Phase 2 Study of MP4CO to Treat Vaso-occlusive Sickle Crisis

NCT ID: NCT01925001

Last Updated: 2013-10-28

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

WITHDRAWN

Clinical Phase

PHASE2

Study Classification

INTERVENTIONAL

Study Start Date

2013-10-31

Study Completion Date

2015-10-31

Brief Summary

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Sickle Cell disease is caused by an inherited hemoglobin disorder. Healthy red blood cells are discoid and can deform and move through small blood vessels to carry oxygen to all parts of the body. In Sickle Cell disease, as red blood cells circulate and oxygen is released, the deoxygenated abnormal Hemoglobin S can begin to polymerize and cause red cells to become sticky and elongated. These "sickled" red cells are less flexible and will obstruct small blood vessels and prevent normal red cells from circulating freely, which limits oxygen delivery to tissues and organs. This is known as a "sickling crisis" or "vaso-occlusive crisis" and is the leading cause of hospitalization in patients with Sickle Cell disease.

Patients suffering from a sickle crisis experience severe pain and are at risk of stroke, heart attack or even death. Current therapy is limited to hydration and symptomatic pain relief. The administration of MP4CO as an adjunct treatment to standard therapy may alleviate pain associated with a sickling crisis and potentially reduce the severity and duration of a crisis. This may shorten the time in hospital and potentially improve the quality of life for patients with sickle cell anemia.

Detailed Description

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Sickle cell disease (SCD) is an autosomal recessive disorder of the β globin gene of the hemoglobin molecule. To date, no specific agent has been approved to treat a sickle cell crisis, to reduce the severity of a sickling crisis, or to shorten the duration of admission. Current therapy for a crisis is limited to hydration and symptomatic pain relief with opiates when pain is severe enough to cause admission to hospital. Administration of oxygen by inhalation alone has not proven effective. The carbon monoxide (CO) molecule binds to Hb S and, while attached, prevents and reverses polymerization of Hb S chains and the distortion of the red cell. CO at very low doses also acts as a cell-signaling molecule, and may reduce inflammation, decrease oxygen requirements, and prevent programmed cell death (apoptosis).

MP4CO is designed as an ischemic rescue therapy to deliver non-toxic levels of CO, to provide an immediate metabolic signal to cells to help reverse red cell sickling, and to reduce inflammation.

Previously published studies provide a foundation to postulate that MP4CO might have the appropriate properties for treatment or reversal of an acute sickling crisis. The initial release of CO from MP4CO is predicted to have a beneficial effect including immediate stabilization of Hb S to prevent further red cell polymerization and reverse existing sickling, dilation of capillaries to enhance tissue perfusion, and anti-inflammatory cell-signalling properties. The subsequent circulation of the MP4 molecule as an oxygen therapeutic (after converting to MP4OX following oxygenation in the lungs) will help to 1) preferentially oxygenate ischemic tissue, 2) reverse partially sickled red cells, and 3) improve perfusion and oxygenation of local tissues to potentially ameliorate the painful crisis caused by sickling of red cells. In addition, MP4CO has enhanced chemical stability, which enables storage at room temperature.

Conditions

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Anemia, Sickle Cell Sickle Cell Anemia Sickle Cell Disease Sickle Cell Disorders Hemoglobin SC Disease Sickle Cell Hemoglobin C Disease

Keywords

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Sickle cell anemia Sickle cell disease Sickling crisis Vaso-occlusive crisis Carboxyhemoglobin Oxygen therapeutic Ischemic rescue therapy Hemoglobin solution Pegylated hemoglobin

Study Design

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Allocation Method

RANDOMIZED

Intervention Model

CROSSOVER

Primary Study Purpose

TREATMENT

Blinding Strategy

TRIPLE

Participants Caregivers Investigators

Study Groups

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MP4CO

Escalating doses of MP4CO, administered intravenously

Group Type EXPERIMENTAL

MP4CO

Intervention Type DRUG

43 mg/mL pegylated carboxyhemoglobin \[≥ 90% CO hemoglobin saturation\] in physiological acetate electrolyte solution

Sodium chloride solution

Normal saline (0.9% Sodium Chloride Injection USP)administered intravenously

Group Type ACTIVE_COMPARATOR

Sodium chloride solution

Intervention Type DRUG

Normal saline solution (0.9% Sodium Chloride Injection USP)

Interventions

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MP4CO

43 mg/mL pegylated carboxyhemoglobin \[≥ 90% CO hemoglobin saturation\] in physiological acetate electrolyte solution

Intervention Type DRUG

Sodium chloride solution

Normal saline solution (0.9% Sodium Chloride Injection USP)

Intervention Type DRUG

Other Intervention Names

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Pegylated carboxyhemoglobin PEG carboxyhemoglobin Normal saline Sodium chloride USP 0.9% NaCl solution

Eligibility Criteria

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Inclusion Criteria

* Signed Informed Consent (and assent as required for minors)
* Diagnosis of SCD (known HbSS or HbSß0)
* Sixteen years of age or older
* Prior history of at least one VOC requiring hospitalization within the last 24 months

Exclusion Criteria

* ≥ 5 VOCs within the preceding 6 months requiring Emergency Room (ER) visits or hospital admissions
* History of overt stroke or cerebral vascular accident within the previous 12 months
* Remained in the hospital for ≥2 weeks (14 days) for VOC management within the previous 6 months
* Known pulmonary hypertension based on an estimated tricuspid regurgitant jet velocity (TRJV) \>2.90 m/s or definitive diagnosis by prior right heart catheterization
* Baseline SaO2 level by pulse oximetry \<92% on room air
* Systemic hypertension (baseline systolic pressure ≥ 160 mmHg or diastolic pressure ≥ 90 mmHg)
* History of myocardial infarction, myocardial ischemia, or angina
* On a chronic red blood cell transfusion therapy program (simple or exchange)
* Renal dysfunction presenting with a GFR\<60 mL/min/1.73m
* Any diagnosis of a concurrent chronic debilitating disease that may affect the completion of the study or results of the study as determined by the investigator
* Currently enrolled in any other investigational treatment study
* Significant substance abuse.
* Known to have HIV, active hepatitis B, or C infection, or active tuberculosis
Minimum Eligible Age

16 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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Sangart

INDUSTRY

Sponsor Role lead

Responsible Party

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Responsibility Role SPONSOR

Principal Investigators

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Tania Small, MD

Role: STUDY_DIRECTOR

Sangart, Inc., San Diego, CA

Swee Lay Thein, MD

Role: PRINCIPAL_INVESTIGATOR

King's College Hospital NHS Trust

Locations

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Salmaniya Medical Complex

Manama, , Bahrain

Site Status

University Hospital Brugmann

Brussels, , Belgium

Site Status

Rio de Janerio Instituto Estadual de Hematologie

Rio de Janerio, , Brazil

Site Status

Hôpital Henri Mondor

Créteil, , France

Site Status

Georges Pompidou European University Hospital

Paris, , France

Site Status

American Univ. of Beirut Medical Center

Beirut, , Lebanon

Site Status

Univ. Medical Center Rizk Hospital

Beirut, , Lebanon

Site Status

Academic Medical Center

Amsterdam, , Netherlands

Site Status

Cornell Medical City

Doha, , Qatar

Site Status

Cukurova University Medical Facilty

Adana, , Turkey (Türkiye)

Site Status

Mersin University Medical Faculty

Mersin, , Turkey (Türkiye)

Site Status

Guys Hospital

London, , United Kingdom

Site Status

King's College Hospital

London, , United Kingdom

Site Status

Queen Mary Hospital

London, , United Kingdom

Site Status

Countries

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Bahrain Belgium Brazil France Lebanon Netherlands Qatar Turkey (Türkiye) United Kingdom

References

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Vandegriff KD, Young MA, Lohman J, Bellelli A, Samaja M, Malavalli A, Winslow RM. CO-MP4, a polyethylene glycol-conjugated haemoglobin derivative and carbon monoxide carrier that reduces myocardial infarct size in rats. Br J Pharmacol. 2008 Aug;154(8):1649-61. doi: 10.1038/bjp.2008.219. Epub 2008 Jun 9.

Reference Type BACKGROUND
PMID: 18536756 (View on PubMed)

Vandegriff KD, Bellelli A, Samaja M, Malavalli A, Brunori M, Winslow RM. Kinetics of NO and O2 binding to a maleimide poly(ethylene glycol)-conjugated human haemoglobin. Biochem J. 2004 Aug 15;382(Pt 1):183-9. doi: 10.1042/BJ20040156.

Reference Type BACKGROUND
PMID: 15175010 (View on PubMed)

Tsai AG, Vandegriff KD, Intaglietta M, Winslow RM. Targeted O2 delivery by low-P50 hemoglobin: a new basis for O2 therapeutics. Am J Physiol Heart Circ Physiol. 2003 Oct;285(4):H1411-9. doi: 10.1152/ajpheart.00307.2003. Epub 2003 Jun 12.

Reference Type BACKGROUND
PMID: 12805024 (View on PubMed)

Cole RH, Vandegriff KD. MP4, a vasodilatory PEGylated hemoglobin. Adv Exp Med Biol. 2011;701:85-90. doi: 10.1007/978-1-4419-7756-4_12.

Reference Type BACKGROUND
PMID: 21445773 (View on PubMed)

Vandegriff KD, Malavalli A, Mkrtchyan GM, Spann SN, Baker DA, Winslow RM. Sites of modification of hemospan, a poly(ethylene glycol)-modified human hemoglobin for use as an oxygen therapeutic. Bioconjug Chem. 2008 Nov 19;19(11):2163-70. doi: 10.1021/bc8002666.

Reference Type BACKGROUND
PMID: 18837531 (View on PubMed)

Svergun DI, Ekstrom F, Vandegriff KD, Malavalli A, Baker DA, Nilsson C, Winslow RM. Solution structure of poly(ethylene) glycol-conjugated hemoglobin revealed by small-angle X-ray scattering: implications for a new oxygen therapeutic. Biophys J. 2008 Jan 1;94(1):173-81. doi: 10.1529/biophysj.107.114314. Epub 2007 Sep 7.

Reference Type BACKGROUND
PMID: 17827244 (View on PubMed)

Tsai AG, Cabrales P, Manjula BN, Acharya SA, Winslow RM, Intaglietta M. Dissociation of local nitric oxide concentration and vasoconstriction in the presence of cell-free hemoglobin oxygen carriers. Blood. 2006 Nov 15;108(10):3603-10. doi: 10.1182/blood-2006-02-005272. Epub 2006 Jul 20.

Reference Type BACKGROUND
PMID: 16857991 (View on PubMed)

Vandegriff KD, McCarthy M, Rohlfs RJ, Winslow RM. Colloid osmotic properties of modified hemoglobins: chemically cross-linked versus polyethylene glycol surface-conjugated. Biophys Chem. 1997 Nov;69(1):23-30. doi: 10.1016/s0301-4622(97)00079-3.

Reference Type BACKGROUND
PMID: 9440206 (View on PubMed)

Ballas SK, Gupta K, Adams-Graves P. Sickle cell pain: a critical reappraisal. Blood. 2012 Nov 1;120(18):3647-56. doi: 10.1182/blood-2012-04-383430. Epub 2012 Aug 24.

Reference Type BACKGROUND
PMID: 22923496 (View on PubMed)

Belcher JD, Young M, Chen C, Nguyen J, Burhop K, Tran P, Vercellotti GM. MP4CO, a pegylated hemoglobin saturated with carbon monoxide, is a modulator of HO-1, inflammation, and vaso-occlusion in transgenic sickle mice. Blood. 2013 Oct 10;122(15):2757-64. doi: 10.1182/blood-2013-02-486282. Epub 2013 Aug 1.

Reference Type BACKGROUND
PMID: 23908468 (View on PubMed)

Belcher JD, Mahaseth H, Welch TE, Otterbein LE, Hebbel RP, Vercellotti GM. Heme oxygenase-1 is a modulator of inflammation and vaso-occlusion in transgenic sickle mice. J Clin Invest. 2006 Mar;116(3):808-16. doi: 10.1172/JCI26857. Epub 2006 Feb 16.

Reference Type BACKGROUND
PMID: 16485041 (View on PubMed)

Bilban M, Haschemi A, Wegiel B, Chin BY, Wagner O, Otterbein LE. Heme oxygenase and carbon monoxide initiate homeostatic signaling. J Mol Med (Berl). 2008 Mar;86(3):267-79. doi: 10.1007/s00109-007-0276-0. Epub 2007 Nov 22.

Reference Type BACKGROUND
PMID: 18034222 (View on PubMed)

Piantadosi CA, Withers CM, Bartz RR, MacGarvey NC, Fu P, Sweeney TE, Welty-Wolf KE, Suliman HB. Heme oxygenase-1 couples activation of mitochondrial biogenesis to anti-inflammatory cytokine expression. J Biol Chem. 2011 May 6;286(18):16374-85. doi: 10.1074/jbc.M110.207738. Epub 2011 Mar 18.

Reference Type BACKGROUND
PMID: 21454555 (View on PubMed)

Powars DR, Chan LS, Hiti A, Ramicone E, Johnson C. Outcome of sickle cell anemia: a 4-decade observational study of 1056 patients. Medicine (Baltimore). 2005 Nov;84(6):363-376. doi: 10.1097/01.md.0000189089.45003.52.

Reference Type BACKGROUND
PMID: 16267411 (View on PubMed)

Related Links

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http://www.sangart.com

Sangart, Inc. (Sponsor home page)

Other Identifiers

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SCD-206

Identifier Type: -

Identifier Source: org_study_id