A First-in-human, Proof of Concept Study of CPK850 in Patients With RLBP1 Retinitis Pigmentosa

NCT ID: NCT03374657

Last Updated: 2026-01-15

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

ACTIVE_NOT_RECRUITING

Clinical Phase

PHASE1/PHASE2

Total Enrollment

12 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-08-22

Study Completion Date

2026-05-11

Brief Summary

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The purpose of this first-in-human study is to explore the maximum tolerated dose (MTD) of CPK850 as determined by the single ascending dose ranging portion of the study. This study will also evaluate the safety and potential efficacy of CPK850 on improving visual function in patients with decreased visual function from RLBP1 retinitis pigmentosa due to biallelic mutations in the RLBP1 gene.

Detailed Description

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This study will potentially include 4 cohorts with a minimum of 3 patients per cohort. This trial design used a staggered patient enrollment with continuous data reviews to limit as much unforeseen risk as possible prior to enrolling each patient in each cohort or initiating another cohort. Only one eye (designated as the study or treated eye) will be dosed per patient. Each patient will be followed for 5 years after the subretinal injection of CPK850.

Conditions

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Retinitis Pigmentosa

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

SINGLE_GROUP

This is a non-confirmatory, open-label single ascending dose gene replacement-therapy study to assess safety, tolerability and efficacy of CPK850 in patients with RLBP1 retinitis pigmentosa due to biallelic mutations in the RLBP1 gene. The trial design uses a staggered patient enrollment.
Primary Study Purpose

TREATMENT

Blinding Strategy

SINGLE

Outcome Assessors
This is a partially masked study. The patients will not be masked. The treating physicians and personnel at the surgical location (surgeons, anesthesiologist, operating room personnel and others) will not be masked.

At the clinical sites, there will be an unmasked ophthalmologist. The remaining assessors at the clinical sites (ophthalmologist, study nurse, ophthalmic technician, etc) doing the ophthalmic examinations should be masked to the study (treated) eye.

The following unmasked sponsor roles are required for this study:

Sponsor clinical staff required to assist in the management and re-supply of investigational drug product.

The independent committee assessing unmasked interim results and the independent analysis team.

All other sponsor staff will stay masked to treatment assignments

Study Groups

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CPK Dose 1 (lowest dose)

CPK850, one subretinal injection to the study eye

Group Type EXPERIMENTAL

CPK850

Intervention Type BIOLOGICAL

In one of 4 dose levels administered via subretinal injection under anesthesia

CPK Dose 2 (next lowest dose)

CPK850, one subretinal injection to the study eye

Group Type EXPERIMENTAL

CPK850

Intervention Type BIOLOGICAL

In one of 4 dose levels administered via subretinal injection under anesthesia

CPK Dose 3 (third lowest dose)

CPK850, one subretinal injection to the study eye

Group Type EXPERIMENTAL

CPK850

Intervention Type BIOLOGICAL

In one of 4 dose levels administered via subretinal injection under anesthesia

CPK Dose 4 (highest dose)

CPK850, one subretinal injection to the study eye

Group Type EXPERIMENTAL

CPK850

Intervention Type BIOLOGICAL

In one of 4 dose levels administered via subretinal injection under anesthesia

Interventions

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CPK850

In one of 4 dose levels administered via subretinal injection under anesthesia

Intervention Type BIOLOGICAL

Eligibility Criteria

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Inclusion Criteria

* Male and female patients aged 18 to 70 years inclusive.
* The visual acuity in the study eye at the screening 1 visit should be no better than 60 ETDRS letters.
* Clinical diagnosis of Bothnia dystrophy, Newfoundland rod-cone dystrophy or other progressive retinitis pigmentosa phenotype with mutations in the RLBP1 gene verified by genetic testing.
* Visible photoreceptor (outer nuclear) and Retinal Pigment Epithelium (RPE) layers on standard OCT scan in the study eye at the screening 1 visit.

Exclusion Criteria

* History of hypersensitivity to the study drug or to drugs of similar classes or to any of the medications required in the perioperative period.
* Pre-existing eye conditions that would preclude the planned surgery or interfere with the interpretation of study endpoints
* Any contraindication to the planned surgery or anesthesia as determined by the treating physician (surgeon, anesthesiologist, internist, or designee).
* Women who are pregnant, or lactating or women of childbearing potential, defined as all women physiologically capable of becoming pregnant, unless they are using highly effective methods of contraception during dosing and for two months after treatment
Minimum Eligible Age

18 Years

Maximum Eligible Age

70 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Novartis Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Novartis Pharmaceuticals

Role: STUDY_DIRECTOR

Novartis Pharmaceuticals

Locations

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Novartis Investigative Site

Stockholm, , Sweden

Site Status

Countries

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Sweden

References

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Kvanta A, Rangaswamy N, Holopigian K, Watters C, Jennings N, Liew MSH, Bigelow C, Grosskreutz C, Burstedt M, Venkataraman A, Westman S, Geirsdottir A, Stasi K, Andre H. Interim safety and efficacy of gene therapy for RLBP1-associated retinal dystrophy: a phase 1/2 trial. Nat Commun. 2024 Sep 10;15(1):7438. doi: 10.1038/s41467-024-51575-4.

Reference Type DERIVED
PMID: 39256350 (View on PubMed)

Other Identifiers

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2016-002696-10

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

CCPK850X2202

Identifier Type: -

Identifier Source: org_study_id

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