Phase III Study With Idebenone in Patients With Duchenne Muscular Dystrophy (SIDEROS-E)

NCT ID: NCT03603288

Last Updated: 2021-12-03

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

TERMINATED

Clinical Phase

PHASE3

Total Enrollment

161 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-07-04

Study Completion Date

2020-11-25

Brief Summary

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The purpose of the study is to assess the long-term safety and efficacy of idebenone in patients with Duchenne muscular dystrophy (DMD) who completed the SIDEROS study.

Detailed Description

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The study is an open-label, single-group, multi-center extension study in patients with DMD receiving glucocorticoid steroids who participated in the SIDEROS study and who meet all the inclusion criteria and none of the exclusion criteria for this extension study.

The study consists of 4 study visits scheduled every 6 months (Visit 1/Baseline, Visit 2/Week 26, Visit 3/ Week 52 and Visit 4/ Week 78), and a follow-up visit 4 weeks after treatment discontinuation. Visit 8/Week 78 in SIDEROS study is also SIDEROS-E Visit 1/Baseline.

Conditions

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Duchenne Muscular Dystrophy

Keywords

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respiratory function in DMD

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Open-Label Extension Study
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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idebenone 150 mg film-coated tablets

900 mg idebenone/day (2 tablets to be taken 3 times a day with meal)

Group Type EXPERIMENTAL

idebenone 150 mg film-coated tablets

Intervention Type DRUG

900 mg idebenone/day

Interventions

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idebenone 150 mg film-coated tablets

900 mg idebenone/day

Intervention Type DRUG

Eligibility Criteria

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Inclusion Criteria

1. Completion of the SIDEROS study at Visit 8/ Week 78
2. Signed and dated Informed Consent Form for SIDEROS-E

Exclusion Criteria

1. Patients who discontinued SIDEROS study prematurely (i.e. did not attend all visits from V1 to V8)
2. Safety, tolerability or other issues arising during the course of the SIDEROS study which in the opinion of the Investigator may put the patient at significant risk or may interfere significantly with the patient's participation in the SIDEROS-E study
3. Use of any investigational drug other than the study medication
Minimum Eligible Age

11 Years

Eligible Sex

MALE

Accepts Healthy Volunteers

No

Sponsors

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Santhera Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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University of Alabama - Birmingham, Child Health Research

Birmingham, Alabama, United States

Site Status

Banner University of Arizona Medical Center

Tucson, Arizona, United States

Site Status

Children's Hospital of Los Angeles

Los Angeles, California, United States

Site Status

UC Davis Department of Physical Medicine and Rehabilitation

Sacramento, California, United States

Site Status

Center for Integrative Rare Disease Research, Rare Disease Research, LLC

Atlanta, Georgia, United States

Site Status

University of Iowa, Department of Pediatrics

Iowa City, Iowa, United States

Site Status

Johns Hopkins University

Baltimore, Maryland, United States

Site Status

Children's Hospital Boston, Harvard Medical School, Department of Neurology

Boston, Massachusetts, United States

Site Status

Gillette Children's Specialty Healthcare

Saint Paul, Minnesota, United States

Site Status

Neurosciences Institute, Neurology - Charlotte Carolinas Healthcare System

Charlotte, North Carolina, United States

Site Status

Cincinnati Children's Hospital

Cincinnati, Ohio, United States

Site Status

MetroHealth Medical Center

Cleveland, Ohio, United States

Site Status

Children's Hospital of Philadelphia, Division of Pulmonology

Philadelphia, Pennsylvania, United States

Site Status

Gottfried von Preyer'sches Kinderspital

Vienna, , Austria

Site Status

University Hospital Leuven

Leuven, , Belgium

Site Status

CHR Citadelle

Liège, , Belgium

Site Status

Service de neuropédiatrie Pôle Pédiatrie CHRU de Lille - Hôpital Jeanne de Flandre

Lille, , France

Site Status

CHRU de Montpellier - Hôpital Gui de Chauliac, Département de pédiatrie - neuropédiatrie

Montpellier, , France

Site Status

Hôpital Hôtel Dieu, Service Explorations Fonctionnelles - Centre de Référence de Maladies Neuromusculaires rares

Nantes, , France

Site Status

I-Motion - Plateforme d'essais cliniques pédiatriques Hôpital Armand Trousseau bâtiment Lemariey porte 20, 2ème étage

Paris, , France

Site Status

Hôpital des enfants, Pédiatrie Neurologie et infectiologie Pôle enfants

Toulouse, , France

Site Status

University Medical Center Hamburg - Eppendorf, Department of Paediatrics

Hamburg, , Germany

Site Status

Center for neuromuscular disorders, Dr. v. Haunersche Kinderklinik, Universität München

München, , Germany

Site Status

Fondazione IRCCS Eugenio Medea

Bosisio Parini, , Italy

Site Status

U.O. Malattie Neuromuscolari, Istituto Giannina Gaslini

Genova, , Italy

Site Status

Scientific Coordinator Nemo Sud Clinical CenterAOU Policlinico "G. Martino"

Messina, , Italy

Site Status

Centro Clinico NEMO (NEuroMuscular Omnicentre), Niguarda Hospital

Milan, , Italy

Site Status

Servizio di Cardiomiologia e Genetica Medica AOU Università degli Studi della Campania Luigi Vanvitelli

Napoli, , Italy

Site Status

Reparto Di Neurologia dell'Osperdale Di Padova

Padua, , Italy

Site Status

Dipartimento di Clinica Neurologica e Psichiatrica dell'Eta Evolutiva della Fondazione IRCCS "C. Mondino" di Pavia

Pavia, , Italy

Site Status

U.O.C. Neuropsichiatria Infantile

Roma, , Italy

Site Status

Hospital Sant Joan de Deu Neuropediatra, Unidad de patologia nueromuscular, Servicio de Neurologia

Barcelona, , Spain

Site Status

Hospital La Fe de Valencia Avinguda de Fernando Abril Martorell Servicio de Neurologia Torre D

Valencia, , Spain

Site Status

Center for neuromuscular disorders, Universitäts-Kinderspital beider Basel (UKBB)

Basel, , Switzerland

Site Status

Leeds Teaching Hospital NHS Trust

Leeds, , United Kingdom

Site Status

UCL, National Hospital for Neurology and Neurosurgery

London, , United Kingdom

Site Status

Great Ormond Street Hospital for Children

London, , United Kingdom

Site Status

Clinical Research Facility Level 6 Leazes Wing Royal Victoria Infirmary

Newcastle upon Tyne, , United Kingdom

Site Status

Robert Jones and Agnes Hunt Orthopaedic Hospital

Oswestry, , United Kingdom

Site Status

Countries

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United States Austria Belgium France Germany Italy Spain Switzerland United Kingdom

References

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Buyse GM, Voit T, Schara U, Straathof CSM, D'Angelo MG, Bernert G, Cuisset JM, Finkel RS, Goemans N, McDonald CM, Rummey C, Meier T; DELOS Study Group. Efficacy of idebenone on respiratory function in patients with Duchenne muscular dystrophy not using glucocorticoids (DELOS): a double-blind randomised placebo-controlled phase 3 trial. Lancet. 2015 May 2;385(9979):1748-1757. doi: 10.1016/S0140-6736(15)60025-3. Epub 2015 Apr 20.

Reference Type BACKGROUND
PMID: 25907158 (View on PubMed)

McDonald CM, Meier T, Voit T, Schara U, Straathof CS, D'Angelo MG, Bernert G, Cuisset JM, Finkel RS, Goemans N, Rummey C, Leinonen M, Spagnolo P, Buyse GM; DELOS Study Group. Idebenone reduces respiratory complications in patients with Duchenne muscular dystrophy. Neuromuscul Disord. 2016 Aug;26(8):473-80. doi: 10.1016/j.nmd.2016.05.008. Epub 2016 May 12.

Reference Type BACKGROUND
PMID: 27238057 (View on PubMed)

Buyse GM, Voit T, Schara U, Straathof CS, D'Angelo MG, Bernert G, Cuisset JM, Finkel RS, Goemans N, Rummey C, Leinonen M, Mayer OH, Spagnolo P, Meier T, McDonald CM; DELOS Study Group. Treatment effect of idebenone on inspiratory function in patients with Duchenne muscular dystrophy. Pediatr Pulmonol. 2017 Apr;52(4):508-515. doi: 10.1002/ppul.23547. Epub 2016 Aug 29.

Reference Type BACKGROUND
PMID: 27571420 (View on PubMed)

Mayer OH, Leinonen M, Rummey C, Meier T, Buyse GM; DELOS Study Group. Efficacy of Idebenone to Preserve Respiratory Function above Clinically Meaningful Thresholds for Forced Vital Capacity (FVC) in Patients with Duchenne Muscular Dystrophy. J Neuromuscul Dis. 2017;4(3):189-198. doi: 10.3233/JND-170245.

Reference Type BACKGROUND
PMID: 28869486 (View on PubMed)

Related Links

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Other Identifiers

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SNT-III-012-E

Identifier Type: -

Identifier Source: org_study_id