A Study to Evaluate the Efficacy and Safety of Pegcetacoplan in Patients With PNH

NCT ID: NCT04085601

Last Updated: 2022-10-21

Study Results

Results available

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE3

Total Enrollment

53 participants

Study Classification

INTERVENTIONAL

Study Start Date

2019-08-27

Study Completion Date

2021-06-23

Brief Summary

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Evaluation of the Efficacy and Safety of Pegcetacoplan in Patients with Paroxysmal Nocturnal Hemoglobinuria .

Detailed Description

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Conditions

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Paroxysmal Nocturnal Hemoglobinuria

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Standard of Care (SOC) excluding complement inhibitors

Group Type NO_INTERVENTION

No interventions assigned to this group

1,080mg APL-2 administered subcutaneously twice weekly

Group Type EXPERIMENTAL

APL-2

Intervention Type DRUG

Complement (C3) Inhibitor

Interventions

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APL-2

Complement (C3) Inhibitor

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

* Be at least 18 years old (inclusive).
* Have LDH ≥1.5 x ULN at the screening visit.
* Have PNH diagnosis, confirmed by high sensitivity flow cytometry (granulocyte or monocyte clone \>10%).
* Have Hb less than the lower limit of normal (LLN) at the screening visit.
* Have ferritin greater than/equal to the LLN, or total iron binding capacity (TIBC) less than/equal to ULN at the screening visit, based on central laboratory reference ranges. If a subject is receiving iron supplements at screening, the Investigator must ensure that the subject's dose has been stable for 4 weeks prior to screening, and it must be maintained throughout the study. Subjects not receiving iron at screening must not start iron supplementation during the course of the study.
* Body mass index (BMI) ≤ 35 kg/m2 at the screening visit.
* Have a platelet count of \>50,000/mm3 at the screening visit.
* Have an absolute neutrophil count \>500/mm3 at the screening visit.

Exclusion Criteria

* Treatment with any complement inhibitor (eg, eculizumab) within 3 months prior to screening.
* Hereditary complement deficiency.
* History of bone marrow transplantation.
* Concomitant use of any of the following medications is prohibited if not on a stable regimen for the time period indicated below prior to screening:

* Erythropoietin or immunosuppressants for at least 8 weeks
* Systemic corticosteroids for at least 4 weeks
* Vitamin K antagonists (eg, warfarin) with a stable international normalized ratio (INR) for at least 4 weeks
* Iron supplements, vitamin B12, or folic acid for at least 4 weeks
* Low-molecular-weight heparin for at least 4 weeks
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Apellis Pharmaceuticals, Inc.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Julian Coronel Medical Center

Cali, , Colombia

Site Status

Research Center of the Colombian Clinical Life Cancer Foundation

Medellín, , Colombia

Site Status

Queen Mary Hospital

Hong Kong, , Hong Kong

Site Status

Princess Margaret Hospital

Kwai Chung, , Hong Kong

Site Status

Prince and Wales Hospital

Shatin, , Hong Kong

Site Status

Hospital Ampang

Ampang, Selangor, Malaysia

Site Status

University Malaya Medical Centre

Kuala Lumpur, , Malaysia

Site Status

Hospital Universitario Dr.Jose Eleuterio Gonzalez

Monterrey, , Mexico

Site Status

Hospital Cayetano Heredia

San Martín de Porres, Lima region, Peru

Site Status

Hospital Cayetano Heredia

Jesús María, Lima, Peru

Site Status

Hospital Nacional Dos de Mayo

Lima, , Peru

Site Status

Baguio General Hospital

Benguet, , Philippines

Site Status

Perpetual Succour Hospital

Cebu City, , Philippines

Site Status

Mary Mediatrix Medical Center

Lipa City, , Philippines

Site Status

Makati Medical Centre

Makati City, , Philippines

Site Status

The Medical City

Pasig, , Philippines

Site Status

St. Lukes Medical Centre

Quezon City, , Philippines

Site Status

Independent Public Clinical Hospital

Lubin, , Poland

Site Status

Institute of Hematology and Transfusiology

Warsaw, , Poland

Site Status

EMC Medical Institute

Wroclaw, , Poland

Site Status

Clinical Centre of Serbia

Belgrade, , Serbia

Site Status

Singapore General Hospital (SGH)

Singapore, , Singapore

Site Status

Ramathibodi Hospital

Bangkok, , Thailand

Site Status

Siriraj Hospital

Bangkok, , Thailand

Site Status

Hospital for Tropical disease

Bangkok, , Thailand

Site Status

Phramongkutklao Hospital

Bangkok, , Thailand

Site Status

Maharaj Nakorn Chiang Mai Hospital

Chiang Mai, , Thailand

Site Status

Srinagaring Hospital

Khon Kaen, , Thailand

Site Status

Thammasat University Hospital

Pathum Thani, , Thailand

Site Status

Songklanagaring Hospital

Songkhla, , Thailand

Site Status

Countries

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Colombia Hong Kong Malaysia Mexico Peru Philippines Poland Serbia Singapore Thailand

References

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de Castro C, Kelly RJ, Griffin M, Patriquin CJ, Mulherin B, Hochsmann B, Selvaratnam V, Wong RSM, Hillmen P, Horneff R, Uchendu UO, Zhang Y, Surova E, Szamosi J, de Latour RP. Efficacy and Safety Maintained up to 3 Years in Adults with Paroxysmal Nocturnal Hemoglobinuria Receiving Pegcetacoplan. Adv Ther. 2025 Sep;42(9):4641-4658. doi: 10.1007/s12325-025-03310-8. Epub 2025 Jul 28.

Reference Type DERIVED
PMID: 40720060 (View on PubMed)

Panse J, Daguindau N, Okuyama S, Peffault de Latour R, Schafhausen P, Straetmans N, Al-Adhami M, Persson E, Wong RSM. Improvements in hematologic markers and decreases in fatigue with pegcetacoplan for patients with paroxysmal nocturnal hemoglobinuria and mild or moderate anemia (hemoglobin >/=10 g/dL) who had received eculizumab or were naive to complement inhibitors. PLoS One. 2024 Jul 29;19(7):e0306407. doi: 10.1371/journal.pone.0306407. eCollection 2024.

Reference Type DERIVED
PMID: 39079163 (View on PubMed)

Mulherin BP, Yeh M, Al-Adhami M, Dingli D. Normalization of Hemoglobin, Lactate Dehydrogenase, and Fatigue in Patients with Paroxysmal Nocturnal Hemoglobinuria Treated with Pegcetacoplan. Drugs R D. 2024 Jun;24(2):169-177. doi: 10.1007/s40268-024-00463-9. Epub 2024 May 10.

Reference Type DERIVED
PMID: 38727860 (View on PubMed)

Fishman J, Wilson K, Drzewiecka A, Pochopien M, Dingli D. The cost-effectiveness of pegcetacoplan in complement treatment-naive adults with paroxysmal nocturnal hemoglobinuria in the USA. J Comp Eff Res. 2023 Oct;12(10):e230055. doi: 10.57264/cer-2023-0055. Epub 2023 Sep 1.

Reference Type DERIVED
PMID: 37655691 (View on PubMed)

Wojciechowski P, Wdowiak M, Hakimi Z, Wilson K, Fishman J, Nazir J, Toumi M. Mapping the EORTC QLQ-C30 onto the EQ-5D-5L index for patients with paroxysmal nocturnal hemoglobinuria in France. J Comp Eff Res. 2023 May;12(5):e220178. doi: 10.57264/cer-2022-0178. Epub 2023 Apr 13.

Reference Type DERIVED
PMID: 37052120 (View on PubMed)

Wong RSM, Navarro-Cabrera JR, Comia NS, Goh YT, Idrobo H, Kongkabpan D, Gomez-Almaguer D, Al-Adhami M, Ajayi T, Alvarenga P, Savage J, Deschatelets P, Francois C, Grossi F, Dumagay T. Pegcetacoplan controls hemolysis in complement inhibitor-naive patients with paroxysmal nocturnal hemoglobinuria. Blood Adv. 2023 Jun 13;7(11):2468-2478. doi: 10.1182/bloodadvances.2022009129.

Reference Type DERIVED
PMID: 36848639 (View on PubMed)

Wong R, Fishman J, Wilson K, Yeh M, Al-Adhami M, Zion A, Yee CW, Huynh L, Duh MS. Comparative Effectiveness of Pegcetacoplan Versus Ravulizumab and Eculizumab in Complement Inhibitor-Naive Patients with Paroxysmal Nocturnal Hemoglobinuria: A Matching-Adjusted Indirect Comparison. Adv Ther. 2023 Apr;40(4):1571-1589. doi: 10.1007/s12325-023-02438-9. Epub 2023 Feb 7.

Reference Type DERIVED
PMID: 36750531 (View on PubMed)

Del Pozo Martin Y. 2021 ASH annual meeting. Lancet Haematol. 2022 Feb;9(2):e92-e93. doi: 10.1016/S2352-3026(21)00384-7. Epub 2021 Dec 16. No abstract available.

Reference Type DERIVED
PMID: 34922648 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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APL2-308

Identifier Type: -

Identifier Source: org_study_id

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