Trial Outcomes & Findings for A Retrospective Study of the Natural History of Patients With Severe Perinatal and Infantile Hypophosphatasia (HPP) (NCT NCT01419028)

NCT ID: NCT01419028

Last Updated: 2019-04-01

Results Overview

Overall survival is defined as the time from birth to time of death.

Recruitment status

COMPLETED

Target enrollment

48 participants

Primary outcome timeframe

Retrospective data collected on or before the data of abstraction.

Results posted on

2019-04-01

Participant Flow

Patients were enrolled between Sept 2012 and Apr 2013. 65 patients were screened and 48 were enrolled at 12 sites in 7 countries. Patients were recruited from investigational sites established at academic research and medical centers known to diagnose and/or treat patients with HPP. Both living and deceased patients were considered to partricipate.

Participant milestones

Participant milestones
Measure
Retrospective Observational
Patients with severe perinatal and/or infantile onset HPP (ie, where signs of the disease are present before 6 months of age).
Overall Study
STARTED
48
Overall Study
COMPLETED
48
Overall Study
NOT COMPLETED
0

Reasons for withdrawal

Withdrawal data not reported

Baseline Characteristics

A Retrospective Study of the Natural History of Patients With Severe Perinatal and Infantile Hypophosphatasia (HPP)

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Retrospective Observational
n=48 Participants
Patients with severe perinatal and/or infantile onset HPP (ie, where signs of the disease are present before 6 months of age).
Age, Continuous
506.9 weeks
STANDARD_DEVIATION 319.24 • n=5 Participants
Age, Customized
<=18 years
10 weeks
n=5 Participants
Age, Customized
Between 18 and 65 years
3 weeks
n=5 Participants
Age, Customized
>=65 years
0 weeks
n=5 Participants
Sex: Female, Male
Female
22 Participants
n=5 Participants
Sex: Female, Male
Male
26 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
1 Participants
n=5 Participants
Race (NIH/OMB)
Asian
2 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
3 Participants
n=5 Participants
Race (NIH/OMB)
White
40 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
2 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Hispanic or Latino
1 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Not Hispanic or Latino
41 Participants
n=5 Participants
Ethnicity (NIH/OMB)
Unknown or Not Reported
6 Participants
n=5 Participants
Region of Enrollment
Australia
2 participants
n=5 Participants
Region of Enrollment
Canada
11 participants
n=5 Participants
Region of Enrollment
Germany
6 participants
n=5 Participants
Region of Enrollment
Spain
1 participants
n=5 Participants
Region of Enrollment
Switzerland
1 participants
n=5 Participants
Region of Enrollment
Taiwan
1 participants
n=5 Participants
Region of Enrollment
United States
26 participants
n=5 Participants

PRIMARY outcome

Timeframe: Retrospective data collected on or before the data of abstraction.

Overall survival is defined as the time from birth to time of death.

Outcome measures

Outcome measures
Measure
Retrospective Observational
n=48 Participants
Patients with severe perinatal and/or infantile onset HPP (ie, where signs of the disease are present before 6 months of age).
Survival
270.5 days
Interval 155.0 to 428.0

SECONDARY outcome

Timeframe: Retrospective data collected on or before the date of abstraction.

Invasive ventilator-free survival is defined as the time during which the patient is alive and not invasively ventilated. For the purpose of this study, invasive ventilation is defined as mechanical ventilation via intubation of trachaeostomy.

Outcome measures

Outcome measures
Measure
Retrospective Observational
n=48 Participants
Patients with severe perinatal and/or infantile onset HPP (ie, where signs of the disease are present before 6 months of age).
Invasive Ventilator-free Survival Time
236 days
Interval 78.0 to 300.0

Adverse Events

Retrospective Observational

Serious events: 0 serious events
Other events: 0 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Adverse event data not reported

Additional Information

Alexion Pharmaceuticals

Alexion International Sarl

Results disclosure agreements

  • Principal investigator is a sponsor employee Participation in a multicenter study involves a commitment to publish the data from the study in a cooperative publication prior to release of study results on an individual basis. Therefore, PIs are subject to certain disclosure and publication limitations.
  • Publication restrictions are in place

Restriction type: OTHER