Trial Outcomes & Findings for A Phase III Study on the Safety, Pharmacokinetics and Efficacy of Coagulation Factor VIIa (NCT NCT02448680)

NCT ID: NCT02448680

Last Updated: 2022-02-25

Results Overview

For the primary efficacy endpoint, successful treatment of mild/moderate bleeding episode was defined as meeting all of the following: * "Good" or "excellent" response noted by the patient/parent/legal guardian or other caregiver, depending on patient's age and maturity * Study drug treatment: No further treatment with LR769 beyond timepoint where a "good" or "excellent" response for this bleeding episode was noted * No other hemostatic treatment needed for this bleeding episode * No administration of blood products that would indicate continuation of bleeding beyond timepoint where a "good" or "excellent" response for this bleeding episode was noted * No increase of pain beyond timepoint where a "good" or "excellent" response for this bleeding episode was noted that could not be explained other than as continuation of bleeding

Recruitment status

COMPLETED

Study phase

PHASE3

Target enrollment

25 participants

Primary outcome timeframe

12 hours after first administration of study drug

Results posted on

2022-02-25

Participant Flow

Participant milestones

Participant milestones
Measure
FVIIa: 75 µg/kg First, Then 225 µg/kg
Coagulation Factor VIIa (Recombinant) : First Intervention (3 months), Second Intervention (3 months), repeat sequence for entirety of study.
FVIIa: 225 µg/kg First, Then 75 µg/kg
Coagulation Factor VIIa (Recombinant) : First Intervention (3 months), Second Intervention (3 months), repeat sequence for entirety of study.
Overall Study
STARTED
12
13
Overall Study
COMPLETED
11
10
Overall Study
NOT COMPLETED
1
3

Reasons for withdrawal

Reasons for withdrawal
Measure
FVIIa: 75 µg/kg First, Then 225 µg/kg
Coagulation Factor VIIa (Recombinant) : First Intervention (3 months), Second Intervention (3 months), repeat sequence for entirety of study.
FVIIa: 225 µg/kg First, Then 75 µg/kg
Coagulation Factor VIIa (Recombinant) : First Intervention (3 months), Second Intervention (3 months), repeat sequence for entirety of study.
Overall Study
Physician Decision
1
1
Overall Study
Withdrawal by Subject
0
2

Baseline Characteristics

A Phase III Study on the Safety, Pharmacokinetics and Efficacy of Coagulation Factor VIIa

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
FVIIa: 75 µg/kg First, Then 225 µg/kg
n=12 Participants
Coagulation Factor VIIa (Recombinant) : First Intervention (3 months), Second Intervention (3 months), repeat sequence for entirety of study.
FVIIa: 225 µg/kg First, Then 75 µg/kg
n=13 Participants
Coagulation Factor VIIa (Recombinant) : First Intervention (3 months), Second Intervention (3 months), repeat sequence for entirety of study.
Total
n=25 Participants
Total of all reporting groups
Age, Continuous
4.9 years
STANDARD_DEVIATION 3.02 • n=5 Participants
4.8 years
STANDARD_DEVIATION 3.63 • n=7 Participants
4.9 years
STANDARD_DEVIATION 3.28 • n=5 Participants
Age, Customized
Age, Categorical · Birth to < 6 years old
6 Participants
n=5 Participants
7 Participants
n=7 Participants
13 Participants
n=5 Participants
Age, Customized
Age, Categorical · >= 6 years to < 12 years old
6 Participants
n=5 Participants
6 Participants
n=7 Participants
12 Participants
n=5 Participants
Sex: Female, Male
Female
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Sex: Female, Male
Male
12 Participants
n=5 Participants
13 Participants
n=7 Participants
25 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
1 Participants
n=5 Participants
2 Participants
n=7 Participants
3 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
11 Participants
n=5 Participants
11 Participants
n=7 Participants
22 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
4 Participants
n=5 Participants
3 Participants
n=7 Participants
7 Participants
n=5 Participants
Race (NIH/OMB)
White
8 Participants
n=5 Participants
10 Participants
n=7 Participants
18 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Weight
19.73 kg
STANDARD_DEVIATION 7.432 • n=5 Participants
21.94 kg
STANDARD_DEVIATION 13.391 • n=7 Participants
20.88 kg
STANDARD_DEVIATION 10.782 • n=5 Participants
Height
104.21 cm
STANDARD_DEVIATION 21.210 • n=5 Participants
108.60 cm
STANDARD_DEVIATION 25.904 • n=7 Participants
106.49 cm
STANDARD_DEVIATION 23.382 • n=5 Participants
Body Mass Index (BMI)
17.74 kg/m^2
STANDARD_DEVIATION 2.505 • n=5 Participants
17.35 kg/m^2
STANDARD_DEVIATION 3.842 • n=7 Participants
17.53 kg/m^2
STANDARD_DEVIATION 3.209 • n=5 Participants

PRIMARY outcome

Timeframe: 12 hours after first administration of study drug

Population: Treated Population

For the primary efficacy endpoint, successful treatment of mild/moderate bleeding episode was defined as meeting all of the following: * "Good" or "excellent" response noted by the patient/parent/legal guardian or other caregiver, depending on patient's age and maturity * Study drug treatment: No further treatment with LR769 beyond timepoint where a "good" or "excellent" response for this bleeding episode was noted * No other hemostatic treatment needed for this bleeding episode * No administration of blood products that would indicate continuation of bleeding beyond timepoint where a "good" or "excellent" response for this bleeding episode was noted * No increase of pain beyond timepoint where a "good" or "excellent" response for this bleeding episode was noted that could not be explained other than as continuation of bleeding

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=239 Bleeding Episodes (BEs)
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=307 Bleeding Episodes (BEs)
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Proportion of Successfully Treated Mild/Moderate Bleeding Episodes Per FDA Requirement.
0.654 Proportion of successfully treated BEs
Interval 0.523 to 0.785
0.603 Proportion of successfully treated BEs
Interval 0.482 to 0.723

PRIMARY outcome

Timeframe: 12 hours after first administration of study drug

Population: Treated Population

* "Good" or "excellent" response noted by the patient/caregiver for mild/moderate bleeding episodes; * "Good" or "excellent" response noted by the physician for severe bleeding episodes.

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=239 Bleeding Episodes (BEs)
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=310 Bleeding Episodes (BEs)
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Proportion of Successfully Treated Bleeding Episodes (Mild/Moderate/Severe) Per EMA Definition
0.667 Proportion of successfully treated BEs
Interval 0.533 to 0.8
0.625 Proportion of successfully treated BEs
Interval 0.5 to 0.75

SECONDARY outcome

Timeframe: 12 hour after first administration of study drug

Population: Treated Population

Based on Patient-Reported "Good" or "Excellent" responses as per the below descriptions: Good: Symptoms of bleed (e.g., swelling, tenderness, and decreased range of motion in the case of musculoskeletal hemorrhage) had largely been reduced by the treatment, but had not completely disappeared. Symptoms had improved enough to not require more infusions of the study drug. Excellent: Full relief of pain and cessation of objective signs of bleed (e.g., swelling, tenderness, and decreased range of motion in the case of musculoskeletal hemorrhage). No additional infusion of study drug was required.

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=239 Bleeding Episodes (BEs)
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=307 Bleeding Episodes (BEs)
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Patient-Reported "Good" or "Excellent" Response for Mild/Moderate Bleeding Episodes
0.667 Proportion of successfully treated BEs
Interval 0.533 to 0.8
0.629 Proportion of successfully treated BEs
Interval 0.502 to 0.756

SECONDARY outcome

Timeframe: Within 24 hours of Bleeding Episode

Population: Treated Population with non-missing measurements

Categories of Response to Treatment are Described as Follows: None: No noticeable effect of the treatment on the bleed or worsening of patient's condition. Continuation of treatment with the study drug was needed. Moderate: Some effect of the treatment on the bleed was noticed, e.g., pain decreased or bleeding signs improved, but bleed continued and required continued treatment with the study drug. Good: Symptoms of bleed (e.g., swelling, tenderness, and decreased range of motion in the case of musculoskeletal haemorrhage) had largely been reduced by the treatment, but had not completely disappeared. Symptoms had improved enough to not require more infusions of the study drug. Excellent: Full relief of pain and cessation of objective signs of bleed (e.g., swelling, tenderness, and decreased range of motion in the case of musculoskeletal haemorrhage). No additional infusion of study drug was required.

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=233 Bleeding Episodes with Event
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=299 Bleeding Episodes with Event
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Time to Patient Assessment of a "Good" or "Excellent" Response for Mild/Moderate Bleeding Episodes
9.00 Hours
Interval 8.92 to 11.83
12.00 Hours
Interval 11.83 to 12.0

SECONDARY outcome

Timeframe: Within 24 hours of Bleeding Episode

Population: Treated Population

The number of study drug administrations with non-missing dose information in order to treat one mild/moderate bleeding episode.

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=239 Bleeding Episodes (BEs)
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=307 Bleeding Episodes (BEs)
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Number of Administrations of Study Drug Per Mild/Moderate Bleeding Episode
3.6 Administrations of Study Drug
Standard Deviation 2.27
2.6 Administrations of Study Drug
Standard Deviation 2.48

SECONDARY outcome

Timeframe: Within 24 hours of Bleeding Episode

Population: Treated Population with non-missing measurements

The total amount of study drug administered in order to treat one mild/moderate bleeding episode.

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=239 Bleeding Episodes (BEs)
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=307 Bleeding Episodes (BEs)
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Total Amount of Study Drug Administered Per Mild/Moderate Bleeding Episode
6.733 mL per bleeding episode
Standard Deviation 6.3693
8.287 mL per bleeding episode
Standard Deviation 5.6531

OTHER_PRE_SPECIFIED outcome

Timeframe: 12 hour after first administration of study drug

Population: Treated Population

Successful pain relief was defined as a Visual Analogue Scale (VAS: 0-100; 0: no pain at all; 100: the worst pain ever possible) pain score at 12 hours after initial study drug administration that was less than the pain score at the start of treatment with study drug.

Outcome measures

Outcome measures
Measure
FVIIa 75 µg/kg
n=239 Bleeding Episodes (BEs)
75 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
FVIIa 225µg/kg
n=307 Bleeding Episodes (BEs)
225 µg/kg Treatment Regimen at Time of Mild/Moderate Bleeding Episode
Mild/Moderate Bleeding Episodes With Successful Pain Relief
220 Bleeding Episodes (BEs)
275 Bleeding Episodes (BEs)

Adverse Events

Coagulation Factor VIIa (Recombinant): 75 µg/kg

Serious events: 0 serious events
Other events: 12 other events
Deaths: 0 deaths

Coagulation Factor VIIa (Recombinant): 225 µg/kg

Serious events: 2 serious events
Other events: 15 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Coagulation Factor VIIa (Recombinant): 75 µg/kg
n=23 participants at risk
75 µg/kg treatment regimen for 3 months Coagulation FVIIa (Recombinant): A cross over design to assess the efficacy of 2 separate dose regimens (75 µg/kg and 225 µg/kg) of Coagulation Factor VIIa (Recombinant) for the treatment of bleeding episodes in hemophilia A or B patients with inhibitors to Factor VIII or Factor IX
Coagulation Factor VIIa (Recombinant): 225 µg/kg
n=25 participants at risk
225 µg/kg treatment regimen for 3 months Coagulation FVIIa (Recombinant): A cross over design to assess the efficacy of 2 separate dose regimens (75 µg/kg and 225 µg/kg) of Coagulation Factor VIIa (Recombinant) for the treatment of bleeding episodes in hemophilia A or B patients with inhibitors to Factor VIII or Factor IX
Infections and infestations
Dysentery
0.00%
0/23 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
4.0%
1/25 • Number of events 1 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Nervous system disorders
Paresis
0.00%
0/23 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
4.0%
1/25 • Number of events 1 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.

Other adverse events

Other adverse events
Measure
Coagulation Factor VIIa (Recombinant): 75 µg/kg
n=23 participants at risk
75 µg/kg treatment regimen for 3 months Coagulation FVIIa (Recombinant): A cross over design to assess the efficacy of 2 separate dose regimens (75 µg/kg and 225 µg/kg) of Coagulation Factor VIIa (Recombinant) for the treatment of bleeding episodes in hemophilia A or B patients with inhibitors to Factor VIII or Factor IX
Coagulation Factor VIIa (Recombinant): 225 µg/kg
n=25 participants at risk
225 µg/kg treatment regimen for 3 months Coagulation FVIIa (Recombinant): A cross over design to assess the efficacy of 2 separate dose regimens (75 µg/kg and 225 µg/kg) of Coagulation Factor VIIa (Recombinant) for the treatment of bleeding episodes in hemophilia A or B patients with inhibitors to Factor VIII or Factor IX
Blood and lymphatic system disorders
Anaemia
8.7%
2/23 • Number of events 2 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
0.00%
0/25 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Gastrointestinal disorders
Diarrhoea
4.3%
1/23 • Number of events 1 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
12.0%
3/25 • Number of events 3 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Gastrointestinal disorders
Vomiting
4.3%
1/23 • Number of events 1 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
8.0%
2/25 • Number of events 2 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Infections and infestations
Bronchitis
4.3%
1/23 • Number of events 1 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
12.0%
3/25 • Number of events 4 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Infections and infestations
Nasopharyngitis
17.4%
4/23 • Number of events 6 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
12.0%
3/25 • Number of events 3 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Infections and infestations
Respiratory tract infection viral
4.3%
1/23 • Number of events 2 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
8.0%
2/25 • Number of events 3 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Infections and infestations
Rhinitis
13.0%
3/23 • Number of events 3 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
12.0%
3/25 • Number of events 3 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
Respiratory, thoracic and mediastinal disorders
Cough
13.0%
3/23 • Number of events 4 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.
12.0%
3/25 • Number of events 4 • From signing of the informed consent/assent until resolution or 30 days after the last dose of LR769 or early termination, whichever came first. The average duration for monitoring adverse event is about 11.2 months per patient.

Additional Information

Kerry Biron, Director US Clinical Operations

LFB USA, Inc.

Phone: 508-370-5166

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place