Trial Outcomes & Findings for CSI-Glucagon for Prevention of Hypoglycemia in Children With Congenital Hyperinsulinism (NCT NCT02937558)

NCT ID: NCT02937558

Last Updated: 2019-12-10

Results Overview

Change from baseline in glucose infusion rate (GIR) will be determined for each subject at 24 and 48 hours from the start of blinded treatment. Subjects with a decrease in GIR ≥ 20% at 24 hours, and ≥ 33% at 48 hours will be considered to have had a clinically meaningful treatment response.

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

5 participants

Primary outcome timeframe

Baseline to end of blinded treatment at 24 or 48 hours

Results posted on

2019-12-10

Participant Flow

A total of 5 subjects were randomized to active or placebo treatment during the double-blind phase of the study. All subjects completing double-blind treatment were eligible for open-label in-patient treatment with CSI Glucagon.

The first enrolled subject was not deemed evaluable for responsive to glucagon based upon prior history of glucagon resistance, per investigator.

Participant milestones

Participant milestones
Measure
CSI-Glucagon
Glucagon solution delivered as a continuous subcutaneous infusion via a patch pump at a starting dosage of 5 mcg/kg/hr. Glucagon: Room-temperature-stable, non-aqueous injectable liquid formulation of synthetic glucagon peptide
Placebo
Vehicle solution delivered as a 24-hour continuous subcutaneous infusion via a patch pump. Placebo: Isotonic saline
Double-blind Phase
STARTED
3
2
Double-blind Phase
COMPLETED
3
2
Double-blind Phase
NOT COMPLETED
0
0
Open-label Phase
STARTED
5
0
Open-label Phase
COMPLETED
5
0
Open-label Phase
NOT COMPLETED
0
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

CSI-Glucagon for Prevention of Hypoglycemia in Children With Congenital Hyperinsulinism

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
CSI-Glucagon
n=3 Participants
Glucagon solution delivered as a continuous subcutaneous infusion via a patch pump at a starting dosage of 5 mcg/kg/hr. Glucagon: Room-temperature-stable, non-aqueous injectable liquid formulation of synthetic glucagon peptide
Placebo
n=2 Participants
Vehicle solution delivered as a 24-hour continuous subcutaneous infusion via a patch pump. Placebo: Isotonic saline
Total
n=5 Participants
Total of all reporting groups
Age, Continuous
25 days
STANDARD_DEVIATION 12.49 • n=5 Participants
78.5 days
STANDARD_DEVIATION 79.90 • n=7 Participants
46.4 days
STANDARD_DEVIATION 50.33 • n=5 Participants
Sex: Female, Male
Female
2 Participants
n=5 Participants
1 Participants
n=7 Participants
3 Participants
n=5 Participants
Sex: Female, Male
Male
1 Participants
n=5 Participants
1 Participants
n=7 Participants
2 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
1 Participants
n=5 Participants
0 Participants
n=7 Participants
1 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
2 Participants
n=5 Participants
2 Participants
n=7 Participants
4 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
1 Participants
n=5 Participants
0 Participants
n=7 Participants
1 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
0 Participants
n=5 Participants
1 Participants
n=7 Participants
1 Participants
n=5 Participants
Race (NIH/OMB)
White
2 Participants
n=5 Participants
1 Participants
n=7 Participants
3 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Region of Enrollment
United States
3 Participants
n=5 Participants
2 Participants
n=7 Participants
5 Participants
n=5 Participants

PRIMARY outcome

Timeframe: Baseline to end of blinded treatment at 24 or 48 hours

Population: Evaluable subjects

Change from baseline in glucose infusion rate (GIR) will be determined for each subject at 24 and 48 hours from the start of blinded treatment. Subjects with a decrease in GIR ≥ 20% at 24 hours, and ≥ 33% at 48 hours will be considered to have had a clinically meaningful treatment response.

Outcome measures

Outcome measures
Measure
CSI-Glucagon
n=2 Participants
Glucagon solution delivered as a continuous subcutaneous infusion via a patch pump at a starting dosage of 5 mcg/kg/hr. Glucagon: Room-temperature-stable, non-aqueous injectable liquid formulation of synthetic glucagon peptide
Placebo
n=2 Participants
Vehicle solution delivered as a 24-hour continuous subcutaneous infusion via a patch pump. Placebo: Isotonic saline
Number of Subjects With Clinically Meaningful Reduction in Glucose Infusion Rate (Double-Blind)
2 Participants
0 Participants

SECONDARY outcome

Timeframe: Baseline to the end of blinded treatment at 24 or 48 hours

Population: Evaluable subjects

The groups will be compared for mean percent change in GIR from baseline to the end of the double-blind study phase.

Outcome measures

Outcome measures
Measure
CSI-Glucagon
n=2 Participants
Glucagon solution delivered as a continuous subcutaneous infusion via a patch pump at a starting dosage of 5 mcg/kg/hr. Glucagon: Room-temperature-stable, non-aqueous injectable liquid formulation of synthetic glucagon peptide
Placebo
n=2 Participants
Vehicle solution delivered as a 24-hour continuous subcutaneous infusion via a patch pump. Placebo: Isotonic saline
Percent Change in GIR (Double-Blind)
-50.1 % change
Standard Deviation 4.5
1.9 % change
Standard Deviation 45.9

SECONDARY outcome

Timeframe: Baseline to the end of open-label treatment at 72 hours

Population: Evaluable subjects

Change from baseline in glucose infusion rate (GIR) will be determined for each subject at the end of open-label treatment. Subjects with a decrease in GIR ≥ 33% will be considered to have had a clinically meaningful treatment response.

Outcome measures

Outcome measures
Measure
CSI-Glucagon
n=4 Participants
Glucagon solution delivered as a continuous subcutaneous infusion via a patch pump at a starting dosage of 5 mcg/kg/hr. Glucagon: Room-temperature-stable, non-aqueous injectable liquid formulation of synthetic glucagon peptide
Placebo
Vehicle solution delivered as a 24-hour continuous subcutaneous infusion via a patch pump. Placebo: Isotonic saline
Number of Subjects With Clinically Meaningful Reduction in Glucose Infusion Rate (Open-Label)
4 Participants
0 Participants

SECONDARY outcome

Timeframe: Baseline to end of treatment at 72 hours

Population: Evaluable subjects

The groups will be compared for mean percent change in GIR from baseline to the end of the open-label study phase.

Outcome measures

Outcome measures
Measure
CSI-Glucagon
n=4 Participants
Glucagon solution delivered as a continuous subcutaneous infusion via a patch pump at a starting dosage of 5 mcg/kg/hr. Glucagon: Room-temperature-stable, non-aqueous injectable liquid formulation of synthetic glucagon peptide
Placebo
Vehicle solution delivered as a 24-hour continuous subcutaneous infusion via a patch pump. Placebo: Isotonic saline
Percent Change in Glucose Infusion Rate (Open-Label)
-51.2 % change
Standard Deviation 10.3

Adverse Events

CSI-Glucagon (Double-Blind)

Serious events: 0 serious events
Other events: 0 other events
Deaths: 0 deaths

Placebo

Serious events: 0 serious events
Other events: 0 other events
Deaths: 0 deaths

CSI-Glucagon (Open-Label)

Serious events: 0 serious events
Other events: 0 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Adverse event data not reported

Additional Information

Khaled Junaidi

Xeris Pharmaceuticals, Inc.

Phone: 312-517-1461

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place