The Study of an Investigational Drug, Patisiran (ALN-TTR02), for the Treatment of Transthyretin (TTR)-Mediated Amyloidosis in Participants Who Have Already Been Treated With ALN-TTR02 (Patisiran)

NCT ID: NCT02510261

Last Updated: 2023-12-06

Study Results

Results available

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Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE3

Total Enrollment

211 participants

Study Classification

INTERVENTIONAL

Study Start Date

2015-07-16

Study Completion Date

2022-11-23

Brief Summary

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The purpose of this study is to evaluate the safety and efficacy of long-term dosing with ALN-TTR02 (patisiran) in participants with transthyretin (TTR) mediated amyloidosis (ATTR).

Detailed Description

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Conditions

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Amyloidosis

Keywords

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RNAi therapeutic FAP Familial Amyloid Polyneuropathy TTR Transthyretin Amyloidosis

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

SINGLE_GROUP

All the participants received only patisiran but divided into 3 arm groups based on administration in the parent study (placebo or patisiran in 003 \[NCT01961921\] or 004 \[NCT01960348\] studies).
Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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Prior Placebo Group of Study 004

Participants who received placebo and completed parent study ALN-TTR02-004 (NCT01960348) were enrolled to receive 0.3 milligrams per kilogram (mg/kg) patisiran intravenously (IV) once every 3 weeks (Q3W) up to 65.5 months.

Group Type EXPERIMENTAL

Patisiran

Intervention Type DRUG

Patisiran was administered IV.

Prior Patisiran Group of Study 004

Participants who received patisiran and completed parent study ALN-TTR02-004 (NCT01960348) were enrolled to receive 0.3 mg/kg patisiran IV Q3W up to 66.9 months.

Group Type EXPERIMENTAL

Patisiran

Intervention Type DRUG

Patisiran was administered IV.

Prior Patisiran Group of Study 003

Participants who received patisiran and completed parent study ALN-TTR02-003 (NCT01961921) were enrolled to receive 0.3 mg/kg patisiran IV Q3W up to 61.4 months.

Group Type EXPERIMENTAL

Patisiran

Intervention Type DRUG

Patisiran was administered IV.

Interventions

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Patisiran

Patisiran was administered IV.

Intervention Type DRUG

Other Intervention Names

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ALN-TTR02

Eligibility Criteria

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Inclusion Criteria

* Have completed a patisiran study (i.e., completed the last efficacy visit in the parent study) and, in the opinion of the investigator, tolerated study drug
* Be willing and able to comply with the protocol-required visit schedule and visit requirements and provide written informed consent

Exclusion Criteria

* Any new or uncontrolled condition that could make the participant unsuitable for participation
Minimum Eligible Age

18 Years

Maximum Eligible Age

85 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Alnylam Pharmaceuticals

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Medical Director

Role: STUDY_DIRECTOR

Alnylam Pharmaceuticals

Locations

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Clinical Trial Site

La Mesa, California, United States

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Aurora, Colorado, United States

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Jacksonville, Florida, United States

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Chicago, Illinois, United States

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Baltimore, Maryland, United States

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Boston, Massachusetts, United States

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Detroit, Michigan, United States

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Rochester, Minnesota, United States

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Joplin, Missouri, United States

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St Louis, Missouri, United States

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Cooperstown, New York, United States

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New York, New York, United States

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New York, New York, United States

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Columbus, Ohio, United States

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Buenos Aires, , Argentina

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Westmead, , Australia

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Rio de Janeiro, , Brazil

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São Paulo, , Brazil

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Sofia, , Bulgaria

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Vancouver, British Columbia, Canada

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Nicosia, , Cyprus

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Fort de France, Martinique, France

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Saint-Pierre, Reunion Island, France

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Créteil, , France

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Le Kremlin-Bicêtre, , France

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Lille, , France

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Marseille, , France

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Cologne, , Germany

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Heidelberg, , Germany

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Münster, , Germany

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Pavia, , Italy

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Rome, , Italy

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Sicily, , Italy

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Ehime, , Japan

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Fukuoka, , Japan

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Hiroshima, , Japan

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Kumamoto, , Japan

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Nagano, , Japan

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Okawasuji, , Japan

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Ono, , Japan

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Ōita, , Japan

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Kuala Lumpur, , Malaysia

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Tlalpan, , Mexico

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Groningen, , Netherlands

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Lisbon, , Portugal

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Porto, , Portugal

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Seoul, , South Korea

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Barcelona, , Spain

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Huelva, , Spain

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Madrid, , Spain

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Palma de Mallorca, , Spain

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Umeå, , Sweden

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Taipei, , Taiwan

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Taipei, , Taiwan

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Istanbul, , Turkey (Türkiye)

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London, , United Kingdom

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Countries

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United States Argentina Australia Brazil Bulgaria Canada Cyprus France Germany Italy Japan Malaysia Mexico Netherlands Portugal South Korea Spain Sweden Taiwan Turkey (Türkiye) United Kingdom

References

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Adams D, Wixner J, Polydefkis M, Berk JL, Conceicao IM, Dispenzieri A, Peltier A, Ueda M, Bender S, Capocelli K, Jay PY, Yureneva E, Obici L; patisiran Global OLE study group. Five-Year Results With Patisiran for Hereditary Transthyretin Amyloidosis With Polyneuropathy: A Randomized Clinical Trial With Open-Label Extension. JAMA Neurol. 2025 Mar 1;82(3):228-236. doi: 10.1001/jamaneurol.2024.4631.

Reference Type DERIVED
PMID: 39804640 (View on PubMed)

Lin KP, Yang CC, Lee YC, Lee MJ, Vest J, Sweetser MT, White MT, Badri P, Hsieh ST, Chao CC. Patisiran, an RNAi therapeutic for hereditary transthyretin-mediated amyloidosis: Sub-analysis in Taiwanese patients from the APOLLO study. J Formos Med Assoc. 2024 Sep;123(9):975-984. doi: 10.1016/j.jfma.2024.03.008. Epub 2024 Mar 27.

Reference Type DERIVED
PMID: 38548524 (View on PubMed)

Adams D, Polydefkis M, Gonzalez-Duarte A, Wixner J, Kristen AV, Schmidt HH, Berk JL, Losada Lopez IA, Dispenzieri A, Quan D, Conceicao IM, Slama MS, Gillmore JD, Kyriakides T, Ajroud-Driss S, Waddington-Cruz M, Mezei MM, Plante-Bordeneuve V, Attarian S, Mauricio E, Brannagan TH 3rd, Ueda M, Aldinc E, Wang JJ, White MT, Vest J, Berber E, Sweetser MT, Coelho T; patisiran Global OLE study group. Long-term safety and efficacy of patisiran for hereditary transthyretin-mediated amyloidosis with polyneuropathy: 12-month results of an open-label extension study. Lancet Neurol. 2021 Jan;20(1):49-59. doi: 10.1016/S1474-4422(20)30368-9. Epub 2020 Nov 16.

Reference Type DERIVED
PMID: 33212063 (View on PubMed)

Provided Documents

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Document Type: Study Protocol

View Document

Document Type: Statistical Analysis Plan

View Document

Other Identifiers

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2014-003877-40

Identifier Type: EUDRACT_NUMBER

Identifier Source: secondary_id

ALN-TTR02-006

Identifier Type: -

Identifier Source: org_study_id