Trial Outcomes & Findings for Comparison of Cortisol Pump With Standard Treatment for Congenital Adrenal Hyperplasia (NCT NCT01859312)

NCT ID: NCT01859312

Last Updated: 2017-12-22

Results Overview

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

8 participants

Primary outcome timeframe

At baseline

Results posted on

2017-12-22

Participant Flow

Eight adult patients with classic CAH due to 21-hydroxylase deficiency participated in this study. Four were recruited from a pool of 147 patients enrolled on a natural history study at the NIH natural history study (NCT00250159); 4 were recruited through advertisements.

Participant milestones

Participant milestones
Measure
Continuous Sub-Q Hydrocortisone Infusion
Enrolled participants with congenital adrenal hyperplasia (CAH) received continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to achieve near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Overall Study
STARTED
8
Overall Study
COMPLETED
8
Overall Study
NOT COMPLETED
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

Comparison of Cortisol Pump With Standard Treatment for Congenital Adrenal Hyperplasia

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Continuous Sub-Q Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Age, Categorical
<=18 years
0 Participants
n=5 Participants
Age, Categorical
Between 18 and 65 years
8 Participants
n=5 Participants
Age, Categorical
>=65 years
0 Participants
n=5 Participants
Sex: Female, Male
Female
5 Participants
n=5 Participants
Sex: Female, Male
Male
3 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
0 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
8 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
0 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
0 Participants
n=5 Participants
Race (NIH/OMB)
White
8 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Region of Enrollment
United States
5 Participants
n=5 Participants
Region of Enrollment
Canada
3 Participants
n=5 Participants
Phenotype
Simple Virilizing (SV)
2 Participants
n=5 Participants
Phenotype
Salt-wasting (SW)
6 Participants
n=5 Participants

PRIMARY outcome

Timeframe: At baseline

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Number of Patients With 17-OHP Levels Equal or Below 1,200 ng/dL at 0700
0 Participants

PRIMARY outcome

Timeframe: At 6 months

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Number of Patients With 17-OH Progesterone Levels Equal or Below 1,200 ng/dL at 0700
3 Participants

SECONDARY outcome

Timeframe: At baseline

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP at 0700
8313 ng/dL
Standard Error 2748

SECONDARY outcome

Timeframe: At 6 months

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP at 0700
2150 ng/dL
Standard Error 531

SECONDARY outcome

Timeframe: At baseline

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - 24 Hours
98.5 h*mcg/dL
Standard Error 39.3

SECONDARY outcome

Timeframe: At 6 months

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - 24 Hours
25.7 h*mcg/dL
Standard Error 9.5

SECONDARY outcome

Timeframe: At baseline

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - Daytime (0700-1500)
48.6 h*mcg/dL
Standard Error 22.4

SECONDARY outcome

Timeframe: At 6 months

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - Daytime (0700-1500)
6.8 h*mcg/dL
Standard Error 1.8

SECONDARY outcome

Timeframe: At baseline

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficienc. AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - Midday (1500 - 2300)
20.5 h*mcg/dL
Standard Error 6.8

SECONDARY outcome

Timeframe: At 6 months

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - Midday (1500 - 2300)
7.5 h*mcg/dL
Standard Error 4.9

SECONDARY outcome

Timeframe: At baseline

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - Nighttime (2300 - 0700)
29.5 h*mcg/dL
Standard Error 11.1

SECONDARY outcome

Timeframe: At 6 months

17-OHP (17-hydroxyprogesterone) is a laboratory blood test to test for congenital adrenal hyperplasia (CAH) due to 21-hydroxylase deficiency. AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of 17-OHP Area Under the Curve (AUC) - Nighttime (2300 - 0700)
11.4 h*mcg/dL
Standard Error 3.0

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Androstenedione at 0700.

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione at 0700
748 ng/dL
Standard Error 295

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Androstenedione at 0700.

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione at 0700
317 ng/dL
Standard Error 77

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - 24 hours. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - 24 Hours
12.7 h*mcg/dL
Standard Error 4.5

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Androstenedione area under the curve (AUC) - 24 hours. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - 24 Hours
5.2 h*mcg/dL
Standard Error 1.4

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Daytime (0700-1500). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Daytime (0700-1500)
5.3 h*mcg/dL
Standard Error 2.1

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Daytime (0700-1500). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Daytime (0700-1500)
1.8 h*mcg/dL
Standard Error 0.4

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Midday (1500 - 2300). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Midday (1500 - 2300)
3.7 h*mcg/dL
Standard Error 1.1

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Midday (1500 - 2300). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Midday (1500 - 2300)
1.6 h*mcg/dL
Standard Error 0.6

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Nighttime (2300 - 0700). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Nighttime (2300 - 0700)
3.7 h*mcg/dL
Standard Error 1.3

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Nighttime (2300 - 0700). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Androstenedione Area Under the Curve (AUC) - Nighttime (2300 - 0700)
1.8 h*mcg/dL
Standard Error 0.4

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of ACTH at 0700.

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH at 0700
405 pg/mL
Standard Error 114

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of ACTH at 0700.

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH at 0700
139 pg/mL
Standard Error 47

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of ACTH Area Under the Curve (AUC) - 24 Hours. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300.Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - 24 Hours
2538 h*pg/mL
Standard Error 743

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of ACTH Area Under the Curve (AUC) - 24 Hours. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - 24 Hours
1087 h*pg/mL
Standard Error 359

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of ACTH Area Under the Curve (AUC) - Daytime (0700-1500). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - Daytime (0700-1500)
1239 h*pg/mL
Standard Error 402

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of ACTH Area Under the Curve (AUC) - Daytime (0700-1500). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - Daytime (0700-1500)
340 h*pg/mL
Standard Error 107

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of ACTH Area Under the Curve (AUC) - Midday (1500 - 2300). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - Midday (1500 - 2300)
458 h*pg/mL
Standard Error 179

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of ACTH Area Under the Curve (AUC) - Midday (1500 - 2300). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - Midday (1500 - 2300)
183 h*pg/mL
Standard Error 55

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of ACTH Area Under the Curve (AUC) - Nighttime (2300 - 0700). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - Nighttime (2300 - 0700)
841 h*pg/mL
Standard Error 233

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of ACTH Area Under the Curve (AUC) - Nighttime (2300 - 0700). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of ACTH Area Under the Curve (AUC) - Nighttime (2300 - 0700)
564 h*pg/mL
Standard Error 216

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Progesterone at 0700

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Progesterone Levels at 0700
9.5 ng/mL
Standard Error 5.4

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Progesterone at 0700

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Progesterone Level at 0700
0.8 ng/mL
Standard Error 0.4

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Progesterone area under the curve (AUC) - 24 hours. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - 24 Hours
101.1 h*ng/dL
Standard Error 48.8

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Progesterone area under the curve (AUC) - 24 hours. AUC was calculated using the linear-up log-down trapezoidal rule for the entire 24 hours and samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700, 0900, 1100, 1300, 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - 24 Hours
13.7 h*ng/dL
Standard Error 4.6

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Progesterone area under the curve (AUC) - Daytime (0700-1500). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - Daytime (0700-1500)
42.2 h*ng/dL
Standard Error 20.0

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Progesterone area under the curve (AUC) - Daytime (0700-1500). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour daytime level, samples were obtained every 2 hours beginning at 0700, 0900, 1100, 1300, 1500. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - Daytime (0700-1500)
4.2 h*ng/dL
Standard Error 1.6

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Progesterone area under the curve (AUC) - Midday (1500 - 2300). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - Midday (1500 - 2300)
30.7 h*ng/dL
Standard Error 17.7

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Progesterone area under the curve (AUC) - Midday (1500 - 2300). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour midday level, samples were obtained every 2 hours beginning at 1500, 1700, 1900, 2100, 2300. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - Midday (1500 - 2300)
5.5 h*ng/dL
Standard Error 3.2

SECONDARY outcome

Timeframe: At baseline

Participants Mean Level of Progesterone area under the curve (AUC) - Nighttime (2300 - 0700). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - Nighttime (2300 - 0700)
28.2 h*ng/dL
Standard Error 12.5

SECONDARY outcome

Timeframe: At 6 months

Participants Mean Level of Progesterone area under the curve (AUC) - Nighttime (2300 - 0700). AUC was calculated using the linear-up log-down trapezoidal rule for the 8 hour nighttime level, samples were obtained every 2 hours beginning at 2300, 0100, 0300, 0500, 0700. Actual collection times were used to define peak plasma concentration (Cmax) and time to peak plasma concentration (Tmax).

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participants Mean Level of Progesterone Area Under the Curve (AUC) - Nighttime (2300 - 0700)
4.0 h*ng/dL
Standard Error 0.5

SECONDARY outcome

Timeframe: At baseline

lean body mass measured by DEXA, Hologic Discovery-A

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participant Lean Body Mass
60.7 kg
Standard Error 3.7

SECONDARY outcome

Timeframe: At 6 months

lean body mass measured by DEXA, Hologic Discovery-A

Outcome measures

Outcome measures
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 Participants
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Participant Lean Body Mass
64.3 kg
Standard Error 4.4

Adverse Events

Continuous Subcutaneous Hydrocortisone Infusion

Serious events: 0 serious events
Other events: 8 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Other adverse events
Measure
Continuous Subcutaneous Hydrocortisone Infusion
n=8 participants at risk
Enrolled participants with congenital adrenal hyperplasia (CAH) will receive continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722Na) to deliver near-physiologic cortisol replacement therapy Hydrocortisone (Solucortef): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA) Insulin pump (Medtronic): Continuous subcutaneous hydrocortisone infusion (CSHI) via Medtronic insulin pump (MMT-722NA)
Skin and subcutaneous tissue disorders
Skin erythema with pruritis at the infusion set site
37.5%
3/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Skin and subcutaneous tissue disorders
Local skin infection at the infusion set site
62.5%
5/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Nervous system disorders
Dizziness
62.5%
5/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Nervous system disorders
Lightheadedness
62.5%
5/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Musculoskeletal and connective tissue disorders
Weakness
37.5%
3/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
General disorders
Fatigue
87.5%
7/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Gastrointestinal disorders
Nausea
25.0%
2/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Nervous system disorders
Headache
87.5%
7/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Musculoskeletal and connective tissue disorders
Carpal tunnel
12.5%
1/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Musculoskeletal and connective tissue disorders
Knee pain when walking
12.5%
1/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Ear and labyrinth disorders
Tinnutus
12.5%
1/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Gastrointestinal disorders
Decreased appetite
25.0%
2/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Gastrointestinal disorders
Increased appetite
75.0%
6/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
General disorders
Difficulty falling asleep or frequent wakening
62.5%
5/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
General disorders
Early morning wakening
37.5%
3/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
Skin and subcutaneous tissue disorders
Increased acne
25.0%
2/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)
General disorders
Weight gain
62.5%
5/8 • At 6 months. Subjects that select the option of continuing CSHI therapy for 1 additional year will be monitored for 1 year, 6 months.
IRB granted a waiver of reporting the following anticipated adverse events (non-UP adverse events) unless they occurring in greater frequency than expected: 1. Local skin reaction (50%) 2. Local skin infection requiring local or antibiotic treatment (10%) 3. Minimal bleeding after removal of the infusion set (90%)

Additional Information

Deborah P. Merke, MD, MS

National Institute of Child Health and Human Development (NICHD)

Phone: 301-496-0718

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place