Stem Cell Transplantation With Identical Donors for Patients With Sickle Cell Disease

NCT ID: NCT00186810

Last Updated: 2009-05-29

Study Results

Results pending

The study team has not published outcome measurements, participant flow, or safety data for this trial yet. Check back later for updates.

Basic Information

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Recruitment Status

COMPLETED

Clinical Phase

PHASE2

Total Enrollment

15 participants

Study Classification

INTERVENTIONAL

Study Start Date

1992-12-31

Study Completion Date

2007-10-31

Brief Summary

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This protocol studied the effect of administration of a myeloablative pretransplant preparative regimen followed by an infusion of donor stem cells in children with severe sickle cell disease. The donor graft consisted of bone marrow or cord blood derived from a genetically matched sibling.

The primary aim of the study was to evaluate how well the donated cells migrated to the bone marrow and begin producing healthy red blood cells, white blood cells and platelets (engrafted), how well the recipients immune system recovered, and assess any regimen related toxicities including a potentially life-threatening transplant related complication called graft-versus-host-disease or GVHD.

Detailed Description

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The secondary objectives of this protocol evaluated the effect of this transplant procedure on the subsequent clinical course of patients with severe SCD. Specifically, to determine whether pre-transplant organ dysfunction (brain, heart, lung, kidney, liver, spleen, etc) resultant from sickle hemoglobinopathy can be reversed following this particular transplant procedure.

Conditions

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Sickle Cell Disease

Keywords

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Anemia Sickle Cell

Study Design

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Allocation Method

NON_RANDOMIZED

Intervention Model

SINGLE_GROUP

Primary Study Purpose

TREATMENT

Blinding Strategy

NONE

Study Groups

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1

Group Type OTHER

Busulfan, Cyclophosphamide, Horse ATG

Intervention Type DRUG

Transplant recipients received a myeloablative conditioning regimen of cyclophosphamide, Anti-Thymocyte Globulin (horse), and Busulfan. Cyclosporine and methotrexate were administered for GVHD prophylaxis.

Allogeneic stem cell transplant

Intervention Type PROCEDURE

Allogeneic stem cell transplant Matched sibling donor transplant Cord blood transplant

Interventions

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Busulfan, Cyclophosphamide, Horse ATG

Transplant recipients received a myeloablative conditioning regimen of cyclophosphamide, Anti-Thymocyte Globulin (horse), and Busulfan. Cyclosporine and methotrexate were administered for GVHD prophylaxis.

Intervention Type DRUG

Allogeneic stem cell transplant

Allogeneic stem cell transplant Matched sibling donor transplant Cord blood transplant

Intervention Type PROCEDURE

Eligibility Criteria

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Inclusion Criteria

Diagnosis of severe' disease is denoted by one of the following:

* Previous central nervous system vaso-occlusive episode with or without residual neurologic findings or
* Frequent painful vaso-occlusive episodes with significant interference with normal life activities and which necessitates chronic transfusion therapy or
* Recurrent SCD chest syndrome events which necessitate chronic transfusion therapy.

Exclusion Criteria

* Patient with SCD chronic lung disease greater than or equal to stage 3
* Patient with severe renal dysfunction defined as creatinine clearance \< 40 ml/min/1.73m2.
* Patient with severe cardiac dysfunction defined as echocardiogram shortening fraction \< 25%.
* Patient with HIV infection.
* Pregnant or lactating.
* Patient with unspecified chronic toxicity that in the opinion of the Principal Investigator is serious enough to detrimentally affect the patient's capacity to tolerate SCT.
* Patient or patient's guardian(s) unable to understand the nature and risks inherent in the BMT process
Maximum Eligible Age

21 Years

Eligible Sex

ALL

Accepts Healthy Volunteers

No

Sponsors

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St. Jude Children's Research Hospital

OTHER

Sponsor Role lead

Responsible Party

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St. Jude Children's Research Hospital

Principal Investigators

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Gregory Hale, MD

Role: PRINCIPAL_INVESTIGATOR

St. Jude Children's Research Hospital

Locations

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St. Jude Children's Research Hospital

Memphis, Tennessee, United States

Site Status

Countries

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United States

References

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Dallas MH, Triplett B, Shook DR, Hartford C, Srinivasan A, Laver J, Ware R, Leung W. Long-term outcome and evaluation of organ function in pediatric patients undergoing haploidentical and matched related hematopoietic cell transplantation for sickle cell disease. Biol Blood Marrow Transplant. 2013 May;19(5):820-30. doi: 10.1016/j.bbmt.2013.02.010. Epub 2013 Feb 14.

Reference Type DERIVED
PMID: 23416852 (View on PubMed)

Related Links

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http://www.stjude.org

St. Jude Children's Research Hospital

Other Identifiers

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SCALLO

Identifier Type: -

Identifier Source: org_study_id