An Open-Label Extension Study of Edasalonexent in Boys With Duchenne Muscular Dystrophy

NCT ID: NCT03917719

Last Updated: 2020-11-23

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

TERMINATED

Clinical Phase

PHASE3

Total Enrollment

130 participants

Study Classification

INTERVENTIONAL

Study Start Date

2019-03-14

Study Completion Date

2020-10-26

Brief Summary

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The GalaxyDMD study is a global Phase 3, open-label, treatment extension study to evaluate the safety, tolerability, and durability of effect in long-term dosing of edasalonexent in pediatric patients with a genetically confirmed diagnosis of DMD. Patients who completed CAT-1004-201 or CAT-1004-301 or siblings of these boys from 4-12 years of age (up to 13th birthday) will be enrolled.

Edasalonexent is an orally administered small molecule that inhibits NF-kB, which is a key link between loss of dystrophin and disease pathology and plays a fundamental role in the initiation and progression of skeletal and cardiac muscle disease in DMD.

Detailed Description

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The study includes a 104-week open-label treatment period with edasalonexent. Patients who completed CAT-1004-201 or CAT-1004-301 and eligible siblings of these boys will be enrolled in this trial.

Conditions

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Duchenne Muscular Dystrophy

Keywords

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Muscular Dystrophies Musculoskeletal Diseases Neuromuscular Diseases DMD dystrophin dystrophy Duchenne

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Dose 1

Edasalonexent 100mg/kg/day. Capsules taken by mouth three times per day.

Group Type EXPERIMENTAL

Edasalonexent

Intervention Type DRUG

100 mg/kg/day

Interventions

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Edasalonexent

100 mg/kg/day

Intervention Type DRUG

Other Intervention Names

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Edasa CAT-1004

Eligibility Criteria

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Inclusion Criteria

* Written consent/assent by patient and/or legal guardian as per regional and/or Institutional Review Board (IRB)/Independent Ethics Committee (IEC) requirements
* Completion of either CAT-1004-201 or CAT-1004-301


* Written consent/assent by patient and/or legal guardian as per regional and/or Institutional Review Board (IRB)/Independent Ethics Committee (IEC) requirements
* A sibling of a patient who completed either CAT-1004-201 or CAT-1004-301
* Diagnosis of DMD based on a clinical phenotype with increased serum creatine kinase (CK) and documentation of mutation(s) in the dystrophin gene known to be associated with a DMD phenotype
* Followed by a doctor or medical professional who coordinates Duchenne care on a regular basis and willingness to disclose patient's study participation with medical professionals

Exclusion Criteria

* In the Investigator's opinion, unwilling or unable for any reason to complete all study assessments and laboratory tests and comply with scheduled visits, administration of drug, and all other study procedures

For Siblings of Patients who Completed CAT-1004-201 or CAT-1004-301:


* Use of oral corticosteroids at screening; use of inhaled, intranasal, and topical corticosteroids is permitted
* Use of another investigational drug, idebenone, or dystrophin-focused therapy within 4 weeks. Exception: Patients who are currently on or plan to initiate treatment with approved oligonucleotide exon-skipping therapies, and expected to continue treatment throughout the study, will be eligible
* Use of the following within 4 weeks prior to Day 1: immunosuppressive therapy, anticoagulants, cyclosporine, dihydroergotamine, ergotamine, fentanyl, alfentanil, pimozide, quinidine, sirolimus or tacrolimus
* Use of human growth hormone within 3 months prior to Day 1
* Other prior or ongoing significant medical conditions
Minimum Eligible Age

4 Years

Maximum Eligible Age

12 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Catabasis Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Joanne M Donovan, MD, PhD

Role: STUDY_CHAIR

Catabasis Pharmaceuticals

Locations

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UC Davis

Sacramento, California, United States

Site Status

Rare Disease Research, LLC

Atlanta, Georgia, United States

Site Status

University of Iowa Children's Hospital

Iowa City, Iowa, United States

Site Status

University of Kansas Medical Center

Fairway, Kansas, United States

Site Status

Kennedy Krieger Institute

Baltimore, Maryland, United States

Site Status

Johns Hopkins School of Medicine

Baltimore, Maryland, United States

Site Status

Boston Children's Hospital

Boston, Massachusetts, United States

Site Status

University of Michigan

Ann Arbor, Michigan, United States

Site Status

Las Vegas Clinic

Las Vegas, Nevada, United States

Site Status

Shriners Hospital for Children

Portland, Oregon, United States

Site Status

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

Vanderbilt University Medical Center

Nashville, Tennessee, United States

Site Status

Cook Children's Medical Center

Fort Worth, Texas, United States

Site Status

University of Texas Health Science Center at San Antonio

San Antonio, Texas, United States

Site Status

University of Utah

Salt Lake City, Utah, United States

Site Status

Royal Children's Hospital

Parkville, Victoria, Australia

Site Status

Children's Hospital of Eastern Ontario

Ottawa, Ontario, Canada

Site Status

University of Hamburg

Hamburg, , Germany

Site Status

University of Munich

Munich, , Germany

Site Status

Queen Silvia Children's Hospital

Gothenburg, , Sweden

Site Status

Bristol Children's Hospital

Bristol, , United Kingdom

Site Status

Great Ormond Street Hospital (GOSH)

London, , United Kingdom

Site Status

Royal Manchester Children's Hospital

Manchester, , United Kingdom

Site Status

Countries

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United States Australia Canada Germany Sweden United Kingdom

Other Identifiers

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CAT-1004-302

Identifier Type: -

Identifier Source: org_study_id