Denosumab Versus Zoledronic Acid in Thalassemia-Induced Osteoporosis

NCT ID: NCT03040765

Last Updated: 2019-12-12

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

TERMINATED

Clinical Phase

PHASE3

Total Enrollment

17 participants

Study Classification

INTERVENTIONAL

Study Start Date

2018-05-14

Study Completion Date

2019-04-08

Brief Summary

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This study is to compare the two medications Denosumab and Zoledronic Acid For Patients With Beta Thalassemia Major Induced Osteoporosis. Patients with B-thalassemia major induce osteoporosis will undergo baseline assessment of the bone densitometry by Dual-energy X-ray absorptiometry scan as a standard of care by the radiology department, then a blood test for bone specific Alkaline phosphatase and type-1 Carboxy Telopeptide will be measured by the chemistry lab.

Patients with B-Thalassemia Major induced osteoporosis, who are 18 years of age or more and willing to participate in the study will be enrolled after consenting by the primary investigator in hematology outpatient clinic. Patients with osteoporosis will receive one of the two medications, at the end of the year Dual-energy X-ray absorptiometry scan will be done to compare the response of the two medications. The potential risks include the drug-related side effects

Detailed Description

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Despite the significant improvements in the therapeutic management of beta thalassemia major (BTM) over the past few decades, osteoporosis is still a common finding, even in optimally treated patients. The relationships between bone mineral densities (BMD) and several clinical characteristics or hematological markers have been described. Chronic anemia, bone marrow expansion due to ineffective erythropoiesis, iron toxicity, calcium and zinc deficiencies, low vitamin D levels and endocrine complications have been suggested to contribute to the etiology of bone diseases in BTM. Nevertheless, the complex etiological mechanisms of this heterogeneous osteopathy remain incompletely clarified. A complex mechanism controls bone remodeling in human. This mechanism includes the receptor activator of nuclear factor kappa B ligand (RANKL), its natural receptor (RANK) and osteoprotegerin (OPG). The RANK/RANKL pathway is an essential to promote osteoclast formation and activation and prolongs osteoclast survival.

OPG acts as a decoy receptor for RANKL and prevents its interaction with RANK thereby inhibiting osteoclast formation, function, and survival. Alteration of the RANK/RANKL/OPG system for increased osteoclastic activity and enhanced osteoblastic dysfunction is proposed as an important mechanism in the etiology of osteoporosis in BTM. Hypogonadism, a common finding in BTM, is associated with enhanced RANKL activity. The sex steroid hormones, androgen, and estrogens, via their respective nuclear receptors, regulate BMD in humans and mice. Testosterone is likely to have direct and indirect inhibitory effects on human osteoclast formation and bone resorption. Animal model and cell culture studies suggest a direct inhibitory effect of androgens on the OPG/RANKL cytokines system. In human osteoblastic cells, testosterone and 5-dihydrotestosterone mediate an androgen receptor-induced specific inhibition of OPG messenger ribonucleic acid (mRNA) expression. Androgens have also been shown to block RANKL-induced osteoclastic formation while RANKL expression was found to be up-regulated in osteoblastic cells from androgen receptor-deficient mice. The effect of oestradiol (E2) on osteoclast precursors and osteoclasts seems to be mediated by osteoblastic cells. Inhibitory effect of E2 is associated with the stimulated secretion of OPG by osteoblasts. Previous studies have focused on the characteristics of thalassemic patients with osteoporosis and their response to therapy with bisphosphonate. Because RANK-RANKL and OPG play a significant role in bone resorption and seem to be the principal implicated mechanism for the development of osteoporosis in BTM, we will conduct this prospective study to evaluate the anti-RANKL denosumab versus zoledronic acid on TM-induced osteoporosis.

Conditions

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Thalassemia Majors (Beta-Thalassemia Major) Osteoporosis

Keywords

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Osteoporosis Beta-Thalassemia Major Denosumab Zoledronic Acid

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Denosumab

Denosumab 60 MG/ML Prefilled Syringe

Denosumab Dose: 60 milligrams, subcutaneous injection, every 6 months (twice a year)

Group Type ACTIVE_COMPARATOR

Denosumab 60 MG/ML Prefilled Syringe

Intervention Type DRUG

Denosumab 60 MG/ML will be administered to 20 patients with b-thalassemia major

Zoledronic Acid

Zoledronic Acid 5Mg/Bag 100Ml Inj

Zoledronic acid will be 5 milligrams, Intravenous injection, once a year

Group Type ACTIVE_COMPARATOR

Zoledronic Acid 5Mg/Bag 100Ml Inj

Intervention Type DRUG

Zoledronic Acid 5Mg/Bag 100Ml Inj will be administered to 20 patients with b-thalassemia major

Interventions

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Denosumab 60 MG/ML Prefilled Syringe

Denosumab 60 MG/ML will be administered to 20 patients with b-thalassemia major

Intervention Type DRUG

Zoledronic Acid 5Mg/Bag 100Ml Inj

Zoledronic Acid 5Mg/Bag 100Ml Inj will be administered to 20 patients with b-thalassemia major

Intervention Type DRUG

Other Intervention Names

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Prolia Aclasta

Eligibility Criteria

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Inclusion Criteria

* Willing to participate in the study
* Age 18 years old or older
* Eastern Cooperative Oncology Group Performance Status less than or equal 2

Exclusion Criteria

* Age less than 18 years old
* Not willing to participate in the study
* Vulnerable subjects or Eastern Cooperative Oncology Group Performance Status 3 or 4
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Hamad Medical Corporation

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Mohamed Yassin

Role: PRINCIPAL_INVESTIGATOR

Hamad Medical Corporation

Locations

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National Center for Cancer Care & Research (NCCCR)

Doha, , Qatar

Site Status

Countries

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Qatar

References

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Other Identifiers

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16441/16

Identifier Type: -

Identifier Source: org_study_id