Trial Outcomes & Findings for HemLibra Prophylaxis in Patients With Hemophilic Pseudotumor (NCT NCT03921294)

NCT ID: NCT03921294

Last Updated: 2024-04-11

Results Overview

Maintenance or increase of hemoglobin (g/dl) from participants' baseline level based on serial blood tests.

Recruitment status

TERMINATED

Study phase

PHASE4

Target enrollment

1 participants

Primary outcome timeframe

Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Results posted on

2024-04-11

Participant Flow

Participant milestones

Participant milestones
Measure
Emicizumab (Single Arm)
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Overall Study
STARTED
1
Overall Study
Enrolled
1
Overall Study
Completed Treatment
1
Overall Study
COMPLETED
1
Overall Study
NOT COMPLETED
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

HemLibra Prophylaxis in Patients With Hemophilic Pseudotumor

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Baseline Characteristics
n=1 Participants
Patients with factor VIII deficiency and a hemophilic pseudotumor.
Age, Categorical
<=18 years
0 Participants
n=5 Participants
Age, Categorical
Between 18 and 65 years
1 Participants
n=5 Participants
Age, Categorical
>=65 years
0 Participants
n=5 Participants
Age, Continuous
31 years
n=5 Participants
Sex: Female, Male
Female
0 Participants
n=5 Participants
Sex: Female, Male
Male
1 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
0 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
1 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
0 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
1 Participants
n=5 Participants
Race (NIH/OMB)
White
0 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Region of Enrollment
United States
1 participants
n=5 Participants

PRIMARY outcome

Timeframe: Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Maintenance or increase of hemoglobin (g/dl) from participants' baseline level based on serial blood tests.

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Hemostatic Efficacy of Prophylactic Weekly Injections of Hemlibra (Emicizumab) Based on Hemoglobin
9.5 gm/dL
Interval 8.0 to 11.0

PRIMARY outcome

Timeframe: Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Whether or not the patient requires blood transfusions (units of RBCs) due to blood loss secondary to lack of hemostatic efficacy during the duration of study treatment duration.

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Hemostatic Efficacy of Prophylactic Weekly Injections of Hemlibra (Emicizumab) Based on Participants' Need for Blood Transfusions or Lack of
0 Participants

SECONDARY outcome

Timeframe: Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Number of breakthrough bleeding events that require hemostatic therapy in addition to Hemlibra prophylaxis

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Breakthrough Bleeds
14 breakthrough bleeding events

SECONDARY outcome

Timeframe: Every 12 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient was unable to return for repeat or final assessments of pseudotumor size by radiology scan after baseline assessment due to global COVID19 pandemic. Only baseline measurements were collected and no follow-up measurements, therefore any change in the pseudotumor status could not be evaluated/determined.

Radiologic evaluation (CT and/or MRI) to evaluate control of progression, stabilization or regression per change in size (measured in cm) of the pseudotumor

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 12 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient was unable to return for repeat or final QoL assessments after baseline assessment, due to the COVID19 global pandemic. Only baseline measurements were collected and no follow-up measurements, therefore any change in the QoL status could not be evaluated/determined.

The subjective change in quality of life and activity with Hemlibra (emicizumab) prophylaxis will be evaluated during the study. QoL and activity will be assessed using Haem-A-QoL and EQ-5D-5L. Changes in these measures will be determined by changes from the baseline scores compared to follow-up scores.

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 12 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient was unable to return for repeat or final QoL assessments after baseline assessment, due to the COVID19 global pandemic. Only baseline measurements were collected and no follow-up measurements, therefore any change in the QoL status could not be evaluated/determined.

The subjective change in quality of life and activity with Hemlibra (emicizumab) prophylaxis will be evaluated during the study. QoL and activity will be assessed using Haem-A-QoL and EQ-5D-5L. Changes in these measures will be determined by changes from the baseline scores compared to follow-up scores.

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 3 months, for the 2 years and 10 months of the patient's study participation duration.

Population: AEs were collected during participant's study participation until study treatment / participation withdrawal.

Number of adverse events while on HemLibra (emicizumab) prophylaxis.

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Adverse Events
3 adverse events

SECONDARY outcome

Timeframe: Every 3 months, for the 2 years and 10 months of the patient's study participation duration.

Number of SAEs while on HemLibra (emicizumab) prophylaxis

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Serious Adverse Events
0 serious adverse events

SECONDARY outcome

Timeframe: Every 3 months, for the 2 years and 10 months of the patient's study participation duration.

Number of participants with adverse events while on HemLibra (emicizumab) prophylaxis

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Number of Participants With Adverse Events
1 participants

SECONDARY outcome

Timeframe: Every 12 months, for the 2 years and 10 months of the patient's study participation duration.

Development of emicizumab anti-drug antibodies using the ADA assay

Outcome measures

Outcome measures
Measure
Single Arm
n=1 Participants
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
Anti-Drug Antibodies (ADA)
0 participants

SECONDARY outcome

Timeframe: Every 12 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient did not develop ADA (anti-drug antibody) during study participation.

If the patient develops an ADA: the ADA's effect on the patient's APTT

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 12 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient did not develop ADA (anti-drug antibody) during study participation.

If the patient develops an ADA: the ADA's effecton the patient's FVIII assay

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient did not require surgery during study treatment.

If the patient requires surgery: Whether the procedure(s) was/were planned versus unplanned

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient did not require surgery during study participation

If the patient requires surgery: Whether hemostatic agents in addition to Hemlibra were required to achieve or maintain hemostasis

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Every 6 months, for the 2 years and 10 months of the patient's study participation duration.

Population: Patient did not have surgery during study participation.

If the patient requires surgery: Whether blood loss exceeded the estimated/predicted blood loss relative to a patient without hemophilia

Outcome measures

Outcome data not reported

Adverse Events

Single Arm

Serious events: 0 serious events
Other events: 1 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Other adverse events
Measure
Single Arm
n=1 participants at risk
Patients with hemophilic pseudotumor will be treated with prophylactic emicizumab and assessed for improvement. Emicizumab: bispecific monoclonal antibody binding to activated Factor IX and Factor X
General disorders
Upper respiratory infection
100.0%
1/1 • Number of events 1 • Every 3 months, for the 2 years and 10 months of the patient's study participation duration.
Standard definitions
Musculoskeletal and connective tissue disorders
Fall with injurty
100.0%
1/1 • Number of events 1 • Every 3 months, for the 2 years and 10 months of the patient's study participation duration.
Standard definitions
Infections and infestations
Malaria infection
100.0%
1/1 • Number of events 1 • Every 3 months, for the 2 years and 10 months of the patient's study participation duration.
Standard definitions

Additional Information

Kat Molitor

Indiana Hemophilia & Thrombosis Center

Phone: 3178710011

Results disclosure agreements

  • Principal investigator is a sponsor employee Sponsor wishes to review final study report prior to submission for publication.
  • Publication restrictions are in place

Restriction type: OTHER