A Study to Assess Efficacy and Safety of RT001 in Subjects With Infantile Neuroaxonal Dystrophy

NCT ID: NCT03570931

Last Updated: 2021-10-14

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE2/PHASE3

Total Enrollment

19 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-11-05

Study Completion Date

2022-06-30

Brief Summary

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The purpose of this study is to evaluate the efficacy and safety of RT001 in patients with Infantile Neuroaxonal Dystrophy (INAD).

Detailed Description

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This is a single arm open-label study with a structured observation of INAD patients treated with RT001. Enrolled subjects will undergo observation and testing to determine the effect of RT001 treatment. Fifteen to twenty eligible subjects will be treated with RT001 for long-term evaluation of efficacy, safety, tolerability, and pharmacokinetics.

Conditions

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Infantile Neuroaxonal Dystrophy

Study Design

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Allocation Method

NA

Intervention Model

SINGLE_GROUP

Single arm open-label study
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Open Label

Study Groups

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RT001

RT001, oral, 3.84 g/day

Group Type EXPERIMENTAL

RT001

Intervention Type DRUG

RT001 is encapsulated di-deutero synthetic homologue of linoleic acid ethyl ester. Each capsule contains 960 mg of RT001.

Interventions

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RT001

RT001 is encapsulated di-deutero synthetic homologue of linoleic acid ethyl ester. Each capsule contains 960 mg of RT001.

Intervention Type DRUG

Other Intervention Names

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Deuterated linoleic acid

Eligibility Criteria

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Inclusion Criteria

1. Male or female 18 months to 10 years of age
2. Medical history consistent with the symptoms of classic INAD (onset of symptoms between the ages of 6 months and 3 years)
3. Homozygous for PLA2G6 deficiency (variant alleles may be mixed heterozygotes)
4. Must have impairment in at least 2 of the assessed categories at baseline
5. Signed informed consent form (ICF) prior to entry into the study
6. Able to provide the necessary blood samples

Exclusion Criteria

1. Received treatment with other experimental therapies within the last 30 days prior to the first dose
2. Requiring mechanical ventilation, other than positive air pressure support primarily for mitigation of sleep apnea.
3. Have a life expectancy of less than one year
4. Diagnosis of atypical NAD (ANAD)
5. Unwilling or unable to comply with the requirements of this protocol, including the presence of any condition (physical, mental, or social) that is likely to affect the subject's ability to return for visits as scheduled
Minimum Eligible Age

18 Months

Maximum Eligible Age

10 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Biojiva LLC

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Peter Milner, MD

Role: STUDY_DIRECTOR

Chief Medical Officer

Locations

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University of California San Francisco, Benioff Children's Hospital

San Francisco, California, United States

Site Status

Jacobs Levy Genomics and Research Program

Morristown, New Jersey, United States

Site Status

Countries

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United States

Other Identifiers

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RT001-008

Identifier Type: -

Identifier Source: org_study_id