Trial Outcomes & Findings for Brentuximab Vedotin in Treating Patients With Advanced Systemic Mastocytosis or Mast Cell Leukemia (NCT NCT01807598)

NCT ID: NCT01807598

Last Updated: 2019-01-29

Results Overview

Overall response rate (ORR) is sum of complete response (CR); partial response (PR); and clinical improvement (CI) in 1 year, ie, ORR=CR+PR+CI. The outcome is the number of participants without dispersion. CR is following with response duration(RD) ≥12 weeks (wk) * No mast cell disease * Tryptase \<20 ng/mL * Neutrophils ≥1x10e9/L with normal differential * Hemoglobin ≥11 g/dL * Platelets ≥100x10e9/L * No hepatosplenomegaly * No systemic mastocytosis(SM)-related organ damage PR is following with RD ≥12wk * Neither CR or progressive disease(PD) * Neoplastic mast cells reduced ≥50% * Tryptase reduced ≥50% * 1+ disease finding resolved CI is following with RD ≥12wk * Neither CR; PR; or PD * 1+ of findings above Stable disease (SD) Not CR, PR, Cl, or PD Progressive disease (PD) Any of: * Worsening organ damage * Doubling of laboratory abnormality * New transfusion dependence of ≥4 units red cells or platelets at 8wk •+ ≥100% in transfusions for 8wk * 10-cm+ splenomegaly

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

10 participants

Primary outcome timeframe

Up to 1 year

Results posted on

2019-01-29

Participant Flow

Participant milestones

Participant milestones
Measure
Brentuximab Vedotin
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Overall Study
STARTED
10
Overall Study
COMPLETED
4
Overall Study
NOT COMPLETED
6

Reasons for withdrawal

Reasons for withdrawal
Measure
Brentuximab Vedotin
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Overall Study
Withdrawal by Subject
4
Overall Study
Adverse Event
1
Overall Study
Other Physician Decision
1

Baseline Characteristics

Brentuximab Vedotin in Treating Patients With Advanced Systemic Mastocytosis or Mast Cell Leukemia

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Brentuximab Vedotin
n=10 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Age, Categorical
<=18 years
0 Participants
n=5 Participants
Age, Categorical
Between 18 and 65 years
4 Participants
n=5 Participants
Age, Categorical
>=65 years
6 Participants
n=5 Participants
Age, Continuous
65.8 Years
n=5 Participants
Sex: Female, Male
Female
6 Participants
n=5 Participants
Sex: Female, Male
Male
4 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
0 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
10 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
1 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
0 Participants
n=5 Participants
Race (NIH/OMB)
White
9 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
0 Participants
n=5 Participants
Region of Enrollment
United States
10 participants
n=5 Participants

PRIMARY outcome

Timeframe: Up to 1 year

Population: 1 of 10 participants were not evaluable due to early death during Cycle 1 (considered unrelated to study treatment)

Overall response rate (ORR) is sum of complete response (CR); partial response (PR); and clinical improvement (CI) in 1 year, ie, ORR=CR+PR+CI. The outcome is the number of participants without dispersion. CR is following with response duration(RD) ≥12 weeks (wk) * No mast cell disease * Tryptase \<20 ng/mL * Neutrophils ≥1x10e9/L with normal differential * Hemoglobin ≥11 g/dL * Platelets ≥100x10e9/L * No hepatosplenomegaly * No systemic mastocytosis(SM)-related organ damage PR is following with RD ≥12wk * Neither CR or progressive disease(PD) * Neoplastic mast cells reduced ≥50% * Tryptase reduced ≥50% * 1+ disease finding resolved CI is following with RD ≥12wk * Neither CR; PR; or PD * 1+ of findings above Stable disease (SD) Not CR, PR, Cl, or PD Progressive disease (PD) Any of: * Worsening organ damage * Doubling of laboratory abnormality * New transfusion dependence of ≥4 units red cells or platelets at 8wk •+ ≥100% in transfusions for 8wk * 10-cm+ splenomegaly

Outcome measures

Outcome measures
Measure
Brentuximab Vedotin
n=9 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Overall Response Rate (ORR) Per Consensus International Response Criteria (Rate of Complete or Partial Remissions or Clinical Improvement)
0 participants

SECONDARY outcome

Timeframe: Up to 1 year

Toxicity was assessed as the number of adverse events considered possibly, probably, or definitely-related to treatment with brentuximab vedotin. The outcome is reported as the total number of related events, a number without dispersion, and the number of related events (without dispersion) considered to be either a hematologic toxicity or non-hematologic toxicity.

Outcome measures

Outcome measures
Measure
Brentuximab Vedotin
n=10 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Brentuximab Vedotin Toxicity
Related hematologic toxicity
12 Related adverse events
Brentuximab Vedotin Toxicity
Related non-hematologic toxicity
24 Related adverse events
Brentuximab Vedotin Toxicity
Total related adverse events (toxicities)
36 Related adverse events

SECONDARY outcome

Timeframe: Baseline and up to 1 year

Population: CD30 marker data was not obtained for some participants.

The presence of the CD30 marker (epitope) on neoplastic (cancerous) mast cells in core bone marrow biopsy samples was assessed by immunohistochemical methods, before and after brentuximab vedotin treatment. CD30 is a member of the TNF-receptor (TNF-R) superfamily, and is a transmembrane glycoprotein receptor that is normally at very low levels on the surface of activated T-cells. Overexpression of the CD30 marker is indicative of T-cell lymphoproliferative disorders and neoplastic mast cells, and the effect of a particular treatment on CD30 expression may be related to the efficacy of that treatment. The outcome is reported as the median percentage change in the level of CD30 detected, reported with full range.

Outcome measures

Outcome measures
Measure
Brentuximab Vedotin
n=8 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Percent Change of CD30 Expression on Neoplastic Mast Cells
-1 percentage change in CD30+ cells
Interval -62.0 to 45.0

SECONDARY outcome

Timeframe: Up to 1 year

The clinical effect of patient symptoms associated with systemic mastocytosis or mast cell leukemia were assessed with the patient-reported outcome survey entitled Myeloproliferative Neoplasm Symptom Assessment Form with Mast Cell Disorder Symptoms \[(MPN-SAF(MCD)\]. The MPN-SAF(MCD) is a 36-question survey, with possible responses ranged from 0 to 10, with 0 indicating not present or no effect; 1 meaning present but most favorable; and 10 meaning worst imaginable (least favorable). Total range is 0 to 360, with 0 being best possible, and 360 being worst possible. Total symptom score is calculated as the sum of the individual survey scores reported at baseline and after treatment, with lower numbers indicating less effect, and larger numbers indicated greater effect. The outcome is reported as mean score value with dispersion.

Outcome measures

Outcome measures
Measure
Brentuximab Vedotin
n=10 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Myeloproliferative Neoplasm Symptom Assessment Form (MPN-SAF) Total Symptom Score
Baseline (Pre-treatment)
36.2 score on a scale
Standard Deviation 18.1
Myeloproliferative Neoplasm Symptom Assessment Form (MPN-SAF) Total Symptom Score
After Treatment
23.6 score on a scale
Standard Deviation 15.6

SECONDARY outcome

Timeframe: Up to 1 year

Overall quality of life (QoL) was assessed by a single specific question from the 36-question Myeloproliferative Neoplasm Symptom Assessment Form with Mast Cell Disorder Symptoms \[(MPN-SAF(MCD)\] survey. Possible responses for theQoL question range from 0 to 10, with 0 indicating "as good as it can be" (most favorable), and 10 meaning "as bad as it can be" (least favorable). The QoL score was obtained at baseline and after treatment. The outcome is reported as mean score with dispersion.

Outcome measures

Outcome measures
Measure
Brentuximab Vedotin
n=10 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Quality of Life (QoL) Score Using a Modified Myeloproliferative Neoplasm Symptom Assessment Form (MPN-SAF)
Baseline (Pre-treatment)
5 score on a scale
Standard Deviation 2.7
Quality of Life (QoL) Score Using a Modified Myeloproliferative Neoplasm Symptom Assessment Form (MPN-SAF)
After Treatment
2.6 score on a scale
Standard Deviation 2.7

SECONDARY outcome

Timeframe: Up to 1 year

Population: Duration of response (DOR) can not be determined if no participants had a response.

Duration of response (DOR) is defined as the time from the start of the first confirmed response until the date of the first documented and confirmed disease progression or death due to ASM or MCL. For participants with a confirmed clinical response, the outcome was to be reported as the median DOR with standard deviation.

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Up to 1 year

Population: Time to response (TTR) can not be determined if no participants had a response.

Time to response (TTR) is defined as the time from the date of start of treatment to the date of first confirmed response. For participants with a confirmed clinical response, the outcome was to be reported as the median TTR with standard deviation.

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Up to 1 year

Progression-free survival (PFS) is defined as the time from the date of start of treatment until disease progression; death; or initiation of new therapy. The outcome is reported as the mean number of days of PFS, with 95% confidence interval. Progressive disease (PD) is any of the following: * Worsening of any organ damage * Doubling of any laboratory abnormality * New transfusion dependence of ≥ 4 units red cells or platelets at 8 wk * ≥ 100% increase in transfusions for 8 wk * 10-cm+ splenomegaly

Outcome measures

Outcome measures
Measure
Brentuximab Vedotin
n=10 Participants
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Progression-free Survival (PFS)
210 Days
Interval 77.0 to 343.0

Adverse Events

Brentuximab Vedotin

Serious events: 4 serious events
Other events: 10 other events
Deaths: 1 deaths

Serious adverse events

Serious adverse events
Measure
Brentuximab Vedotin
n=10 participants at risk
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Nervous system disorders
Intracranial hemorrhage
10.0%
1/10 • Number of events 1 • 1 year
Hepatobiliary disorders
Portal vein thrombosis
10.0%
1/10 • Number of events 1 • 1 year
Respiratory, thoracic and mediastinal disorders
Respiratory, thoracic and mediastinal disorders - Other, Epiglottitis
10.0%
1/10 • Number of events 1 • 1 year
Respiratory, thoracic and mediastinal disorders
Pleural effusion
10.0%
1/10 • Number of events 1 • 1 year

Other adverse events

Other adverse events
Measure
Brentuximab Vedotin
n=10 participants at risk
Subjects receive a 30-minute IV infusion of brentuximab vedotin once every 21 days for 8 courses, in the absence of disease progression or unacceptable toxicity.
Blood and lymphatic system disorders
Neutropenia
30.0%
3/10 • Number of events 11 • 1 year
Blood and lymphatic system disorders
Anemia
20.0%
2/10 • Number of events 3 • 1 year
Blood and lymphatic system disorders
Thrombocytopenia
10.0%
1/10 • Number of events 1 • 1 year
General disorders
Fatigue
40.0%
4/10 • Number of events 9 • 1 year
Gastrointestinal disorders
Abdominal Pain
20.0%
2/10 • Number of events 4 • 1 year
Metabolism and nutrition disorders
Anorexia
20.0%
2/10 • Number of events 3 • 1 year
Gastrointestinal disorders
Constipation
20.0%
2/10 • Number of events 2 • 1 year
Respiratory, thoracic and mediastinal disorders
Cough
20.0%
2/10 • Number of events 2 • 1 year
Psychiatric disorders
Depression
20.0%
2/10 • Number of events 2 • 1 year
Gastrointestinal disorders
Diarrhea
20.0%
2/10 • Number of events 3 • 1 year
Respiratory, thoracic and mediastinal disorders
Dyspnea
20.0%
2/10 • Number of events 2 • 1 year
General disorders
Infusion Related Reaction
20.0%
2/10 • Number of events 5 • 1 year
Skin and subcutaneous tissue disorders
Rash
20.0%
2/10 • Number of events 4 • 1 year
Gastrointestinal disorders
Vomiting
20.0%
2/10 • Number of events 3 • 1 year
Gastrointestinal disorders
Ascites
10.0%
1/10 • Number of events 1 • 1 year
Gastrointestinal disorders
Dysphagia
10.0%
1/10 • Number of events 1 • 1 year
Gastrointestinal disorders
Nausea
10.0%
1/10 • Number of events 1 • 1 year
Gastrointestinal disorders
Oral pain
10.0%
1/10 • Number of events 1 • 1 year
General disorders
Edema limbs
10.0%
1/10 • Number of events 1 • 1 year
General disorders
Fever
10.0%
1/10 • Number of events 1 • 1 year
Skin and subcutaneous tissue disorders
Alopecia
10.0%
1/10 • Number of events 1 • 1 year
Skin and subcutaneous tissue disorders
Dry skin
10.0%
1/10 • Number of events 1 • 1 year
Skin and subcutaneous tissue disorders
Hyperhidrosis
10.0%
1/10 • Number of events 1 • 1 year
Skin and subcutaneous tissue disorders
Pruritus
10.0%
1/10 • Number of events 1 • 1 year
Infections and infestations
Sinusitis
10.0%
1/10 • Number of events 1 • 1 year
Infections and infestations
Upper respiratory infection
10.0%
1/10 • Number of events 1 • 1 year
Infections and infestations
Vaginal infection
10.0%
1/10 • Number of events 1 • 1 year
Infections and infestations
Wound infection
10.0%
1/10 • Number of events 1 • 1 year
Respiratory, thoracic and mediastinal disorders
Pleural effusion
10.0%
1/10 • Number of events 1 • 1 year
Respiratory, thoracic and mediastinal disorders
Postnasal drip
10.0%
1/10 • Number of events 1 • 1 year
Respiratory, thoracic and mediastinal disorders
Sore throat
10.0%
1/10 • Number of events 1 • 1 year
Metabolism and nutrition disorders
Dehydration
10.0%
1/10 • Number of events 1 • 1 year
Metabolism and nutrition disorders
Hypoalbuminemia
10.0%
1/10 • Number of events 2 • 1 year
Psychiatric disorders
Insomnia
10.0%
1/10 • Number of events 1 • 1 year
Ear and labyrinth disorders
Ear pain
10.0%
1/10 • Number of events 1 • 1 year
Eye disorders
Watering eyes
10.0%
1/10 • Number of events 1 • 1 year
Musculoskeletal and connective tissue disorders
Pain in extremity
10.0%
1/10 • Number of events 1 • 1 year
Renal and urinary disorders
Urinary frequency
10.0%
1/10 • Number of events 1 • 1 year

Additional Information

Jason R. Gotlib

Stanford University

Phone: 650-736-1253

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place