Trial Outcomes & Findings for Phase III Study of Idebenone in Duchenne Muscular Dystrophy (DMD) (NCT NCT01027884)

NCT ID: NCT01027884

Last Updated: 2015-10-19

Results Overview

Change from Baseline in Percent Predicted Peak Expiratory Flow (PEF) at Week 52

Recruitment status

COMPLETED

Study phase

PHASE3

Target enrollment

65 participants

Primary outcome timeframe

Baseline and Week 52

Results posted on

2015-10-19

Participant Flow

Recruiting centres were in Belgium, Germany, the Netherlands, Switzerland, France, Sweden, Austria, Italy, Spain, and the USA. Patients were enrolled between July 27, 2009 (study start date), and Dec 14, 2012; the study end date (last patient completed the study) was Jan 14, 2014.

65 patients were randomly assigned and two patients were allocated to the same treatment as their randomly assigned siblings. One patient never took study medication, resulting in 66 patients who were treated and included in the safety population (34 in the placebo group and 32 in the idebenone group).

Participant milestones

Participant milestones
Measure
Placebo
Two matching placebo tablets were taken three times a day with meals
Idebenone
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Overall Study
STARTED
34
32
Overall Study
COMPLETED
30
25
Overall Study
NOT COMPLETED
4
7

Reasons for withdrawal

Reasons for withdrawal
Measure
Placebo
Two matching placebo tablets were taken three times a day with meals
Idebenone
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Overall Study
Adverse Event
2
1
Overall Study
Protocol Violation
1
0
Overall Study
Non-compliance
1
1
Overall Study
Withdrawal by Subject
0
1
Overall Study
Lost to Follow-up
0
1
Overall Study
Spinal fixation surgery
0
3

Baseline Characteristics

Phase III Study of Idebenone in Duchenne Muscular Dystrophy (DMD)

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Placebo
n=34 Participants
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=32 Participants
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Total
n=66 Participants
Total of all reporting groups
Age, Continuous
15 years
STANDARD_DEVIATION 2.5 • n=5 Participants
13.5 years
STANDARD_DEVIATION 2.7 • n=7 Participants
14.3 years
STANDARD_DEVIATION 2.7 • n=5 Participants
Sex: Female, Male
Female
0 Participants
n=5 Participants
0 Participants
n=7 Participants
0 Participants
n=5 Participants
Sex: Female, Male
Male
34 Participants
n=5 Participants
32 Participants
n=7 Participants
66 Participants
n=5 Participants

PRIMARY outcome

Timeframe: Baseline and Week 52

Population: This analysis was performed on the ITT population(n=64). This population included all randomized patients who received at least one dose of the study medication and provided at least one post-Baseline assessment. It excluded siblings who had been allocated to the same study treatment as a randomized sibling.

Change from Baseline in Percent Predicted Peak Expiratory Flow (PEF) at Week 52

Outcome measures

Outcome measures
Measure
Placebo
n=33 Participants
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=31 Participants
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Change From Baseline in Percent Predicted Peak Expiratory Flow (PEF) at Week 52
-8.84 percentage
Interval -12.73 to -4.95
-2.57 percentage
Interval -6.68 to 1.54

SECONDARY outcome

Timeframe: Baseline and Week 52

Population: This analysis was performed on the ITT population(n=64). This population included all randomized patients who received at least one dose of the study medication and provided at least one post-Baseline assessment. It excluded siblings who had been allocated to the same study treatment as a randomized sibling.

Change From Baseline in Percent Predicted Forced Vital Capacity (FVC) at Week 52

Outcome measures

Outcome measures
Measure
Placebo
n=33 Participants
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=31 Participants
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Change From Baseline in Percent Predicted Forced Vital Capacity (FVC) at Week 52
-8.95 percentage of Predicted FVC
Interval -11.47 to -6.42
-5.67 percentage of Predicted FVC
Interval -8.36 to -2.99

SECONDARY outcome

Timeframe: Baseline and Week 52

Population: The number of patients (N) in each treatment group is the number of patients with baseline assessments

The change from Baseline to Week 52 in muscle strength as measured by Hand-Held Myometry (HHM) was performed following standardized procedures. As almost all patients were non-ambulatory, only analyses of upper limb muscle strength were performed. Results for elbow flexors and for elbow extensors are reported below.The highest value of 3 consecutive measurements with an interval of at least 10 seconds were recorded. The HHM was measured using MicroFET2, a digital hand held muscle tester. The selected unit of measure was Newtons (N).

Outcome measures

Outcome measures
Measure
Placebo
n=27 Participants
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=25 Participants
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Change From Baseline to Week 52 in Muscle Strength
Elbow Extensors
1.32 Newtons
Interval -2.53 to 5.18
0.26 Newtons
Interval -3.95 to 4.46
Change From Baseline to Week 52 in Muscle Strength
Elbow Flexors
0.13 Newtons
Interval -4.16 to 4.41
-2.32 Newtons
Interval -6.73 to 2.09

SECONDARY outcome

Timeframe: Baseline and Week 52

Population: The number of patients (N) in each treatment group is the number of patients with Baseline assessments.

PedsQL Quality of Life Inventory contains paediatric HRQOL measurements: Physical, Emotional,Social and School Functioning. Item Scaling: 5-point Likert scale from 0 (Never) to 4 (Almost always). 3-point scale: 0 (Not at all), 2 (Sometimes) and 4 (A lot) for the Young Child (ages 5-7). Scores are transformed on a scale from 0 to 100 ( 0=100, 1=75, 2=50, 3=25, 4=0) Total Score: Sum of all the items over the number of items answered on all the Scales. The values reported below are overall scores on Paediatric Quality of Life Inventory in Child/Teen Report. These scores were obtained by averaging scores for all the described subscales. The overall scores range between 0-100 with 0 = worst outcome and 100= best outcome

Outcome measures

Outcome measures
Measure
Placebo
n=33 Participants
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=30 Participants
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Change From Baseline to Week 52 in Quality of Life Assessed by PedsQL™ Paediatric Quality of Life Inventory
2.46 units on a scale
Interval -1.77 to 6.69
-1.34 units on a scale
Interval -5.99 to 3.31

SECONDARY outcome

Timeframe: 52 Weeks

Outcome measures

Outcome measures
Measure
Placebo
n=34 Participants
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=32 Participants
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Percentage of Patients Reporting Adverse Events
94.1 percentage of patients reporting AEs
93.8 percentage of patients reporting AEs

Adverse Events

Placebo

Serious events: 5 serious events
Other events: 32 other events
Deaths: 0 deaths

Idebenone

Serious events: 2 serious events
Other events: 30 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Placebo
n=34 participants at risk
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=32 participants at risk
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Injury, poisoning and procedural complications
Femur fracture
2.9%
1/34 • Number of events 1
0.00%
0/32
Respiratory, thoracic and mediastinal disorders
Acute respiratory failure
2.9%
1/34 • Number of events 1
0.00%
0/32
Respiratory, thoracic and mediastinal disorders
Pulmunary microemboli
2.9%
1/34 • Number of events 1
0.00%
0/32
Respiratory, thoracic and mediastinal disorders
Respiratory failure
0.00%
0/34
3.1%
1/32 • Number of events 1
General disorders
Pyrexia
2.9%
1/34 • Number of events 1
0.00%
0/32
Psychiatric disorders
Sleep apnoea syndrome
0.00%
0/34
3.1%
1/32
Gastrointestinal disorders
Vomitig
2.9%
1/34
0.00%
0/32
Skin and subcutaneous tissue disorders
Urticaria
0.00%
0/34
3.1%
1/32 • Number of events 1
Musculoskeletal and connective tissue disorders
Tendinous contracture
2.9%
1/34 • Number of events 2
0.00%
0/32
Metabolism and nutrition disorders
Dehydration
2.9%
1/34 • Number of events 1
0.00%
0/32
Infections and infestations
Pneumonia
5.9%
2/34 • Number of events 3
0.00%
0/32
Infections and infestations
Nasopharyngitis
2.9%
1/34 • Number of events 1
0.00%
0/32

Other adverse events

Other adverse events
Measure
Placebo
n=34 participants at risk
Two matching placebo tablets were taken three times a day with meals
Idebenone
n=32 participants at risk
Two150 mg tablets were taken three times a day with meals (total dose 900 mg daily).
Cardiac disorders
Left ventricular failure
2.9%
1/34 • Number of events 1
9.4%
3/32 • Number of events 3
Cardiac disorders
Electrocardiogram abnormal
2.9%
1/34 • Number of events 1
6.2%
2/32 • Number of events 3
Blood and lymphatic system disorders
Blood phosporus increased
8.8%
3/34 • Number of events 4
3.1%
1/32 • Number of events 1
Respiratory, thoracic and mediastinal disorders
Bronchitis
17.6%
6/34 • Number of events 7
12.5%
4/32 • Number of events 5
Respiratory, thoracic and mediastinal disorders
Rhinorrhoea
5.9%
2/34 • Number of events 2
9.4%
3/32 • Number of events 3
Respiratory, thoracic and mediastinal disorders
Nasal congestion
2.9%
1/34 • Number of events 1
6.2%
2/32 • Number of events 2
Respiratory, thoracic and mediastinal disorders
Oropharyngeal pain
2.9%
1/34 • Number of events 1
6.2%
2/32 • Number of events 2
Nervous system disorders
Headache
20.6%
7/34 • Number of events 15
18.8%
6/32 • Number of events 13
General disorders
Pyrexia
8.8%
3/34 • Number of events 4
15.6%
5/32 • Number of events 6
General disorders
Influenza like illness
2.9%
1/34 • Number of events 2
6.2%
2/32 • Number of events 2
Gastrointestinal disorders
Diarrhoea
11.8%
4/34 • Number of events 6
25.0%
8/32 • Number of events 10
Gastrointestinal disorders
Constipation
17.6%
6/34 • Number of events 6
9.4%
3/32 • Number of events 4
Gastrointestinal disorders
Abdominal pain
8.8%
3/34 • Number of events 5
9.4%
3/32 • Number of events 4
Gastrointestinal disorders
Nausea
5.9%
2/34 • Number of events 2
3.1%
1/32 • Number of events 2
Gastrointestinal disorders
Vomiting
5.9%
2/34 • Number of events 3
3.1%
1/32 • Number of events 1
Renal and urinary disorders
Chromaturia
0.00%
0/34
9.4%
3/32 • Number of events 3
Skin and subcutaneous tissue disorders
Seborrhoeic dermatitis
5.9%
2/34 • Number of events 2
3.1%
1/32 • Number of events 1
Musculoskeletal and connective tissue disorders
Back pain
11.8%
4/34 • Number of events 6
6.2%
2/32 • Number of events 2
Musculoskeletal and connective tissue disorders
Scoliosis
2.9%
1/34 • Number of events 1
6.2%
2/32 • Number of events 2
Infections and infestations
Nasopharyngitis
26.5%
9/34 • Number of events 11
25.0%
8/32 • Number of events 12
Infections and infestations
Upper respiratory tract infection
17.6%
6/34 • Number of events 10
6.2%
2/32 • Number of events 2
Infections and infestations
Gastroenteritis
2.9%
1/34 • Number of events 1
18.8%
6/32 • Number of events 7
Infections and infestations
Rhinitis
17.6%
6/34 • Number of events 8
3.1%
1/32 • Number of events 1
Infections and infestations
Otitis media
0.00%
0/34
9.4%
3/32 • Number of events 3

Additional Information

Dr Gunnar Buyse

University Hospital Leuven-Children Hospital

Phone: +32 016343845

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place