A Study of the Dosing, Efficacy, and Safety of Oral Cysteamine in Adult Patients With Cystic Fibrosis Exacerbations

NCT ID: NCT03000348

Last Updated: 2021-04-14

Study Results

Results available

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

91 participants

Study Classification

INTERVENTIONAL

Study Start Date

2016-12-31

Study Completion Date

2018-04-30

Brief Summary

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This study investigates the use of cysteamine in the treatment of adults with Cystic Fibrosis who are experiencing an exacerbation of CF-associated lung disease. There are six different potential dosing regimens, including one that is placebo.

Detailed Description

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This is a multicenter, double-blind, randomized, placebo-controlled, 6-arm study to investigate the optimal dose regimen, efficacy, and safety of cysteamine in the treatment of adult patients with CF who are experiencing an exacerbation of CF-associated lung disease. Patients will be screened for the study and eligible patients will be randomized to receive either cysteamine or placebo as add-on therapy to their standard of care treatment for CF-associated lung disease.

Conditions

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Cystic Fibrosis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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High Dose, Once per day

Patient takes one oral dose of Cysteamine (high dose) per day, in the morning. The patient takes two oral placebo doses, one at mid-day and one in the evening.

Group Type ACTIVE_COMPARATOR

Cysteamine

Intervention Type DRUG

Oral Cysteamine Capsule

Placebo Oral Capsule

Intervention Type DRUG

Placebo Oral Capsule

High Dose, Twice per day

Patient takes two oral doses of Cysteamine (high dose) per day, one in the morning and one in the evening. The patient takes one oral placebo dose, at mid-day.

Group Type ACTIVE_COMPARATOR

Cysteamine

Intervention Type DRUG

Oral Cysteamine Capsule

Placebo Oral Capsule

Intervention Type DRUG

Placebo Oral Capsule

High Dose, Three times per day

Patient takes three oral doses of Cysteamine (high dose) per day, one in the morning, one at mid-day and one in the evening.

Group Type ACTIVE_COMPARATOR

Cysteamine

Intervention Type DRUG

Oral Cysteamine Capsule

Placebo

Patient takes three oral doses of placebo, one in the morning, one at mid-day and one in the evening.

Group Type PLACEBO_COMPARATOR

Placebo Oral Capsule

Intervention Type DRUG

Placebo Oral Capsule

Low Dose, Three times per day

Patient takes three oral doses of Cysteamine (low dose) per day, one in the morning, one at mid-day and one in the evening.

Group Type ACTIVE_COMPARATOR

Cysteamine

Intervention Type DRUG

Oral Cysteamine Capsule

Placebo Oral Capsule

Intervention Type DRUG

Placebo Oral Capsule

Mid-Range Dose, Three times per day

Patient takes three oral doses of Cysteamine (mid-range dose) per day, one in the morning, one at mid-day and one in the evening.

Group Type ACTIVE_COMPARATOR

Cysteamine

Intervention Type DRUG

Oral Cysteamine Capsule

Placebo Oral Capsule

Intervention Type DRUG

Placebo Oral Capsule

Interventions

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Cysteamine

Oral Cysteamine Capsule

Intervention Type DRUG

Placebo Oral Capsule

Placebo Oral Capsule

Intervention Type DRUG

Other Intervention Names

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Lynovex NM001 Lynovex Oral

Eligibility Criteria

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Inclusion Criteria

1. CF-associated lung disease with documented history of chronic infection with Gram-negative organism(s)
2. Established patient of the Principal Investigator's CF Multi Disciplinary Team (MDT)
3. Age ≥18 years
4. Weight \>40 kg
5. FEV1 \>30% of predicted within the 6 months prior to study exacerbation
6. At the baseline visit: experiencing a new exacerbation of CF-associated lung disease (based on Investigator assessment of ≥4 symptoms present on the Fuchs' criteria) requiring treatment that includes an aminoglycoside antibiotic
7. Females of childbearing potential will be included if they are either sexually inactive (sexually abstinent for 14 days prior to the first study drug dose continuing through 28 days after the last study drug dose, or using one of the following highly effective contraceptive (i.e. results in \<1% failure rate when used consistently and correctly) methods in this trial:

1. intrauterine device (IUD);
2. surgical sterilization of the partner (vasectomy for 6 months minimum);
3. combined (estrogen or progestogen containing) hormonal contraception associated with the inhibition of ovulation (either oral, intravaginal, or transdermal);
4. progestogen only hormonal contraception associated with the inhibition of ovulation (either oral, injectable, or implantable);
5. intrauterine hormone releasing system (IUS);
6. bilateral tubal occlusion.
8. Females of childbearing potential agree to remain sexually inactive or to keep the same birth control method for at least 28 days following the last dose.
9. A female of non-childbearing potential must have undergone one of the following sterilization procedures at least 6 months prior to the first study drug dose:

1. hysteroscopic sterilization;
2. bilateral tubal ligation or bilateral salpingectomy;
3. hysterectomy;
4. bilateral oophorectomy; or be postmenopausal with amenorrhea for at least 1 year prior to the first study drug dose and follicle stimulating hormone (FSH) serum levels consistent with postmenopausal status.
10. A non-vasectomized male subject agrees to use a condom with spermicide or abstain from sexual intercourse during the study until 90 days beyond the last dose of study medication and the female partner agrees to comply with inclusion 7 or 9. For a vasectomized male who has had his vasectomy 6 months or more prior to study start, it is required that they use a condom during sexual intercourse. A male who has been vasectomized less than 6 months prior to study start must follow the same restrictions as a non-vasectomized male.
11. If male, agrees not to donate sperm from the first study drug dose until 90 days after dosing.
12. Willing and able to comply with all protocol requirements and procedures, including induction of sputum, if necessary
13. Willing and able to provide signed and dated informed consent

Exclusion Criteria

1. Hypersensitive to cysteamine or to any of the excipients
2. Hypersensitive to penicillamine
3. Transplant recipient
4. Participation in any other interventional clinical research study (participation in observational studies is not exclusionary) within 30 days of Baseline (Day 0), and any planned participation in an interventional clinical research study for the duration of this study
5. If female, pregnancy, planned pregnancy, or breast-feeding
6. Any other significant disease/disorder which, in the Investigator's opinion, either puts the patient at risk due to study participation, or may influence the results of the study or the patient's ability to participate in the study
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Agility Clinical, Inc.

INDUSTRY

Sponsor Role collaborator

PSR Group B.V.

INDUSTRY

Sponsor Role collaborator

NovaBiotics Ltd.

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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Banner University of Arizona Medical Center

Tucson, Arizona, United States

Site Status

San Francisco Critical Care Medical Group California Pacific Medical Center

San Francisco, California, United States

Site Status

University of Florida

Gainesville, Florida, United States

Site Status

Central Florida Pulmonary

Orlando, Florida, United States

Site Status

Albany Medical College

Albany, New York, United States

Site Status

Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

West Virginia University

Morgantown, West Virginia, United States

Site Status

The Medical College of Wisconsin/Froedtert Hospital

Milwaukee, Wisconsin, United States

Site Status

Ospedale Padiatrico Bambino Gesu Centro Fibrosi Cistica

Roma, , Italy

Site Status

Azienda Ospedaliera Universitaria Integrato di Verona Borgo Trento Centro Fibrosi Cistica

Verona, , Italy

Site Status

Aberdeen Royal Infirmary

Aberdeen, Scotland, United Kingdom

Site Status

Ninewells Hospital Scottish Adult Cystic Fibrosis Service

Dundee, , United Kingdom

Site Status

Western General Hospital Edinburgh, CF Adults / CF Unit

Edinburgh, , United Kingdom

Site Status

NHS GGC

Glasgow, , United Kingdom

Site Status

Raigmore Hospital

Inverness, , United Kingdom

Site Status

St. James University Hospital

Leeds, , United Kingdom

Site Status

Royal Victoria Infirmary Adult CF Centre

Newcastle upon Tyne, , United Kingdom

Site Status

Countries

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United States Italy United Kingdom

References

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Devereux G, Wrolstad D, Bourke SJ, Daines CL, Doe S, Dougherty R, Franco R, Innes A, Kopp BT, Lascano J, Layish D, MacGregor G, Murray L, Peckham D, Lucidi V, Lovie E, Robertson J, Fraser-Pitt DJ, O'Neil DA. Oral cysteamine as an adjunct treatment in cystic fibrosis pulmonary exacerbations: An exploratory randomized clinical trial. PLoS One. 2020 Dec 28;15(12):e0242945. doi: 10.1371/journal.pone.0242945. eCollection 2020.

Reference Type DERIVED
PMID: 33370348 (View on PubMed)

Provided Documents

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Document Type: Study Protocol and Statistical Analysis Plan

View Document

Related Links

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Other Identifiers

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NBTCS02

Identifier Type: -

Identifier Source: org_study_id

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