

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Inclusion Criteria

* Provide written informed consent;
* Males and Females ≥18 years of age with late-onset Pompe disease;
* Received ERT for at least the previous 24 months
* Have clinically moderate, late-onset Pompe disease characteristics;
* Agree to use reliable contraception.

Exclusion Criteria

* Active hepatitis B and/or C;
* Significant underlying liver disease;
* Human immunodeficiency virus (HIV) infection;
* Prior hypersensitivity to rhGAA;
* Pre-existing anti-AAV neutralizing antibody titers;
* High titer antibody responses to rhGAA;
* Requires any invasive ventilation or requires noninvasive ventilation while awake and upright;
* Received any prior vector or gene transfer agent;
* Active malignancy (except non-melanoma skin cancer);
* History of liver cancer;
* Pregnant or nursing women;
* Any evidence of active infection at the time of SPK-3006 infusion.
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Spark Therapeutics, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Tahseen Mozaffar, MD

Role: PRINCIPAL_INVESTIGATOR

University of California Irvine Health

Locations

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Barrow Neurological Institute

Phoenix, Arizona, United States

Site Status

University of California Irvine Health

Orange, California, United States

Site Status

Emory University School of Medicine

Atlanta, Georgia, United States

Site Status

University of Kansas Medical Center Research Institute

Kansas City, Kansas, United States

Site Status

University of Minnesota

Minneapolis, Minnesota, United States

Site Status

Oregon Health & Science University

Portland, Oregon, United States

Site Status

University of Pennsylvania

Philadelphia, Pennsylvania, United States

Site Status

University of Pittsburgh Medical Center

Pittsburgh, Pennsylvania, United States

Site Status

University of Utah

Salt Lake City, Utah, United States

Site Status

Lysosomal and Rare Disorders Research & Treatment Center

Fairfax, Virginia, United States

Site Status

Vancouver General Hospital

Vancouver, British Columbia, Canada

Site Status

The Ottawa Hospital

Ottawa, Ontario, Canada

Site Status

Montreal Neurological Hospital

Montreal, Quebec, Canada

Site Status

Rigshospitalet

Copenhagen, , Denmark

Site Status

Centre Hospitalier Universitaire d'Angers

Angers, , France

Site Status

CHU Paris IdF Ouest - Hôpital Raymond Poincaré

Garches, , France

Site Status

Centre Hospitalier Régional Universitaire de Lille

Lille, , France

Site Status

Assistance Publique Hôpitaux de Marseille

Marseille, , France

Site Status

Nice University Hospital

Nice, , France

Site Status

Friedrich-Baur-Institut Neurologische Klinik Ludwig-Maximilians-Universität München

München, , Germany

Site Status

Universita Degli Studi Di Messina - Dipartimento di Medicina Clinica e Sperimentale

Messina, , Italy

Site Status

Universita Degli Studi Di Milano, Laboratorio di Biochimica e Genetica della Malattie Neuromuscolari

Milan, , Italy

Site Status

Malattie Metaboliche Universita Degli Studi Di Napoli Federico II

Naples, , Italy

Site Status

UO Neurologia Azienda Ospedaliera Universitaria Pisana

Pisa, , Italy

Site Status

Azienda Ospedaliera Universitaria Città della Salute e della Scienza di Torino - Neurology, Osp. Molinette

Torino, , Italy

Site Status

Erasmus Medical Center

Rotterdam, , Netherlands

Site Status

New Queen Elizabeth Hospital Birmingham

Birmingham, GBR, United Kingdom

Site Status

The Royal Free London NHS Foundation Trust

London, GBR, United Kingdom

Site Status

Salford Royal MHS Foundation Trust

Salford, , United Kingdom

Site Status

Countries

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United States Canada Denmark France Germany Italy Netherlands United Kingdom

Other Identifiers

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2019-001283-30

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

SPK-3006-101

Identifier Type: -

Identifier Source: org_study_id

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