Trial Outcomes & Findings for A Long-Term Extension Study of AT2101 (Afegostat Tartrate) in Type 1 Gaucher Patients (NCT NCT00813865)

NCT ID: NCT00813865

Last Updated: 2018-08-15

Results Overview

A TEAE was defined as any adverse event (AE) with start date on or after administration of study drug or pre-existing conditions that worsened on or after the start of the first study drug administration (on Day 1). A severe AE defined as an AE that was incapacitating and required medical intervention. The number of participants who experienced 1 or more severe TEAEs after dosing on Day 1 through the end of follow-up is presented. A summary of serious and all other non-serious AEs regardless of causality is located in the Reported Adverse Events module.

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

8 participants

Primary outcome timeframe

Day 1 (after dosing) through end of follow-up (6 months after EOT)

Results posted on

2018-08-15

Participant Flow

Participants were screened for evaluation of eligibility to participate in the study. Eight participants received at least 1 dose of study drug.

Participant milestones

Participant milestones
Measure
Afegostat Tartrate
Afegostat tartrate was administered orally at a dose of 225 milligram (mg) once daily (QD) on Monday, Wednesday, and Friday, with no study medication on Tuesday, Thursday, Saturday, and Sunday (MWF 3-days-on/4-days-off). Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after the end of treatment (EOT).
Overall Study
STARTED
8
Overall Study
Safety Population
8
Overall Study
Pharmacodynamic (PD) Population
8
Overall Study
COMPLETED
1
Overall Study
NOT COMPLETED
7

Reasons for withdrawal

Reasons for withdrawal
Measure
Afegostat Tartrate
Afegostat tartrate was administered orally at a dose of 225 milligram (mg) once daily (QD) on Monday, Wednesday, and Friday, with no study medication on Tuesday, Thursday, Saturday, and Sunday (MWF 3-days-on/4-days-off). Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after the end of treatment (EOT).
Overall Study
Failure to Respond
3
Overall Study
Lost to Follow-up
3
Overall Study
Withdrawal by Subject
1

Baseline Characteristics

A Long-Term Extension Study of AT2101 (Afegostat Tartrate) in Type 1 Gaucher Patients

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
Afegostat Tartrate
n=8 Participants
Afegostat tartrate was administered orally at a dose of 225 mg QD MWF 3-days-on/4-days-off. Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after EOT.
Age, Continuous
41.3 years
STANDARD_DEVIATION 20.74 • n=5 Participants
Sex: Female, Male
Female
1 Participants
n=5 Participants
Sex: Female, Male
Male
7 Participants
n=5 Participants

PRIMARY outcome

Timeframe: Day 1 (after dosing) through end of follow-up (6 months after EOT)

Population: Safety Population: all participants who received at least 1 dose of study drug.

A TEAE was defined as any adverse event (AE) with start date on or after administration of study drug or pre-existing conditions that worsened on or after the start of the first study drug administration (on Day 1). A severe AE defined as an AE that was incapacitating and required medical intervention. The number of participants who experienced 1 or more severe TEAEs after dosing on Day 1 through the end of follow-up is presented. A summary of serious and all other non-serious AEs regardless of causality is located in the Reported Adverse Events module.

Outcome measures

Outcome measures
Measure
Afegostat Tartrate
n=8 Participants
Afegostat tartrate was administered orally at a dose of 225 mg QD MWF 3-days-on/4-days-off. Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after EOT.
Number Of Participants Who Experienced Severe Treatment-emergent Adverse Events (TEAEs)
0 Participants

SECONDARY outcome

Timeframe: Baseline, Month 30

Population: PD Population: all participants in the Safety Population who had a baseline and at least 1 post-baseline PD measurement. Seven of 8 participants did not complete the study and did not contribute data to this endpoint.

Standard MRI procedures were used to measure the volume of the spleen. The baseline value was defined as the value recorded on Days 1 to 3 of the study (certain values could have been carried over from the last assessment in the lead-in study, GAU-CL-202). A negative change from Baseline indicates that spleen volume decreased.

Outcome measures

Outcome measures
Measure
Afegostat Tartrate
n=1 Participants
Afegostat tartrate was administered orally at a dose of 225 mg QD MWF 3-days-on/4-days-off. Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after EOT.
Change From Baseline To EOT In Volume Of Spleen As Assessed By Magnetic Resonance Imaging (MRI)
-138 cubic centimeters (cm^3)

SECONDARY outcome

Timeframe: Baseline, Month 30

Population: PD Population: all participants in the Safety Population who had a baseline and at least 1 post-baseline PD measurement. Seven of 8 participants did not complete the study and did not contribute data to this endpoint.

Standard MRI procedures were used to measure the volume of the liver. The baseline value was defined as the value recorded on Days 1 to 3 of the study (certain values could have been carried over from the last assessment in the lead-in study, GAU-CL-202). A negative change from Baseline indicates that liver volume decreased.

Outcome measures

Outcome measures
Measure
Afegostat Tartrate
n=1 Participants
Afegostat tartrate was administered orally at a dose of 225 mg QD MWF 3-days-on/4-days-off. Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after EOT.
Change From Baseline To EOT In Volume Of Liver As Assessed By MRI
57 cm^3

Adverse Events

Afegostat Tartrate

Serious events: 0 serious events
Other events: 6 other events
Deaths: 0 deaths

Serious adverse events

Adverse event data not reported

Other adverse events

Other adverse events
Measure
Afegostat Tartrate
n=8 participants at risk
Afegostat tartrate was administered orally at a dose of 225 mg QD MWF 3-days-on/4-days-off. Participants were to receive afegostat tartrate for 30 months and be followed for 6 months after EOT.
Blood and lymphatic system disorders
Splenomegaly
25.0%
2/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Blood and lymphatic system disorders
Splenic infarction
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Eye disorders
Blepharitis
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Eye disorders
Conjunctivitis
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Eye disorders
Lacrimation increased
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Eye disorders
Macular scar
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Eye disorders
Vision blurred
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Gastrointestinal disorders
Abdominal pain
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
General disorders
Chest pain
25.0%
2/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
General disorders
Gait disturbance
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Hepatobiliary disorders
Hepatomegaly
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Injury, poisoning and procedural complications
Ligament sprain
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Injury, poisoning and procedural complications
Muscle strain
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Musculoskeletal and connective tissue disorders
Arthralgia
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Musculoskeletal and connective tissue disorders
Intervertebral disc protrusion
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Musculoskeletal and connective tissue disorders
Pain in extremity
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Skin and subcutaneous tissue disorders
Pruritus
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Skin and subcutaneous tissue disorders
Skin exfoliation
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)
Skin and subcutaneous tissue disorders
Skin hyperpigmentation
12.5%
1/8 • Day 1 (after dosing) through end of follow-up (6 months after EOT)

Additional Information

Amicus Therapeutics

Patient Advocacy

Phone: +1-609-662-2000

Results disclosure agreements

  • Principal investigator is a sponsor employee The investigator can publish only the results from this trial, provided they supply the sponsor (or authorized entity) a copy of any proposed publication for review prior to submission for publication. If requested and prior to publication, the investigator will remove information deemed confidential or proprietary by the sponsor and will withhold publication for an additional period of time to allow the sponsor to take appropriate measures to establish and preserve its proprietary rights.
  • Publication restrictions are in place

Restriction type: OTHER