Trial Outcomes & Findings for Effect of Glycine in Cystic Fibrosis (NCT NCT01417481)

NCT ID: NCT01417481

Last Updated: 2014-11-05

Results Overview

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Then, percentages were log-transformed to adjust to a normal distribution.

Recruitment status

TERMINATED

Study phase

PHASE2

Target enrollment

13 participants

Primary outcome timeframe

8 weeks

Results posted on

2014-11-05

Participant Flow

Patients attending the Hospital Infantil de México and the Instituto Mexicano del Seguro Social (both in Mexico city) were recruited from March 7, 2012 to October 31, 2012. The two arms of the study were: 1) Glycine, then placebo, and 2) Placebo, then glycine.

Participant milestones

Participant milestones
Measure
Glycine, Then Placebo
First intervention (8 weeks) with Glycine (0.5 g/kg/day divided in three doses). Washout period of 2 weeks. Second intervention (8 weeks) with Placebo (sugar glass, 0.5 g/kg/day divided in three doses).
Placebo, Then Glycine
First intervention (8 weeks) with Placebo (sugar glass, 0.5 g/kg/day divided in three doses). Washout period of 2 weeks. Second intervention (8 weeks) with Glycine (0.5 g/kg/day divided in three doses).
First Intervention (8 Weeks)
STARTED
8
7
First Intervention (8 Weeks)
COMPLETED
8
5
First Intervention (8 Weeks)
NOT COMPLETED
0
2
Washout (2 Weeks)
STARTED
8
5
Washout (2 Weeks)
COMPLETED
8
5
Washout (2 Weeks)
NOT COMPLETED
0
0
Second Period (8 Weeks)
STARTED
8
5
Second Period (8 Weeks)
COMPLETED
8
5
Second Period (8 Weeks)
NOT COMPLETED
0
0

Reasons for withdrawal

Reasons for withdrawal
Measure
Glycine, Then Placebo
First intervention (8 weeks) with Glycine (0.5 g/kg/day divided in three doses). Washout period of 2 weeks. Second intervention (8 weeks) with Placebo (sugar glass, 0.5 g/kg/day divided in three doses).
Placebo, Then Glycine
First intervention (8 weeks) with Placebo (sugar glass, 0.5 g/kg/day divided in three doses). Washout period of 2 weeks. Second intervention (8 weeks) with Glycine (0.5 g/kg/day divided in three doses).
First Intervention (8 Weeks)
Withdrawal by Subject
0
2

Baseline Characteristics

Effect of Glycine in Cystic Fibrosis

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Glycine, Then Placebo
n=8 Participants
First intervention (8 weeks) with Glycine (0.5 g/kg/day divided in three doses). Washout period of 2 weeks. Second intervention (8 weeks) with Placebo (sugar glass, 0.5 g/kg/day divided in three doses).
Placebo, Then Glycine
n=7 Participants
First intervention (8 weeks) with Placebo (sugar glass, 0.5 g/kg/day divided in three doses). Washout period of 2 weeks. Second intervention (8 weeks) with Glycine (0.5 g/kg/day divided in three doses).
Total
n=15 Participants
Total of all reporting groups
Age, Categorical
<=18 years
6 Participants
n=5 Participants
7 Participants
n=7 Participants
13 Participants
n=5 Participants
Age, Categorical
Between 18 and 65 years
2 Participants
n=5 Participants
0 Participants
n=7 Participants
2 Participants
n=5 Participants
Age, Categorical
>=65 years
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Age, Continuous
14.39 years
STANDARD_DEVIATION 5.82 • n=5 Participants
11.00 years
STANDARD_DEVIATION 4.01 • n=7 Participants
12.81 years
STANDARD_DEVIATION 5.19 • n=5 Participants
Sex: Female, Male
Female
6 Participants
n=5 Participants
3 Participants
n=7 Participants
9 Participants
n=5 Participants
Sex: Female, Male
Male
2 Participants
n=5 Participants
4 Participants
n=7 Participants
6 Participants
n=5 Participants
Region of Enrollment
Mexico
8 participants
n=5 Participants
7 participants
n=7 Participants
15 participants
n=5 Participants

PRIMARY outcome

Timeframe: 8 weeks

Population: From the 13 patients who initiated the study, some parents did not give consent for blood sampling, and some children refused the venous puncture at some visits. Thus, only a non-paired population of 9 children per group could be analyzed.

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Then, percentages were log-transformed to adjust to a normal distribution.

Outcome measures

Outcome measures
Measure
Glycine
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
MCP-1
-0.0836 log (percent change)
Standard Error 0.1041
0.0472 log (percent change)
Standard Error 0.0894
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
MIP-1beta
0.0330 log (percent change)
Standard Error 0.1426
-0.0608 log (percent change)
Standard Error 0.0963
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
Myeloperoxidase
-0.4361 log (percent change)
Standard Error 0.2184
-0.2906 log (percent change)
Standard Error 0.2877
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-1
-0.1635 log (percent change)
Standard Error 0.1467
-0.0352 log (percent change)
Standard Error 0.1294
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-4
0.2964 log (percent change)
Standard Error 0.1420
0.1470 log (percent change)
Standard Error 0.2223
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-6
0.0085 log (percent change)
Standard Error 0.2064
0.2255 log (percent change)
Standard Error 0.1865
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-7
0.0356 log (percent change)
Standard Error 0.0613
0.0819 log (percent change)
Standard Error 0.0986
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-8
-0.1466 log (percent change)
Standard Error 0.2981
-0.2364 log (percent change)
Standard Error 0.1761
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-12
0.3203 log (percent change)
Standard Error 0.1449
0.2603 log (percent change)
Standard Error 0.2117
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IL-13
-0.0561 log (percent change)
Standard Error 0.1684
0.1953 log (percent change)
Standard Error 0.1849
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
G-CSF
-0.0776 log (percent change)
Standard Error 0.1554
0.2272 log (percent change)
Standard Error 0.1983
Changes in Serum Concentration of Inflammatory Biomarkers (Other Than TNF-alpha)
IFN-gamma
0.3272 log (percent change)
Standard Error 0.1761
0.3639 log (percent change)
Standard Error 0.2505

PRIMARY outcome

Timeframe: 8 weeks

Population: From the 13 patients who initiated the study, some children at some visits could not give an appropriate sputum sample. Thus, only a non-paired population of 9 (glycine group) and 11 (placebo group) children could be analyzed.

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Then, percentage change was log-transformed to adjust to a normal distribution.

Outcome measures

Outcome measures
Measure
Glycine
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=11 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
Myeloperoxidase
0.1294 log (percent change)
Standard Error 0.2204
0.0669 log (percent change)
Standard Error 0.1725
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-1
-0.0918 log (percent change)
Standard Error 0.1552
-0.0102 log (percent change)
Standard Error 0.1329
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-2
0.0233 log (percent change)
Standard Error 0.0828
-0.0274 log (percent change)
Standard Error 0.1243
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-4
-0.0161 log (percent change)
Standard Error 0.0482
0.0522 log (percent change)
Standard Error 0.0671
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-5
0.2498 log (percent change)
Standard Error 0.1855
0.1304 log (percent change)
Standard Error 0.1864
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-7
0.0611 log (percent change)
Standard Error 0.0852
0.1387 log (percent change)
Standard Error 0.1028
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-8
-0.0824 log (percent change)
Standard Error 0.2311
0.0542 log (percent change)
Standard Error 0.0934
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-10
0.0549 log (percent change)
Standard Error 0.0847
0.0074 log (percent change)
Standard Error 0.0849
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-12
0.1675 log (percent change)
Standard Error 0.1443
0.0677 log (percent change)
Standard Error 0.1250
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-13
0.1630 log (percent change)
Standard Error 0.1379
0.0953 log (percent change)
Standard Error 0.1049
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IL-17
0.0680 log (percent change)
Standard Error 0.0411
0.1140 log (percent change)
Standard Error 0.0823
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
IFN-gamma
0.0248 log (percent change)
Standard Error 0.0652
0.0649 log (percent change)
Standard Error 0.0730
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
MCP-1
0.0042 log (percent change)
Standard Error 0.0694
0.2608 log (percent change)
Standard Error 0.2025
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
MIP-1beta
-0.0303 log (percent change)
Standard Error 0.1234
0.0977 log (percent change)
Standard Error 0.1207
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
TNF-alpha
0.0412 log (percent change)
Standard Error 0.1091
0.1568 log (percent change)
Standard Error 0.1393
Changes in Sputum Concentration of Inflammatory Biomarkers (Other Than IL-6 and G-CSF)
GM-CSF
-0.0538 log (percent change)
Standard Error 0.0338
-0.0822 log (percent change)
Standard Error 0.0468

PRIMARY outcome

Timeframe: 8 weeks

Population: From the 13 patients who initiated the study, some parents did not give consent for blood sampling, and some children refused the venous puncture at some visits. Thus, only a non-paired population of 9 children per group could be analyzed.

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Then, percentages were log-transformed to adjust to a normal distribution.

Outcome measures

Outcome measures
Measure
Glycine
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Serum Concentration of Inflammatory Biomarkers (TNF-alpha)
-0.3908 log (percent change)
Standard Error 0.2744
0.2035 log (percent change)
Standard Error 0.2384

PRIMARY outcome

Timeframe: 8 weeks

Population: From the 13 patients who initiated the study, some children did not expectorate at some visits. Thus, only a non-paired population of 9 children under glycine and 11 under placebo could be analyzed.

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Then, percentage change was log-transformed to adjust to a normal distribution.

Outcome measures

Outcome measures
Measure
Glycine
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=11 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Sputum Concentration of Inflammatory Biomarkers (IL-6)
-0.00007 log (percent change)
Standard Error 0.0677
0.1739 log (percent change)
Standard Error 0.0838

PRIMARY outcome

Timeframe: 8 weeks

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Then, percentage change was log-transformed to adjust to a normal distribution.

Outcome measures

Outcome measures
Measure
Glycine
n=9 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=11 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Sputum Concentration of Inflammatory Biomarkers (G-CSF)
-0.0819 log (percent change)
Standard Error 0.0790
0.1668 log (percent change)
Standard Error 0.1022

SECONDARY outcome

Timeframe: 8 weeks

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). Each respiratory symptom (Cough severity, Sputum features, Appetite, Dyspnea, and Energy perception) was evaluated in a 5-options Likert scale, ranging from 1 (better) to 5 (worse). The total score was computed by the simple sum of the five symptoms.

Outcome measures

Outcome measures
Measure
Glycine
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Cough questionnaire score
81.1 Percentage of baseline
Standard Error 12.6
89.1 Percentage of baseline
Standard Error 4.9
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Appetite questionnaire score
89.1 Percentage of baseline
Standard Error 11.0
132.1 Percentage of baseline
Standard Error 25.4
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Energy questionnaire score
84.6 Percentage of baseline
Standard Error 7.4
111.5 Percentage of baseline
Standard Error 16.2
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Body weight
101.6 Percentage of baseline
Standard Error 1.1
103.6 Percentage of baseline
Standard Error 1.0
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Height
100.5 Percentage of baseline
Standard Error 0.2
100.5 Percentage of baseline
Standard Error 0.2
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Heart rate
103.5 Percentage of baseline
Standard Error 6.0
98.1 Percentage of baseline
Standard Error 3.0
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Respiratory rate
94.8 Percentage of baseline
Standard Error 5.5
109.0 Percentage of baseline
Standard Error 6.4
Changes in Clinical Data Scores (Other Than Sputum Production, Dyspnea and Global Symptoms)
Temperature
100.0 Percentage of baseline
Standard Error 0.3
100.1 Percentage of baseline
Standard Error 0.5

SECONDARY outcome

Timeframe: 8 weeks

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]). In the symptoms questionnaire, each respiratory symptom (Cough severity, Sputum features, Appetite, Dyspnea, and Energy perception) was evaluated in a 5-options Likert scale, ranging from 1 (better) to 5 (worse). The total score was computed by the simple sum of the five symptoms.

Outcome measures

Outcome measures
Measure
Glycine
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Score for Sputum Production, Dyspnea and Global Symptoms
Dyspnea questionnaire score
75.6 Percentage of baseline
Standard Error 7.5
103.8 Percentage of baseline
Standard Error 10.7
Changes in Score for Sputum Production, Dyspnea and Global Symptoms
Sputum questionnaire score
82.0 Percentage of baseline
Standard Error 7.0
102.6 Percentage of baseline
Standard Error 10.1
Changes in Score for Sputum Production, Dyspnea and Global Symptoms
Total questionnaire score
77.7 Percentage of baseline
Standard Error 5.2
98.7 Percentage of baseline
Standard Error 8.4

SECONDARY outcome

Timeframe: 8 weeks

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]).

Outcome measures

Outcome measures
Measure
Glycine
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Pulse Oximetry, FEV1/FVC, and FEF50.
Peripheral oxygen saturation (SpO2)
105.2 Percentage of baseline
Standard Error 2.5
98.9 Percentage of baseline
Standard Error 1.4
Changes in Pulse Oximetry, FEV1/FVC, and FEF50.
FEV1/FVC
105.2 Percentage of baseline
Standard Error 2.9
94.9 Percentage of baseline
Standard Error 4.2
Changes in Pulse Oximetry, FEV1/FVC, and FEF50.
Forced expiratory flow at 50%FVC (FEF50)
115.5 Percentage of baseline
Standard Error 10.4
93.1 Percentage of baseline
Standard Error 7.8

SECONDARY outcome

Timeframe: 8 weeks

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]).

Outcome measures

Outcome measures
Measure
Glycine
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in FEV1, FEF25, and FEFmax
Forced expiratory volume at first second (FEV1)
109.7 Percentage of baseline
Standard Error 6.4
91.4 Percentage of baseline
Standard Error 4.1
Changes in FEV1, FEF25, and FEFmax
Forced expiratory flow at 25%FVC (FEF25)
133.9 Percentage of baseline
Standard Error 13.6
83.3 Percentage of baseline
Standard Error 7.7
Changes in FEV1, FEF25, and FEFmax
Maximal forced expiratory flow (FEFmax, PEFR)
115.3 Percentage of baseline
Standard Error 6.1
91.2 Percentage of baseline
Standard Error 4.6

SECONDARY outcome

Timeframe: 8 weeks

To correct for the baseline variability, all measurements were expressed as percentage of baseline (value at week 8 with respect to baseline value \[beginning of the glycine or placebo period, respectively\]).

Outcome measures

Outcome measures
Measure
Glycine
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg glycine dissolved in water during 8 weeks.
Placebo
n=13 Participants
All study participants receiving a daily oral supplement of 0.5 g/kg placebo (sugar glass) dissolved in water during 8 weeks.
Changes in Other Spirometric Variables
Forced vital capacity (FVC)
104.1 Percentage of baseline
Standard Error 4.1
100.6 Percentage of baseline
Standard Error 9.8
Changes in Other Spirometric Variables
Forced expiratory flow at 75%FVC (FEF75)
111.8 Percentage of baseline
Standard Error 11.7
108.9 Percentage of baseline
Standard Error 15.8

Adverse Events

Glycine

Serious events: 0 serious events
Other events: 0 other events
Deaths: 0 deaths

Placebo

Serious events: 0 serious events
Other events: 0 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Adverse event data not reported

Additional Information

Dr. Mario H. Vargas

Instituto Nacional de Enfermedades Respiratorias

Phone: (+55)54871771

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place