Trial Outcomes & Findings for Bevacizumab for Symptomatic Vestibular Schwannoma in Neurofibromatosis Type 2 (NF2) (NCT NCT01207687)

NCT ID: NCT01207687

Last Updated: 2018-08-27

Results Overview

A hearing response was defined as increased word recognition score above the 95% critical threshold that is maintained across two sequential evaluation time points. The word recognition score (WRS) is the percentage of phonetically-balanced, monosyllabic words that a patient can accurately repeat presented at either most comfortable level or most intelligible level.The proportion of patients with hearing response in the target ear was estimated using a binomial distribution along with 95% confidence intervals.

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

14 participants

Primary outcome timeframe

Baseline to 12 months

Results posted on

2018-08-27

Participant Flow

Participant milestones

Participant milestones
Measure
Treatment (Bevacizumab) - All Participants
Bevacizumab IV over 30-90 minutes once every 3 weeks. Courses repeat every 6 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity.
Overall Study
STARTED
14
Overall Study
COMPLETED
12
Overall Study
NOT COMPLETED
2

Reasons for withdrawal

Reasons for withdrawal
Measure
Treatment (Bevacizumab) - All Participants
Bevacizumab IV over 30-90 minutes once every 3 weeks. Courses repeat every 6 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity.
Overall Study
Adverse Event
1
Overall Study
Withdrawal by Subject
1

Baseline Characteristics

Bevacizumab for Symptomatic Vestibular Schwannoma in Neurofibromatosis Type 2 (NF2)

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Treatment (Bevacizumab)
n=14 Participants
People with NF2, not eligible for surgery with progressive vestibular schwannoma
Age, Categorical
<=18 years
2 Participants
n=5 Participants
Age, Categorical
Between 18 and 65 years
11 Participants
n=5 Participants
Age, Categorical
>=65 years
1 Participants
n=5 Participants
Age, Continuous
30.5 years
n=5 Participants
Sex: Female, Male
Female
10 Participants
n=5 Participants
Sex: Female, Male
Male
4 Participants
n=5 Participants
Race (NIH/OMB)
American Indian or Alaska Native
0 Participants
n=5 Participants
Race (NIH/OMB)
Asian
1 Participants
n=5 Participants
Race (NIH/OMB)
Native Hawaiian or Other Pacific Islander
0 Participants
n=5 Participants
Race (NIH/OMB)
Black or African American
0 Participants
n=5 Participants
Race (NIH/OMB)
White
11 Participants
n=5 Participants
Race (NIH/OMB)
More than one race
0 Participants
n=5 Participants
Race (NIH/OMB)
Unknown or Not Reported
2 Participants
n=5 Participants
Region of Enrollment
United States
14 Participants
n=5 Participants
Karnofsky performance status scale
80 units on a scale
n=5 Participants
word recognition score of target ear
60.5 units on a scale
n=5 Participants

PRIMARY outcome

Timeframe: Baseline to 12 months

Population: All people who underwent treatment were analyzed. Two patients stopped treatment early. One due to toxicity at week 25 and one due to need for medical care not permitted while on treatment at week 49.

A hearing response was defined as increased word recognition score above the 95% critical threshold that is maintained across two sequential evaluation time points. The word recognition score (WRS) is the percentage of phonetically-balanced, monosyllabic words that a patient can accurately repeat presented at either most comfortable level or most intelligible level.The proportion of patients with hearing response in the target ear was estimated using a binomial distribution along with 95% confidence intervals.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
n=2 Participants
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Proportion of Patients With Hearing Response
0.36 Proportion with hearing response
Interval 0.13 to 0.65
0.50 Proportion with hearing response
Interval 0.01 to 0.99

SECONDARY outcome

Timeframe: Up to 6 months post-treatment

Population: Participants evaluated for serious or life threatening toxicities

The number of patients with serious or life threatening toxicities (CTCAE grade 3 or above)

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
n=2 Participants
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Incidence of Serious or Life Threatening Toxicities
2 Participants
0 Participants

SECONDARY outcome

Timeframe: Baseline to 6 months post-treatment

The proportion of participants with radiographic response as measured by a \>/= 20% reduction in tumor volume from baseline on MRI imaging will be estimated using a binomial distribution.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
n=2 Participants
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Radiographic Response
0.43 participants
Interval 0.18 to 0.71
0.50 participants
Interval 0.13 to 0.99

SECONDARY outcome

Timeframe: Baseline to 12 months

The median percent change in the volume of the target vestibular schwannoma using volumetric MRI

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
n=2 Participants
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Median Percent Change in Target Vestibular Schwannoma Volume Using Volumetric MRI
0.5 percentage of change in tumor volume
Interval -29.0 to 41.0
10.8 percentage of change in tumor volume
Interval 3.4 to 18.2

SECONDARY outcome

Timeframe: Baseline to 6 months post-treatment

Population: Distortion product optoacoustic emissions (DPOEs) were only obtained for participants at the NCI site; thus, data from 5 participants were analyzed.

The primary distortion product optoacoustic emissions (DPOAE) measurement will be treated non-parametrically (present or absent across time) DPOAE's will be considered present at the frequency of F2 when the distortion product is 6dB above the noise floor. Variables will be analyzed for differences using t-tests if the effects and sample sizes warrant, but this may not be advisable given the small numbers to be accrued.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=5 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Number of Participants With Changes in Function of the Auditory System
Present
3 Participants
Number of Participants With Changes in Function of the Auditory System
Absent
2 Participants

SECONDARY outcome

Timeframe: Baseline to week 72

Correlation assessment were planned for imaging parameters and hearing response based on the estimated changes in Ktrans: a MRI measure of vascular permeability. Only 1/14 participants had complete Ktrans data that was amenable to analysis at baseline and week 72. Hence, these statistical analyses were not possible.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=1 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Percent Change in Median Vascular Permeability (Ktrans)
-20 percent change in median Ktrans

SECONDARY outcome

Timeframe: Baseline

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. The total score is the median of the all the individual items.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Total Score
77.85 units on a scale
Interval 27.36 to 98.19

SECONDARY outcome

Timeframe: Baseline

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. Scores are commonly reported as a physical component summary (PCS) and mental component summary (MCS). The PCS and MCS score have been transformed to the T-score metric, which has a mean of 50 and a standard deviation of 10 for the U.S. general population.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Physical Component Summary (PCS)
50.67 T-score
Interval 22.8 to 61.05
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Mental Component Summary
50.79 T-score
Interval 33.01 to 56.58

SECONDARY outcome

Timeframe: 6 months

Population: One participant was off study at this point secondary to an adverse event and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 1 - 100, with a higher value indicating a more favorable health state. The total score is the median of the all the individual items.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Total Score
80.56 units on a scale
Interval 26.25 to 95.97

SECONDARY outcome

Timeframe: 6 months

Population: One participant was off study at this point secondary to an adverse event and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. Scores are commonly reported as a physical component summary (PCS) and mental component summary (MCS). The PCS and MCS score have been transformed to the T-score metric, which has a mean of 50 and a standard deviation of 10 for the U.S. general population.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Physical Component Score (PCS)
52.23 T-score
Interval 22.73 to 60.45
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Mental component Summary (MCS)
54.30 T-score
Interval 36.22 to 59.22

SECONDARY outcome

Timeframe: 12 months

Population: One participant was off study at this point secondary to an adverse event and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. The total score is the median of the all the individual items.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Total Score
75.97 units on a scale
Interval 35.42 to 95.42

SECONDARY outcome

Timeframe: 12 months

Population: One participant was off study at this point secondary to an adverse event and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. Scores are commonly reported as a physical component summary (PCS) and mental component summary (MCS). The PCS and MCS score have been transformed to the T-score metric, which has a mean of 50 and a standard deviation of 10 for the U.S. general population.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Physical Component Summary (PCS)
47.88 T-score
Interval 19.98 to 62.34
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Mental Component Summary (MCS)
56.62 T-score
Interval 21.1 to 60.94

SECONDARY outcome

Timeframe: 18 months

Population: One participant had withdrawn consent from the study and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. The total score is the median of the all the individual items.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Total Score
75.28 units on a scale
Interval 51.67 to 92.64

SECONDARY outcome

Timeframe: 18 months

Population: One participant had withdrawn consent from the study and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SF-36 is a patient reported outcome. SF-36 (v.1) was administered and was scored according to instructions found on the RAND website. The range of scores is 0 - 100, with a higher value indicating a more favorable health state. Scores are commonly reported as a physical component summary (PCS) and mental component summary (MCS). The PCS and MCS score have been transformed to the T-score metric, which has a mean of 50 and a standard deviation of 10 for the U.S. general population.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Physical Component Summary (PCS)
51.73 T-score
Interval 21.07 to 60.02
Quality of Life Assessed Using Health Survey Short Form-36 (SF-36) - Component Scores
Mental Component Summary (MCS)
51.51 T-score
Interval 26.94 to 67.78

SECONDARY outcome

Timeframe: baseline

The SSQ is a 49 item patient-reported outcome with three subscales: speech understanding (14 questions), spatial location of sounds (17 questions), and the qualities of sounds (18 questions) as they appear to the patient with hearing impairment. Each response is recorded on an 11 point scale (0 - 10), with the anchor points "not at all" (= 0) and "perfectly" (=10). A higher score indicates better hearing. The median score is reported for each subscale. The minimum and maximum scores for the median of each subscale would be 0 and 10, respectively.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Speech Understanding
3.2 units on a scale
Interval 0.9 to 6.9
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Spatial Location of Sounds
3.2 units on a scale
Interval 0.3 to 8.6
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Qualities of Sounds
4.7 units on a scale
Interval 3.1 to 8.9

SECONDARY outcome

Timeframe: 6 months

Population: At this time point, one participant was off study due to adverse events and did not complete the questionnaire. Three participants did not complete the questionnaire at this time point. Hence, data from 10 participants were available for analysis.

The SSQ is a 49 item patient-reported outcome with three subscales: speech understanding (14 questions), spatial location of sounds (17 questions), and the qualities of sounds (18 questions) as they appear to the patient with hearing impairment. Responses are recorded on a scale from 0 - 10, with the anchor points "not at all" (= 0) and "perfectly" (=10). A higher score indicates better hearing. The median score for each subscale is reported. The minimum and maximum scores for the median of each subscale would be 0 and 10, respectively.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=10 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Speech Understanding
4.2 units on a scale
Interval 1.3 to 6.8
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Spatial Location of Sounds
4.0 units on a scale
Interval 0.9 to 7.2
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Qualities of Sounds
6.8 units on a scale
Interval 3.1 to 8.2

SECONDARY outcome

Timeframe: 12 months

Population: At this time point, one participant was off study due to an adverse event and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SSQ is a 49 item patient-reported outcome with three subscales: speech understanding (14 questions), spatial location of sounds (17 questions), and the qualities of sounds (18 questions) as they appear to the patient with hearing impairment. Responses are recorded on a scale from 0 - 10, with the anchor points "not at all" (= 0) and "perfectly" (=10). A higher score indicates better hearing. The median score for each subscale is reported. The minimum and maximum scores for the median of each subscale would be 0 and 10, respectively.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Speech Understanding
5.4 units on a scale
Interval 2.9 to 8.1
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Spatial Location of Sounds
4.8 units on a scale
Interval 1.6 to 9.4
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Qualities of Sounds
6.9 units on a scale
Interval 3.1 to 9.7

SECONDARY outcome

Timeframe: 18 months

Population: One participant had withdrawn consent from the study and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The SSQ is a 49 item patient-reported outcome with three subscales: speech understanding (14 questions), spatial location of sounds (17 questions), and the qualities of sounds (18 questions) as they appear to the patient with hearing impairment. Responses are recorded on a scale from 0 - 10, with the anchor points "not at all" (= 0) and "perfectly" (=10). A higher score indicates better hearing. The median score for each subscale is reported. The minimum and maximum scores for the median of each subscale would be 0 and 10, respectively.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Speech Understanding
4.1 units on a scale
Interval 2.1 to 7.4
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Spatial Location of Sounds
3.6 units on a scale
Interval 0.2 to 9.4
Quality of Life as Assessed by the Speech and Spatial Qualities Questionnaire (SSQ)
Qualities of Sounds
6.3 units on a scale
Interval 3.2 to 9.6

SECONDARY outcome

Timeframe: baseline

The TRQ is a 26 item patient reported outcome. It is scored using a 5 point Likert scale (0-4). The responses are summed, resulting in a range of 0 - 104 with higher scores indicating more distress related to tinnitus.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=14 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed by the Tinnitus Reaction Questionnaire (TRQ)
18 units on a scale
Interval 0.0 to 81.0

SECONDARY outcome

Timeframe: 6 months

Population: At this time point, one participant was off study due to an adverse event and did not complete the questionnaire. One participant did not complete this questionnaire at this time point. Hence, data from 12 of the 14 participants were available for analysis at this time point.

The TRQ is a 26 item patient reported outcome. It is scored using a 5 point Likert scale (0-4). The responses are summed, resulting in a range of 0 - 104 with higher scores indicating more distress related to tinnitus.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=12 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed by the Tinnitus Reaction Questionnaire (TRQ)
18 units on a scale
Interval 0.0 to 43.0

SECONDARY outcome

Timeframe: 12 months

Population: At this time point, one participant was off study due to an adverse event and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The TRQ is a 26 item patient reported outcome. It is scored using a 5 point Likert scale (0-4). The responses are summed, resulting in a range of 0 - 104 with higher scores indicating more distress related to tinnitus.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed by the Tinnitus Reaction Questionnaire (TRQ)
10 units on a scale
Interval 0.0 to 56.0

SECONDARY outcome

Timeframe: 18 months

Population: At this time point, one participant had withdrawn consent from the study and did not complete the questionnaire. Hence, data from 13 of the 14 participants were available for analysis at this time point.

The TRQ is a 26 item patient reported outcome. It is scored using a 5 point Likert scale (0-4). The responses are summed, resulting in a range of 0 - 104 with higher scores indicating more distress related to tinnitus.

Outcome measures

Outcome measures
Measure
Treatment (Bevacizumab) - All Participants
n=13 Participants
Patients who met all eligibility criteria underwent baseline evaluation and then received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 48 weeks in the absence of disease progression or unacceptable toxicity. Hearing evaluation for word recognition score was evaluated every 12 weeks. Hearing response was defined as improvement beyond the 95% CI maintained across 2 timepoints.
Treatment (Bevacizumab) - Pediatric Participants Only
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Quality of Life Assessed by the Tinnitus Reaction Questionnaire (TRQ)
23 units on a scale
Interval 0.0 to 40.0

Adverse Events

Treatment (Bevacizumab) - All Participants

Serious events: 2 serious events
Other events: 13 other events
Deaths: 0 deaths

Treatment (Bevacizumab) - Pediatric Participants

Serious events: 0 serious events
Other events: 1 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Treatment (Bevacizumab) - All Participants
n=14 participants at risk
All enrolled participants received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 12 months.
Treatment (Bevacizumab) - Pediatric Participants
n=2 participants at risk
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Vascular disorders
Hypertension
7.1%
1/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Blood and lymphatic system disorders
Idiopathic thrombocytopenia purpura
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov

Other adverse events

Other adverse events
Measure
Treatment (Bevacizumab) - All Participants
n=14 participants at risk
All enrolled participants received bevacizumab 7.5mg/kg IV once every 3 weeks for up to 12 months.
Treatment (Bevacizumab) - Pediatric Participants
n=2 participants at risk
All enrolled patients \< 18 years of age received bevacizumab 7.5mg/kg IV once every 3 weeks for 12 months.
Gastrointestinal disorders
Abdominal pain
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
ALT increased
35.7%
5/14 • Number of events 8 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Allergic rhinitis
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Blood and lymphatic system disorders
Anemia
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Metabolism and nutrition disorders
Anorexia
7.1%
1/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
AST increase
28.6%
4/14 • Number of events 8 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Injury, poisoning and procedural complications
Bruising
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
CPK increase
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Diarrhea
21.4%
3/14 • Number of events 3 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Nervous system disorders
Dizziness
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Skin and subcutaneous tissue disorders
Dry skin
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Dyspepsia
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Dyspnea
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
Electrocardiogram with prolonged QTc
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Epistaxis
50.0%
7/14 • Number of events 10 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
General disorders
Fatigue
64.3%
9/14 • Number of events 13 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Nervous system disorders
Headache
7.1%
1/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Renal and urinary disorders
Hemoglobinuria
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Blood and lymphatic system disorders
Hemolysis
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Hemorrhoidal hemorrhage
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Hoarseness
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Metabolism and nutrition disorders
Hyperglycemia
14.3%
2/14 • Number of events 4 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Metabolism and nutrition disorders
Hypermagnesemia
14.3%
2/14 • Number of events 3 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Vascular disorders
Hypomagnesemia
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
Increased blood bicarbonate
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Reproductive system and breast disorders
Irregular menstruation
28.6%
2/7 • Number of events 6 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 4 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Reproductive system and breast disorders
Menorrhagia
14.3%
1/7 • Number of events 3 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Mucositis oral
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Nausea
28.6%
4/14 • Number of events 7 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Oral hemorrhage
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Oral pain
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Cardiac disorders
Palpitations
14.3%
2/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Nervous system disorders
Peripheral sensory neuropathy
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
Platelet count decreased
7.1%
1/14 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Renal and urinary disorders
Proteinuria
14.3%
2/14 • Number of events 10 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 6 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Rectal hemorrhage
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Nasal septum perforation
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Sore throat
14.3%
2/14 • Number of events 4 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Ear and labyrinth disorders
Vertigo
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
50.0%
1/2 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Respiratory, thoracic and mediastinal disorders
Voice alteration
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Vomiting
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Investigations
Weight gain
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Gastrointestinal disorders
Weight loss
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
Injury, poisoning and procedural complications
Wound complication
7.1%
1/14 • Number of events 1 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov
0.00%
0/2 • From first dose until 6 months off of drug or until resolution of all SAE to baseline, assessed up to 12 months
definition is that used in clinicaltrials.gov

Additional Information

Dr. Jaishri Blakeley

Johns Hopkins Comprehensive Neurofibromatosis Center

Phone: 410-614-3853

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place

Restriction type: LTE60