Bleeding Incidence in VWD Patients Undergoing On-Demand Treatment

NCT ID: NCT04053699

Last Updated: 2023-12-07

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Total Enrollment

56 participants

Study Classification

OBSERVATIONAL

Study Start Date

2019-06-25

Study Completion Date

2021-01-31

Brief Summary

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The purpose of this study is to prospectively obtain reliable data on the bleeding and treatment pattern of patients with VWD undergoing on-demand treatment with a VWF-containing product over a period of 6 months. The data obtained will be used as a basis for historical comparisons with the bleeding and treatment pattern obtained from a clinical study on the efficacy of prophylactic treatment with a VWF/FVIII concentrate.

Detailed Description

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Conditions

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Von Willebrand Diseases

Study Design

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Observational Model Type

COHORT

Study Time Perspective

PROSPECTIVE

Study Groups

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Patients undergoing treatment with a VWF-containing product

Patients with type 3, type 2 (except 2N), or severe type 1 VWD undergoing routine on-demand treatment with a VWF-containing product over a period of 6 months

Von Willebrand Factor-Containing Product

Intervention Type DRUG

Active substances: VWF concentrates, VWF/FVIII concentrates, Cryoprecipitate VWF-containing products licensed in each participating country

Interventions

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Von Willebrand Factor-Containing Product

Active substances: VWF concentrates, VWF/FVIII concentrates, Cryoprecipitate VWF-containing products licensed in each participating country

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

Patients who meet all of the following criteria are eligible for the study:

* Male or female patients aged ≥5.5 years at the time of enrolment
* VWD type 1 (baseline von Willebrand factor activity \[VWF:RCo\], \<30 IU/dL), 2A, 2B, 2M, or 3 according to medical history requiring substitution therapy with a VWF-containing product to control bleeding
* Currently receiving frequent on-demand treatment with a VWF-containing product
* In female patients of child-bearing potential using hormonal contraception, the medication class should remain unchanged for the duration of their study participation
* Voluntarily given, fully informed written and signed consent obtained before collection of any patient data

Exclusion Criteria

Patients who meet any of the following criteria are not eligible for the study:

* Patients currently on prophylaxis for VWD (except for perioperative prophylaxis) as well as patients having received treatment once a month for menstrual bleeding, but not for any other bleeds
* Patients whose VWD treatment is planned to be switched from on-demand to prophylactic treatment in the next 6 months
* History, or current suspicion, of VWF or FVIII inhibitors
* Medical history of a thromboembolic event within 6 months before enrolment
* Severe liver or kidney diseases as described in the medical records
* Female patients with an existing or suspected pregnancy or who are breast-feeding at the time of enrolment
* Change in hormonal contraception within 6 months before enrolment
* Cervical or uterine conditions causing abnormal uterine bleeding (including infection or dysplasia)
* Other coagulation disorders or bleeding disorders due to anatomical reasons
* Participation in an interventional clinical study during the 6-month of study period
* Inability to complete the patient diary to reliably evaluate the type, frequency, and treatment of BEs during the 6-month study period
Minimum Eligible Age

66 Months

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Octapharma

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Cristina Solomon, MD

Role: STUDY_DIRECTOR

Octapharma

Locations

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Children's Healthcare of Atlanta

Atlanta, Georgia, United States

Site Status

Republican Research Center for Radiation Medicine and Human Ecology

Homyel, , Belarus

Site Status

Specialized Hospital for Active Treatment of Haematological Diseases" EAD, Sofia

Sofia, , Bulgaria

Site Status

"UMHAT Sveta Marina" EAD.

Varna, , Bulgaria

Site Status

University Hospital Centre Zagreb

Zagreb, , Croatia

Site Status

Medical Centre Hungarian Defence Forces

Budapest, , Hungary

Site Status

Debreceni Egyetem Klinikai Központ, Regionális Haemophilia és Thrombophilia Központ

Debrecen, , Hungary

Site Status

University Clinical Center, Department of Internal Medicine, Hematology

Pécs, , Hungary

Site Status

Hotel Dieu de France Hospital

Beirut, , Lebanon

Site Status

American University of Beirut Medical Center

Beirut, , Lebanon

Site Status

Nini Hospital

Tripoli, , Lebanon

Site Status

Federal State Budgetary Scientific Institution Kirov Scientific-Research Institute of Hematology and Blood Transfusion of Federal

Kirov, , Russia

Site Status

Morosovskaya Children Clinical Hospital, Moscow Health Department, Department of General Hematology with the Pathology of Hemostasis

Moscow, , Russia

Site Status

State Institution "National Children's Specialized Hospital "OKHMATDYT" of the Ministry of Health of Ukraine," Center of Hemostasis Pathology

Kyiv, , Ukraine

Site Status

Community Institution of Lviv Oblast Council "West-Ukrainian Specialized Children's Medical Center

Lviv, , Ukraine

Site Status

Countries

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Moldova United States Belarus Bulgaria Croatia Hungary Lebanon Russia Ukraine

References

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Sadler JE. A revised classification of von Willebrand disease. For the Subcommittee on von Willebrand Factor of the Scientific and Standardization Committee of the International Society on Thrombosis and Haemostasis. Thromb Haemost. 1994 Apr;71(4):520-5.

Reference Type BACKGROUND
PMID: 8052974 (View on PubMed)

Rodeghiero F, Castaman G, Tosetto A. How I treat von Willebrand disease. Blood. 2009 Aug 6;114(6):1158-65. doi: 10.1182/blood-2009-01-153296. Epub 2009 May 27.

Reference Type BACKGROUND
PMID: 19474451 (View on PubMed)

Castaman G, Goodeve A, Eikenboom J; European Group on von Willebrand Disease. Principles of care for the diagnosis and treatment of von Willebrand disease. Haematologica. 2013 May;98(5):667-74. doi: 10.3324/haematol.2012.077263.

Reference Type BACKGROUND
PMID: 23633542 (View on PubMed)

Mondorf W, Siegmund B, Mahnel R, Richter H, Westfeld M, Galler A, Pollmann H. Haemoassist--a hand-held electronic patient diary for haemophilia home care. Haemophilia. 2009 Mar;15(2):464-72. doi: 10.1111/j.1365-2516.2008.01941.x. Epub 2009 Feb 16.

Reference Type BACKGROUND
PMID: 19226411 (View on PubMed)

Broderick CR, Herbert RD, Latimer J, Mathieu E, van Doorn N, Curtin JA. Feasibility of short message service to document bleeding episodes in children with haemophilia. Haemophilia. 2012 Nov;18(6):906-10. doi: 10.1111/j.1365-2516.2012.02869.x. Epub 2012 Jun 11.

Reference Type BACKGROUND
PMID: 22681182 (View on PubMed)

Sholapur NS, Barty R, Wang G, Almonte T, Heddle NM. A survey of patients with haemophilia to understand how they track product used at home. Haemophilia. 2013 Sep;19(5):e289-95. doi: 10.1111/hae.12170. Epub 2013 May 15.

Reference Type BACKGROUND
PMID: 23672744 (View on PubMed)

Maruish M. User's manual for the SF-36v2 Health Survey (3rd edition). Optum Incorporated; 2011.

Reference Type BACKGROUND

Saris-Baglama, R,DeRosa, M, Raczek, A, Bjorner, J,Turner-Bowker, D, Ware, J. The SF-10™ Health Survey for Children: A User's Guide. QualityMetric Incorporated; 2007.

Reference Type BACKGROUND

Hays RD, Spritzer KL, Schalet BD, Cella D. PROMIS(R)-29 v2.0 profile physical and mental health summary scores. Qual Life Res. 2018 Jul;27(7):1885-1891. doi: 10.1007/s11136-018-1842-3. Epub 2018 Mar 22.

Reference Type BACKGROUND
PMID: 29569016 (View on PubMed)

Sidonio RF Jr, Boban A, Dubey L, Inati A, Kiss C, Boda Z, Lissitchkov T, Nemes L, Novik D, Peteva E, Taher AT, Timofeeva MA, Vilchevska KV, Vdovin V, Werner S, Knaub S, Djambas Khayat C. von Willebrand factor/factor VIII concentrate (Wilate) prophylaxis in children and adults with von Willebrand disease. Blood Adv. 2024 Mar 26;8(6):1405-1414. doi: 10.1182/bloodadvances.2023011742.

Reference Type DERIVED
PMID: 38237075 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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WIL-29

Identifier Type: -

Identifier Source: org_study_id