Study to Evaluate the Safety and Efficacy of CTP-656 in Patients With Cystic Fibrosis With CFTR Gating Mutations

NCT ID: NCT02971839

Last Updated: 2020-08-26

Study Results

Results available

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Basic Information

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Recruitment Status

TERMINATED

Clinical Phase

PHASE2

Total Enrollment

11 participants

Study Classification

INTERVENTIONAL

Study Start Date

2016-12-31

Study Completion Date

2017-08-31

Brief Summary

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This study will evaluate the efficacy and safety of CTP-656 in patients with cystic fibrosis (CF) who have a cystic fibrosis transmembrane conductance regulator (CFTR) gating mutation.

Detailed Description

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This is a randomized, parallel-group, double-blind, placebo controlled multicenter study to evaluate the safety and efficacy of CTP-656 in CF patients with CFTR gating mutations, compared to Kalydeco, for a total of 28 days. Subjects will be randomized to receive either double-blind CTP-656 or placebo, or open-label Kalydeco.

Conditions

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Cystic Fibrosis

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

PARALLEL

Primary Study Purpose

TREATMENT

Blinding Strategy

QUADRUPLE

Participants Caregivers Investigators Outcome Assessors

Study Groups

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VX-561 20 mg

Group Type EXPERIMENTAL

VX-561

Intervention Type DRUG

VX-561 100 mg

Group Type EXPERIMENTAL

VX-561

Intervention Type DRUG

VX-561 150 mg

Group Type EXPERIMENTAL

VX-561

Intervention Type DRUG

Ivacaftor

Group Type ACTIVE_COMPARATOR

IVA

Intervention Type DRUG

Placebo

Group Type PLACEBO_COMPARATOR

Placebo

Intervention Type DRUG

Interventions

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VX-561

Intervention Type DRUG

Placebo

Intervention Type DRUG

IVA

Intervention Type DRUG

Other Intervention Names

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CTP-656 ivacaftor; VX-770 Kalydeco

Eligibility Criteria

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Inclusion Criteria

* 18 years of age or older
* Has a confirmed diagnosis of CF with at least one allele of the following CFTR gating mutations: G551D, G1244E, G1349D, G178R, G551S, S1251N, S1255P, S549N, and S549R.
* Has been stable on Kalydeco therapy for at least 3 months prior to screening
* Has FEV1 ≥ 60% of predicted normal for age, sex, and height at screening and baseline (Day 1) assessments
* Weighs at least 40 kg at screening
* Patients of either gender and women of childbearing potential must be willing to use a medically highly effective form of birth control during the treatment period and 30 days after the last dose of study treatment.

Exclusion Criteria

* Acute upper respiratory infection or lower respiratory infection, pulmonary exacerbation, or changes in therapy within 4 weeks of study treatment
* Uncontrolled type 2 diabetes, or uncontrolled CF-related diabetes
* History of hepatitis C or chronic active hepatitis B infection
* History of pulmonary tuberculosis, non-tuberculosis mycobacterial infections or allergic bronchopulmonary aspergillosis (ABPA) treated during screening or within 2 years prior to screening
* Colonization with B. cenocepacia, B. dolosa, B. multivorans, and/or M. abcessus within 2 years prior to Screening
* Abnormal liver function
* History of abnormal renal function
* History of prolonged QTcF \> 450 msec for males or QTcF \> 470 msec for females
* History of solid organ or hematological transplantation
* Using any inhibitor or inducer of cytochrome P450/3A during the study or within 30 days of screening
* Women who are pregnant or lactating, or have plans to become pregnant during the study or within 1 month following the last dose
Minimum Eligible Age

18 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Vertex Pharmaceuticals Incorporated

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Locations

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University of Southern California

Los Angeles, California, United States

Site Status

Stanford Hospital

Palo Alto, California, United States

Site Status

Children's National Health

Washington D.C., District of Columbia, United States

Site Status

University of Miami

Miami, Florida, United States

Site Status

Rush University

Chicago, Illinois, United States

Site Status

Indiana University

Indianapolis, Indiana, United States

Site Status

Boston Children's Hospital

Boston, Massachusetts, United States

Site Status

University of Massachusetts

Worcester, Massachusetts, United States

Site Status

Washington University

St Louis, Missouri, United States

Site Status

Atlantic Health

Morristown, New Jersey, United States

Site Status

New York Medical College

Valhalla, New York, United States

Site Status

Cincinnati Children's Hospital

Cincinnati, Ohio, United States

Site Status

Nationwide Children's Hospital

Columbus, Ohio, United States

Site Status

Children's Hospital of Philadelphia

Philadelphia, Pennsylvania, United States

Site Status

Countries

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United States

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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CP656.2001

Identifier Type: -

Identifier Source: org_study_id

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