A Study to Evaluate Efficacy and Safety of TEZ/IVA in Subjects Aged 6 Through 11 Years With Cystic Fibrosis

NCT ID: NCT03559062

Last Updated: 2020-02-11

Study Results

Results available

Outcome measurements, participant flow, baseline characteristics, and adverse events have been published for this study.

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE3

Total Enrollment

67 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-05-17

Study Completion Date

2018-12-21

Brief Summary

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This study will evaluate the efficacy of tezacaftor in combination with ivacaftor (TEZ/IVA) in participants with cystic fibrosis (CF) aged 6 through 11 years, who are homozygous for the F508del mutation (F/F) or heterozygous for F508del with an eligible residual function mutation (F/RF).

Detailed Description

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Conditions

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Cystic Fibrosis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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Placebo

Participants with genotype F/F received placebo matched to TEZ/IVA fixed dose combination (FDC) in the morning and placebo matched to IVA in the evening for 8 weeks.

Group Type OTHER

Placebo

Intervention Type DRUG

Placebo matched to TEZ/IVA FDC

Placebo

Intervention Type DRUG

Placebo matched to IVA

TEZ/IVA

Participants with genotype F/F received TEZ/IVA FDC in the morning and IVA in the evening for 8 weeks. Participants with genotype F/RF received TEZ/IVA FDC and placebo matched to IVA in the morning and IVA in the evening for 8 weeks.

Group Type EXPERIMENTAL

TEZ/IVA

Intervention Type DRUG

Participants weighing \<40 kg received TEZ 50 mg/IVA 75 mg FDC tablet and those weighing ≥40 kg received TEZ 100 mg/IVA 150 mg FDC tablet.

IVA

Intervention Type DRUG

Participants weighing \<40 kg IVA 75 mg tablet and those weighing ≥40 kg received IVA 150 mg tablet.

Placebo

Intervention Type DRUG

Placebo matched to IVA

Ivacaftor

Participants with genotype F/RF received placebo matched to TEZ/IVA FDC in the morning and IVA in morning and evening for 8 weeks.

Group Type EXPERIMENTAL

IVA

Intervention Type DRUG

Participants weighing \<40 kg IVA 75 mg tablet and those weighing ≥40 kg received IVA 150 mg tablet.

Placebo

Intervention Type DRUG

Placebo matched to TEZ/IVA FDC

Interventions

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TEZ/IVA

Participants weighing \<40 kg received TEZ 50 mg/IVA 75 mg FDC tablet and those weighing ≥40 kg received TEZ 100 mg/IVA 150 mg FDC tablet.

Intervention Type DRUG

IVA

Participants weighing \<40 kg IVA 75 mg tablet and those weighing ≥40 kg received IVA 150 mg tablet.

Intervention Type DRUG

Placebo

Placebo matched to TEZ/IVA FDC

Intervention Type DRUG

Placebo

Placebo matched to IVA

Intervention Type DRUG

Other Intervention Names

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VX-661/VX-770 tezacaftor/ivacaftor fixed dose combination VX-770 ivacaftor

Eligibility Criteria

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Inclusion Criteria

* Homozygous for F508del or heterozygous for F508del and an RF mutation (as defined in the protocol).
* Participants with ppFEV1 of ≥70 percentage points adjusted for age, sex, height.
* Participants with a screening LCI2.5 result ≥7.5.
* Participants who are able to swallow tablets.

Exclusion Criteria

* Clinically significant cirrhosis with or without portal hypertension.
* Colonization with organisms associated with a more rapid decline in pulmonary status.
* Solid organ or hematological transplantation.
Minimum Eligible Age

6 Years

Maximum Eligible Age

11 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Vertex Pharmaceuticals Incorporated

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Hunter Medical Research Institute (HMRI)

New Lambton Heights, , Australia

Site Status

Princess Margaret Hospital for Children

Perth, , Australia

Site Status

Lady Cilento Children's Hospital

South Brisbane, , Australia

Site Status

The Children's Hospital at Westmead

Westmead, , Australia

Site Status

Universitair Ziekenhuis Brussel - Campus Jette

Brussels, , Belgium

Site Status

Universitaire Ziekenhuizen Leuven - Campus Gasthuisberg

Leuven, , Belgium

Site Status

University of Copenhagen Rigshospitalet

Copenhagen, , Denmark

Site Status

Groupe Hospitalier Pellegrin - Hôpital des Enfants

Bordeaux, , France

Site Status

Hôpital Necker - Enfants Malades

Paris, , France

Site Status

Universitaetsklinikum Koeln

Cologne, , Germany

Site Status

Universitaetsklinikum Essen

Essen, , Germany

Site Status

Klinikum der Johann Wolfgang Goethe-Universitaet

Frankfurt, , Germany

Site Status

Universitaetsklinikum Giessen und Marburg GmbH Standort Giessen

Giessen, , Germany

Site Status

Medizinische Hochschule Hannover

Hanover, , Germany

Site Status

Universitaetsklinikum Heidelberg

Heidelberg, , Germany

Site Status

Universitaetsklinikum Jena

Jena, , Germany

Site Status

Universitaetsklinikum Tuebingen

Tübingen, , Germany

Site Status

Our Lady's Children's Hospital

Dublin, , Ireland

Site Status

University Hospital Limerick

Limerick, , Ireland

Site Status

Klinika Mukowiscydozy, Oddział Chorób Płuc SZP ZOZ

Dziekanów Leśny, , Poland

Site Status

Inselspital - Universitaetsspital Bern

Bern, , Switzerland

Site Status

Kinderspital Zuerich

Zurich, , Switzerland

Site Status

Royal Hospital for Sick Children

Edinburgh, , United Kingdom

Site Status

Leeds General Infirmary

Leeds, , United Kingdom

Site Status

Royal Brompton Hospital

London, , United Kingdom

Site Status

Nottingham University Hospital City Campus

Nottingham, , United Kingdom

Site Status

Southampton General Hospital

Southampton, , United Kingdom

Site Status

Countries

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Australia Belgium Denmark France Germany Ireland Poland Switzerland United Kingdom

References

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Heneghan M, Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2023 Nov 20;11(11):CD010966. doi: 10.1002/14651858.CD010966.pub4.

Reference Type DERIVED
PMID: 37983082 (View on PubMed)

Southern KW, Murphy J, Sinha IP, Nevitt SJ. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Cochrane Database Syst Rev. 2020 Dec 17;12(12):CD010966. doi: 10.1002/14651858.CD010966.pub3.

Reference Type DERIVED
PMID: 33331662 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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2016-004479-35

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

VX16-661-115

Identifier Type: -

Identifier Source: org_study_id

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