Trial Outcomes & Findings for Study of Eteplirsen in DMD Patients (NCT NCT02255552)

NCT ID: NCT02255552

Last Updated: 2021-01-25

Results Overview

6MWT was performed by standardized procedures for all participants. Participants were asked to walk a set course of 25 meters for 6 minutes (timed), and the distance walked (in meters) was recorded. Change from baseline in 6MWT distance at Week 96 was reported.

Recruitment status

COMPLETED

Study phase

PHASE3

Target enrollment

109 participants

Primary outcome timeframe

Baseline, Week 96

Results posted on

2021-01-25

Participant Flow

The study was conducted at 40 sites in the United States.

A total of 109 participants were enrolled in the study. Only 79 participants were treated and the remaining participants were not applicable for treatment as those participants assessed under "Untreated" arm.

Participant milestones

Participant milestones
Measure
Eteplirsen 30 mg/kg
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Overall Study
STARTED
79
30
Overall Study
COMPLETED
78
15
Overall Study
NOT COMPLETED
1
15

Reasons for withdrawal

Reasons for withdrawal
Measure
Eteplirsen 30 mg/kg
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Overall Study
Participants enrolled into another study
0
11
Overall Study
Withdrawal by Subject
1
4

Baseline Characteristics

Study of Eteplirsen in DMD Patients

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Eteplirsen 30 mg/kg
n=79 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=30 Participants
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Total
n=109 Participants
Total of all reporting groups
Age, Continuous
9.1 Years
STANDARD_DEVIATION 2.04 • n=5 Participants
8.8 Years
STANDARD_DEVIATION 1.76 • n=7 Participants
9.0 Years
STANDARD_DEVIATION 1.96 • n=5 Participants
Sex: Female, Male
Female
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Sex: Female, Male
Male
79 Participants
n=5 Participants
30 Participants
n=7 Participants
109 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
7 Participants
n=5 Participants
6 Participants
n=7 Participants
13 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
71 Participants
n=5 Participants
24 Participants
n=7 Participants
95 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
1 Participants
n=5 Participants
0 Participants
n=7 Participants
1 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
5 Participants
n=5 Participants
1 Participants
n=7 Participants
6 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
2 Participants
n=5 Participants
0 Participants
n=7 Participants
2 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
2 Participants
n=5 Participants
0 Participants
n=7 Participants
2 Participants
n=5 Participants
Race (NIH/OMB)
White
67 Participants
n=5 Participants
26 Participants
n=7 Participants
93 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
3 Participants
n=5 Participants
3 Participants
n=7 Participants
6 Participants
n=5 Participants
Region of Enrollment
United States
79 Participants
n=5 Participants
30 Participants
n=7 Participants
109 Participants
n=5 Participants

PRIMARY outcome

Timeframe: Baseline, Week 96

Population: Primary efficacy set: all participants in the efficacy set (all participants in eteplirsen-treated and untreated control groups who had at least 1 post-baseline functional assessment) who had a Baseline 6MWT distance of 300 to 450 meters, inclusive. Here, "Overall Number of Participants Analyzed"=participants evaluable for this outcome measure.

6MWT was performed by standardized procedures for all participants. Participants were asked to walk a set course of 25 meters for 6 minutes (timed), and the distance walked (in meters) was recorded. Change from baseline in 6MWT distance at Week 96 was reported.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=65 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=9 Participants
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Change From Baseline in the 6 Minute Walk Test (6MWT) Distance at Week 96
-117.91 meters
Standard Deviation 128.488
-133.56 meters
Standard Deviation 129.333

SECONDARY outcome

Timeframe: Baseline, Week 96

Population: Analysis Set consisted of a subset of participants who received at least 1 dose of eteplirsen and had both baseline and 1 post-dose muscle biopsy samples evaluable for dystrophin expression at Week 96. Here, "Overall Number of Participants Analyzed" signifies number of participants who were evaluable for this outcome measure. Data for this outcome measure was not planned to be collected and analyzed for the Untreated Control group.

Change from baseline in dystrophin protein levels (in muscle biopsy samples) were determined by Western blot. For each time point, 2 blocks of tissues were analyzed by Western blot, each with 2 replicates of gels to determine the dystrophin level as compared to a healthy individual (Percent Normal). The block average value from 2 replicate gels was computed. The overall average was calculated as the mean of the block average values. The overall average values were used for all analyses. In case only 1 gel was available for a block, then that value was used as the block average value.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=16 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Change From Baseline in Dystrophin Protein Levels Determined by Western Blot at Week 96
0.516 Percent Normal Dystrophin Protein Level
Standard Deviation 0.7236

SECONDARY outcome

Timeframe: Week 96

Population: Primary efficacy set: all participants in the efficacy set (all participants in eteplirsen-treated and untreated control groups who had at least 1 post-baseline functional assessment) who had a Baseline 6MWT distance of 300 to 450 meters, inclusive. Here, "Overall Number of Participants Analyzed"=participants evaluable for this outcome measure.

NSAA is a clinician-administered scale that rates participant performance on 17-items and included assessments of abilities such as 10-meter walk/run, rising from a sit to stand, standing on 1 leg, climbing a box step, descending a box step, rising from lying to sitting, rising from the floor, lifting the head, standing on heels, and jumping. For all activities, participants were graded as follows: 0 = unable to achieve goal independently; 1 = modified method but achieves goal independent of physical assistance from another and 2 = normal, no obvious modification of activity. Number of participants having ability to rise independently from the floor indicated by a NSAA Rise from floor sub score greater than 0 (unable to achieve goal independently) was reported.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=61 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=9 Participants
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Number of Participants Having Ability to Rise Independently From the Floor Determined Based on North Star Ambulatory Assessment (NSAA) at Week 96
33 Participants
3 Participants

SECONDARY outcome

Timeframe: Up to Week 96

Population: Primary efficacy set consisted of all participants in the efficacy set (all participants in eteplirsen-treated and untreated control groups who had at least 1 post-baseline functional assessment) who had a Baseline 6MWT distance of 300 to 450 meters, inclusive.

Number of participants who lost ambulation (LOA) by Week 96 was reported. Participant were considered non-ambulatory if each of the 3 conditions below were met: NSAA walk subscore was "0" (unable to achieve goal independently) on 2 consecutive days within a visit or NSAA was not done due to reason related to non-ambulation; 6MWT was not done with any reason related to permanent non-ambulation; and no later data showing this participant was still ambulatory. This was not required if non ambulatory status occurred at the time of early withdrawal or at the end of Week 96 assessment. NSAA is a 17-item scale to assess the participant's abilities; total score range from 0 (if all the activities are failed) to 34 (if all the activities are achieved) with higher scores indicating better performance on the assessment/ fully-independent function.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=67 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=20 Participants
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Number of Participants Who Lost Ambulation (LOA) by Week 96
12 Participants
1 Participants

SECONDARY outcome

Timeframe: Baseline, Week 96

Population: Primary efficacy set: all participants in the efficacy set (all participants in eteplirsen-treated and untreated control groups who had at least 1 post-baseline functional assessment) who had a Baseline 6MWT distance of 300 to 450 meters, inclusive. Here, "Overall Number of Participants Analyzed"=participants evaluable for this outcome measure.

FVC is the total amount of air exhaled during the forced expiratory volume test that is measured during spirometry; and is the most important measurement of lung function. This test requires participant to breath into a tube connected to a machine that measures the amount of air that can be moved in and out of the lungs after taking an inhaled bronchodilator medicine which is used to dilate participant's bronchial (breathing) tubes. Percent of predicted FVC = (observed value) / (predicted value) \* 100%.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=66 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=9 Participants
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Change From Baseline in Forced Vital Capacity Percent (FVC%) Predicted at Weeks 96
-3.413 Percentage of predicted FVC
Standard Deviation 12.4011
-2.461 Percentage of predicted FVC
Standard Deviation 9.6000

SECONDARY outcome

Timeframe: Baseline, Week 96

Population: Primary efficacy: all participants in the efficacy set (all participants in eteplirsen-treated and untreated control groups who had at least 1 post-baseline functional assessment) who had a Baseline 6MWT distance of 300 to 450 meters, inclusive. Here, "Overall Number of Participants Analyzed"=participants evaluable for this outcome measure.

NSAA is a clinician-administered scale that rates participant performance on 17-items and included assessments of abilities such as 10-meter walk/run, rising from a sit to stand, standing on 1 leg, climbing a box step, descending a box step, rising from lying to sitting, rising from the floor, lifting the head, standing on heels, and jumping. Participant were graded as follows: 0 = unable to achieve goal independently; 1 = modified method but achieves goal independent of physical assistance from another and 2 = normal, no obvious modification of activity. NSAA total score was derived by summing the scores for all the individual items and range from 0 (if all the activities are failed) to 34 (if all the activities are achieved) with higher scores indicating better performance on the assessment/ fully-independent function.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=61 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=9 Participants
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Change From Baseline in North Star Ambulatory Assessment (NSAA) Total Scores at Week 96
-7.23 Unit on scale
Standard Deviation 5.173
-8.44 Unit on scale
Standard Deviation 9.812

SECONDARY outcome

Timeframe: Baseline, Week 96

Population: Analysis Set consisted of a subset of participants who received at least 1 dose of eteplirsen and had both baseline and 1 post-dose muscle biopsy samples evaluable for dystrophin expression at Week 96. Here, "Overall Number of Participants Analyzed" signifies number of participants who were evaluable for this outcome measure. Data for this outcome measure was not planned to be collected and analyzed for the Untreated Control group.

Change from baseline in dystrophin intensity levels (in muscle biopsy samples) was determined by Immunohistochemistry.

Outcome measures

Outcome measures
Measure
Eteplirsen 30 mg/kg
n=16 Participants
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Change From Baseline in Dystrophin Intensity Levels Determined by Immunohistochemistry (IHC) at Week 96
0.030 Percent dystrophin positive fibers
Standard Deviation 0.0360

Adverse Events

Eteplirsen 30 mg/kg

Serious events: 11 serious events
Other events: 78 other events
Deaths: 0 deaths

Untreated Control Group (Non-exon 51 Amenable Participants)

Serious events: 2 serious events
Other events: 24 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Eteplirsen 30 mg/kg
n=79 participants at risk
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=30 participants at risk
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Injury, poisoning and procedural complications
Femoral neck fracture
2.5%
2/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Femur fracture
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Hip fracture
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Pneumonitis chemical
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Cardiac disorders
Arrhythmia
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Cardiac disorders
Myocarditis
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Acute respiratory failure
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Aspiration
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Nervous system disorders
Generalised tonic-clonic seizure
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Nervous system disorders
Loss of consciousness
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Gait disturbance
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Abasia
0.00%
0/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Psychiatric disorders
Aggression
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Psychiatric disorders
Major depression
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Skin and subcutaneous tissue disorders
Dermatitis contact
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Skin and subcutaneous tissue disorders
Urticaria
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Infections and infestations
Catheter site infection
1.3%
1/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Infections and infestations
Lymphadenitis viral
0.00%
0/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144

Other adverse events

Other adverse events
Measure
Eteplirsen 30 mg/kg
n=79 participants at risk
Participants with genotypically confirmed Duchenne muscular dystrophy (DMD) with genetic deletions amenable to treatment by exon 51 skipping received Eteplirsen as an Intravenous (IV) infusion, at a dose of 30 milligram per kilogram (mg/kg) once weekly for 96 weeks.
Untreated Control Group (Non-exon 51 Amenable Participants)
n=30 participants at risk
DMD participants with mutations amenable to skipping of any exon(s) except exon 51 did not receive any treatment, but completed study assessments up to 96 weeks.
Vascular disorders
Flushing
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Neoplasms benign, malignant and unspecified (incl cysts and polyps)
Skin papilloma
6.3%
5/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Immune system disorders
Seasonal allergy
17.7%
14/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Pyrexia
25.3%
20/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
General disorders
Non-cardiac chest pain
11.4%
9/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Fatigue
10.1%
8/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Catheter site pain
8.9%
7/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Peripheral swelling
6.3%
5/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Infusion site bruising
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
General disorders
Infusion site pain
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Psychiatric disorders
Anxiety
7.6%
6/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Psychiatric disorders
Insomnia
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Procedural pain
31.6%
25/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Contusion
30.4%
24/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Fall
27.8%
22/79 • From start of study drug administration to Week 144
20.0%
6/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Skin abrasion
26.6%
21/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Ligament sprain
15.2%
12/79 • From start of study drug administration to Week 144
10.0%
3/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Arthropod bite
12.7%
10/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Muscle strain
8.9%
7/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Laceration
5.1%
4/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Limb injury
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Spinal compression fracture
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Injury, poisoning and procedural complications
Torus fracture
0.00%
0/79 • From start of study drug administration to Week 144
6.7%
2/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Cough
45.6%
36/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Nasal congestion
31.6%
25/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Rhinorrhoea
27.8%
22/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Oropharyngeal pain
25.3%
20/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Epistaxis
13.9%
11/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Respiratory tract congestion
8.9%
7/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Dyspnoea
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Respiratory, thoracic and mediastinal disorders
Upper respiratory tract congestion
5.1%
4/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Nervous system disorders
Headache
50.6%
40/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Nervous system disorders
Dizziness
11.4%
9/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Nervous system disorders
Migraine
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Ear and labyrinth disorders
Ear pain
5.1%
4/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Vomiting
49.4%
39/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Diarrhoea
25.3%
20/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Nausea
21.5%
17/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Abdominal pain upper
17.7%
14/79 • From start of study drug administration to Week 144
10.0%
3/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Abdominal pain
10.1%
8/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Constipation
10.1%
8/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Gastrooesophageal reflux disease
6.3%
5/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Gastrointestinal disorders
Abdominal discomfort
5.1%
4/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Renal and urinary disorders
Proteinuria
10.1%
8/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Skin and subcutaneous tissue disorders
Rash
21.5%
17/79 • From start of study drug administration to Week 144
6.7%
2/30 • From start of study drug administration to Week 144
Skin and subcutaneous tissue disorders
Erythema
7.6%
6/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Back pain
36.7%
29/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Pain in extremity
32.9%
26/79 • From start of study drug administration to Week 144
6.7%
2/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Arthralgia
20.3%
16/79 • From start of study drug administration to Week 144
6.7%
2/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Myalgia
11.4%
9/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Muscle spasms
7.6%
6/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Musculoskeletal pain
7.6%
6/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Musculoskeletal and connective tissue disorders
Muscular weakness
5.1%
4/79 • From start of study drug administration to Week 144
6.7%
2/30 • From start of study drug administration to Week 144
Infections and infestations
Nasopharyngitis
36.7%
29/79 • From start of study drug administration to Week 144
10.0%
3/30 • From start of study drug administration to Week 144
Infections and infestations
Upper respiratory tract infection
31.6%
25/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Infections and infestations
Ear infection
13.9%
11/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Infections and infestations
Influenza
10.1%
8/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Infections and infestations
Gastroenteritis
8.9%
7/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Infections and infestations
Gastroenteritis viral
8.9%
7/79 • From start of study drug administration to Week 144
0.00%
0/30 • From start of study drug administration to Week 144
Infections and infestations
Pharyngitis streptococcal
7.6%
6/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144
Infections and infestations
Sinusitis
7.6%
6/79 • From start of study drug administration to Week 144
3.3%
1/30 • From start of study drug administration to Week 144

Additional Information

Medical Director

Sarepta Therapeutics, Inc.

Phone: +1-800-690-2003

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place

Restriction type: OTHER