Trial Outcomes & Findings for LDE225 for Patients With PTCH1 or SMO Mutated Tumors (NCT NCT02002689)

NCT ID: NCT02002689

Last Updated: 2016-05-02

Results Overview

Clinical benefit rate (CBR) Number and percentage of subjects with CBR (responses of CR, PR or SD ≥ 16 weeks) as assessed by investigator was reported for all patients along with 95% exact confidence interval (CI). Overall Response Rate (ORR) Overall response was to be determined by investigator assessment for each tumor in the study. For subjects with solid tumors, the assessment criteria was RECIST 1.1 and included responses of CR and/or PR. The number and percentage of subjects for different categories of overall response (e.g., for solid tumors - CR, PR, SD, PD, Not Evaluable) were to be provided for solid tumors, and each hematological tumor type (if applicable). Ninety-five percent (95%) exact CI was to be provided for the response rate(s) (e.g., for solid tumors - CRn and/or PR) as well.

Recruitment status

TERMINATED

Study phase

PHASE2

Target enrollment

10 participants

Primary outcome timeframe

16 weeks

Results posted on

2016-05-02

Participant Flow

The study was closed for accrual when the sponsor realized that not enough patients will be recruited for any meaningful stat analysis even if the study were kept open beyond the original planned accrual window.

Participant milestones

Participant milestones
Measure
Sonidegib
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Overall Study
STARTED
10
Overall Study
COMPLETED
0
Overall Study
NOT COMPLETED
10

Reasons for withdrawal

Reasons for withdrawal
Measure
Sonidegib
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Overall Study
Disease Progression
7
Overall Study
Adverse Event
3

Baseline Characteristics

LDE225 for Patients With PTCH1 or SMO Mutated Tumors

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Sonidegib
n=10 Participants
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Age, Categorical
<=18 years
0 Participants
n=5 Participants
Age, Categorical
Between 18 and 65 years
4 Participants
n=5 Participants
Age, Categorical
>=65 years
6 Participants
n=5 Participants
Age, Continuous
63.2 years
STANDARD_DEVIATION 7.64 • n=5 Participants
Sex: Female, Male
Female
6 Participants
n=5 Participants
Sex: Female, Male
Male
4 Participants
n=5 Participants

PRIMARY outcome

Timeframe: 16 weeks

Population: Full analysis set

Clinical benefit rate (CBR) Number and percentage of subjects with CBR (responses of CR, PR or SD ≥ 16 weeks) as assessed by investigator was reported for all patients along with 95% exact confidence interval (CI). Overall Response Rate (ORR) Overall response was to be determined by investigator assessment for each tumor in the study. For subjects with solid tumors, the assessment criteria was RECIST 1.1 and included responses of CR and/or PR. The number and percentage of subjects for different categories of overall response (e.g., for solid tumors - CR, PR, SD, PD, Not Evaluable) were to be provided for solid tumors, and each hematological tumor type (if applicable). Ninety-five percent (95%) exact CI was to be provided for the response rate(s) (e.g., for solid tumors - CRn and/or PR) as well.

Outcome measures

Outcome measures
Measure
Sonidegib
n=10 Participants
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Complete response (CR)
0 percent responders
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Partial response (PR)
0 percent responders
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Stable disease (SD)
0 percent responders
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Progressive disease (PD)
8 percent responders
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Non-evaluable (NE)
2 percent responders
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Overall response rate (ORR: CR+PR)
0 percent responders
Summary of Overall Response (ORR) and Clinical Benefit (CBR)
Clinical benefit rate (CBR: CR+PR+SD)
0 percent responders

SECONDARY outcome

Timeframe: 4 months

Population: Full Analysis set

Progression-free survival (PFS) is the time from the date of start of treatment to the date of event defined as the first documented progression or death due to any cause within 30 days of last dose. If a subject has not had an event, progression-free survival is censored at the date of last adequate tumor assessment.

Outcome measures

Outcome measures
Measure
Sonidegib
n=10 Participants
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Summary of Timing and Estimated Rate for Progression-free Survival (PFS) - Full Analysis Set
1 Month
88.9 % progression free surviors
Interval 43.3 to 98.4
Summary of Timing and Estimated Rate for Progression-free Survival (PFS) - Full Analysis Set
2 Months
33.3 % progression free surviors
Interval 7.8 to 62.3
Summary of Timing and Estimated Rate for Progression-free Survival (PFS) - Full Analysis Set
3 Months
33.3 % progression free surviors
Interval 7.8 to 62.3
Summary of Timing and Estimated Rate for Progression-free Survival (PFS) - Full Analysis Set
4 Months
0.0 % progression free surviors
limits not needed for 0 observations

SECONDARY outcome

Timeframe: 4 months

Outcome measures

Outcome measures
Measure
Sonidegib
n=10 Participants
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Kaplan-Meier Estimates of Progression Free Survival (PFS )Timing, Months
1.8 months
Interval 0.9 to 3.6

Adverse Events

LDE225

Serious events: 7 serious events
Other events: 10 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
LDE225
n=10 participants at risk
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Gastrointestinal disorders
Abdominal pain
20.0%
2/10
Gastrointestinal disorders
Dysphagia
10.0%
1/10
Gastrointestinal disorders
Small intestinal obstruction
10.0%
1/10
Infections and infestations
Pneumonia
10.0%
1/10
Metabolism and nutrition disorders
Dehydration
20.0%
2/10
Metabolism and nutrition disorders
Failure to thrive
10.0%
1/10
Musculoskeletal and connective tissue disorders
Muscular weakness
10.0%
1/10
Respiratory, thoracic and mediastinal disorders
Chronic obstructive pulmonary disease
10.0%
1/10
Respiratory, thoracic and mediastinal disorders
Cough
10.0%
1/10
Respiratory, thoracic and mediastinal disorders
Dysphonia
10.0%
1/10
Respiratory, thoracic and mediastinal disorders
Dyspnoea
10.0%
1/10
Respiratory, thoracic and mediastinal disorders
Pulmonary embolism
10.0%
1/10

Other adverse events

Other adverse events
Measure
LDE225
n=10 participants at risk
All the patients received sonidegib on a flat scale of 800 mg (e.g., 4 x 200 mg hard gelatin capsules) once daily on a continuous dosing cycle.
Blood and lymphatic system disorders
Anaemia
10.0%
1/10
Gastrointestinal disorders
Abdominal pain
20.0%
2/10
Gastrointestinal disorders
Constipation
30.0%
3/10
Gastrointestinal disorders
Diarrhoea
30.0%
3/10
Gastrointestinal disorders
Dyspepsia
10.0%
1/10
Gastrointestinal disorders
Dysphagia
10.0%
1/10
Gastrointestinal disorders
Nausea
80.0%
8/10
Gastrointestinal disorders
Vomiting
40.0%
4/10
General disorders
Asthenia
20.0%
2/10
General disorders
Fatigue
60.0%
6/10
General disorders
Oedema peripheral
10.0%
1/10
General disorders
Pain
10.0%
1/10
Infections and infestations
Urinary tract infection
30.0%
3/10
Investigations
Activated partial thromboplastin time prolonged
10.0%
1/10
Investigations
Alanine aminotransferase increased
30.0%
3/10
Investigations
Aspartate aminotransferase increased
30.0%
3/10
Investigations
Blood alkaline phosphatase increased
20.0%
2/10
Investigations
Blood creatine phosphokinase increased
30.0%
3/10
Investigations
Blood lactate dehydrogenase increased
10.0%
1/10
Investigations
Blood uric acid increased
10.0%
1/10
Investigations
Gamma-glutamyltransferase increased
30.0%
3/10
Investigations
Haemoglobin decreased
10.0%
1/10
Investigations
Weight decreased
40.0%
4/10
Investigations
White blood cell count decreased
10.0%
1/10
Metabolism and nutrition disorders
Decreased appetite
50.0%
5/10
Metabolism and nutrition disorders
Dehydration
10.0%
1/10
Metabolism and nutrition disorders
Hypercalcaemia
10.0%
1/10
Metabolism and nutrition disorders
Hyperglycaemia
20.0%
2/10
Metabolism and nutrition disorders
Hypoglycaemia
10.0%
1/10
Metabolism and nutrition disorders
Hypomagnesaemia
10.0%
1/10
Metabolism and nutrition disorders
Hyponatraemia
10.0%
1/10
Musculoskeletal and connective tissue disorders
Arthralgia
10.0%
1/10
Musculoskeletal and connective tissue disorders
Back pain
10.0%
1/10
Musculoskeletal and connective tissue disorders
Muscle spasms
20.0%
2/10
Musculoskeletal and connective tissue disorders
Musculoskeletal chest pain
10.0%
1/10
Musculoskeletal and connective tissue disorders
Myalgia
10.0%
1/10
Nervous system disorders
Dysgeusia
20.0%
2/10
Nervous system disorders
Headache
10.0%
1/10
Nervous system disorders
Neuropathy peripheral
10.0%
1/10
Psychiatric disorders
Depression
10.0%
1/10
Psychiatric disorders
Irritability
10.0%
1/10
Renal and urinary disorders
Proteinuria
30.0%
3/10
Respiratory, thoracic and mediastinal disorders
Cough
30.0%
3/10
Respiratory, thoracic and mediastinal disorders
Dyspnoea
10.0%
1/10
Respiratory, thoracic and mediastinal disorders
Pleural effusion
10.0%
1/10
Skin and subcutaneous tissue disorders
Alopecia
20.0%
2/10

Additional Information

Clinical Disclosure Office

Novartis Pharmaceuticals

Phone: 862-778-8300

Results disclosure agreements

  • Principal investigator is a sponsor employee The terms and conditions of Novartis' agreements with its investigators may vary. However, Novartis does not prohibit any investigator from publishing. Any publications from a single-site are postponed until the publication of the pooled data (ie, data from all sites) in the clinical trial.
  • Publication restrictions are in place

Restriction type: OTHER