Trial Outcomes & Findings for 17AAG to Treat Kidney Tumors in Von Hippel-Lindau Disease (NCT NCT00088374)

NCT ID: NCT00088374

Last Updated: 2012-07-27

Results Overview

Response is defined as the number of patients who experience a disease response (complete response (CR) or partial response (PR) of renal tumors)per RECIST criteria. CR is the disappearance of all target lesions. PR is at least a 20% decrease in the sum of the longest diameter (LD) of target lesions, taking as reference the baseline sum LD. See the protocol Link module for the full criteria if desired.

Recruitment status

COMPLETED

Study phase

PHASE2

Target enrollment

9 participants

Primary outcome timeframe

12 weeks

Results posted on

2012-07-27

Participant Flow

The accrual ceiling for this study is 25 patients. With an expected accrual of 10-12 patients per year, we expect to complete the accrual within 2-3 years.

Participant milestones

Participant milestones
Measure
VHL Associated Renal Tumors
17-AAG intravenous infusions at a dose of 300 mg/m2 into a vein once a week for 3 weeks out of every 4, for 3 months; on days 1, 8, and 15 of 28 cycles. The infusions last up to 1 to 2 hours.
Overall Study
STARTED
9
Overall Study
COMPLETED
7
Overall Study
NOT COMPLETED
2

Reasons for withdrawal

Reasons for withdrawal
Measure
VHL Associated Renal Tumors
17-AAG intravenous infusions at a dose of 300 mg/m2 into a vein once a week for 3 weeks out of every 4, for 3 months; on days 1, 8, and 15 of 28 cycles. The infusions last up to 1 to 2 hours.
Overall Study
patient did not receive any 17AAG
1
Overall Study
patient received <1 cycle only of 17AAG
1

Baseline Characteristics

17AAG to Treat Kidney Tumors in Von Hippel-Lindau Disease

Baseline characteristics by cohort

Baseline characteristics by cohort
Measure
VHL Associated Renal Tumors
n=9 Participants
17-AAG intravenous infusions at a dose of 300 mg/m2 into a vein once a week for 3 weeks out of every 4, for 3 months; on days 1, 8, and 15 of 28 cycles. The infusions last up to 1 to 2 hours.
Age, Categorical
<=18 years
0 Participants
n=93 Participants
Age, Categorical
Between 18 and 65 years
8 Participants
n=93 Participants
Age, Categorical
>=65 years
1 Participants
n=93 Participants
Age Continuous
48.32 years
STANDARD_DEVIATION 10.82 • n=93 Participants
Sex: Female, Male
Female
3 Participants
n=93 Participants
Sex: Female, Male
Male
6 Participants
n=93 Participants
Region of Enrollment
United States
9 participants
n=93 Participants

PRIMARY outcome

Timeframe: 12 weeks

Population: 8 patients were evaluable (received at least one dose of drug and had a follow up scan).

Response is defined as the number of patients who experience a disease response (complete response (CR) or partial response (PR) of renal tumors)per RECIST criteria. CR is the disappearance of all target lesions. PR is at least a 20% decrease in the sum of the longest diameter (LD) of target lesions, taking as reference the baseline sum LD. See the protocol Link module for the full criteria if desired.

Outcome measures

Outcome measures
Measure
Participants With VHL Associated Renal Tumors
n=8 Participants
Number of Participants With a Renal Tumor Response
0 participants

SECONDARY outcome

Timeframe: Baseline and 12 weeks

Population: There were only two patients with measurable nonrenal tumors and hence the number of participants analyzed is correct.

Number of patients who have a PR or CR of non-renal lesions (pancreatic tumors, pheochromocytomas, and hemangioblastomas). The effect of treatment on the lesions will be evaluated at baseline and at the time of restaging (12 weeks) per RECIST criteria. RECIST is defined as changes in only the largest diameter (unidimensional measurement) of the tumor lesions. Lesions are either measurable or non-measurable using the criteria. See the protocol Link module for the full criteria if desired.

Outcome measures

Outcome measures
Measure
Participants With VHL Associated Renal Tumors
n=2 Participants
Number of Participants With a Non-renal Tumor Response
0 participants

SECONDARY outcome

Timeframe: 1 yr, 364 days

Here are the total number of participants with adverse events. For the detailed list of adverse events see the adverse event module. The descriptions and grading scales found in the revised NCI Common Terminology Criteria for Adverse Events (CTCAE) version 3.0 will be utilized for adverse event reporting. For a detailed description see the link in the Protocol Link module.

Outcome measures

Outcome measures
Measure
Participants With VHL Associated Renal Tumors
n=9 Participants
The Number of Participants With Adverse Events
9 participants

SECONDARY outcome

Timeframe: Baseline and 12 weeks

Population: This analysis was not performed as it was felt that there were not a sufficient number of samples to enable a meaningful analysis.

Measurement of HIF, HSP90 and HSP70 levels by Western Blot in tumor tissue and/or lymphocytes to assess modulation of these biomarkers in response to 17 AAG treatment. Pretreatment tumor samples (when available) and resected tumors (in those patients who did not have a response and underwent surgical resection of their tumor) were to be used for this analysis. Levels of Hsp90, Hsp70, HIF and HIF transcriptional targets in resected tumor will be compared to respective levels in tumors previously resected from other VHL patients (not treated with 17AAG).

Outcome measures

Outcome data not reported

SECONDARY outcome

Timeframe: Baseline and at 12 weeks

Population: Response was not the endpoint. The SUV values were in the 2-3 range and hence renal tumors could not be clearly identified by this technique in any of the patients.

Images were acquired after the intravenous administration of 18FDG and H2015 and used to analyze glucose uptake and estimate blood flow. The parameter to be measured is SUV (standard uptake value(s)) and/or mL/min/gm.

Outcome measures

Outcome measures
Measure
Participants With VHL Associated Renal Tumors
n=5 Participants
Number of Patients in Whom Renal Tumors Could be Identified by Positron Emission Tomography (PET)Based on Fludeoxyglucose 18F (18FDG) Uptake
0 participants

SECONDARY outcome

Timeframe: Baseline and during therapy (12 weeks)

Population: It is not the magnitude of changes in Ktrans, Kep, and Ve that limit our abililty, but the fact that this data was available in only a small number of patients.

Dynamic images will be acquired before and after the intravenous administration of 0.1 mmol/kg of Gadolinium Diethylene triamine pentaacetic acid (DTPA). Time activity curves will be generated over a period of ten minutes. The parameter to be measured is the forward contrast transfer rate (Ktrans), the reverse contrast transfer rate (Kep), and/or the extravascular extracellular space volume fraction (Ve). Flow dynamics are a measure of blood flow changes in the tumor and are determined using the parameters we had previously defined (Ktrans, Kep, etc.).

Outcome measures

Outcome measures
Measure
Participants With VHL Associated Renal Tumors
n=4 Participants
Number of Participants With Flow Dynamics Measured by DCE MRI Within the Renal and Non-renal Tumor
3 participants with changes

Adverse Events

Participants With VHL Associated Renal Tumors

Serious events: 1 serious events
Other events: 8 other events
Deaths: 0 deaths

Serious adverse events

Serious adverse events
Measure
Participants With VHL Associated Renal Tumors
n=9 participants at risk
Nervous system disorders
Dizziness
11.1%
1/9 • Number of events 1 • 2 years, 364 days

Other adverse events

Other adverse events
Measure
Participants With VHL Associated Renal Tumors
n=9 participants at risk
Respiratory, thoracic and mediastinal disorders
ALLERGY/IMMUNOLOGY:: Allergic rhinitis (including sneezing, nasal stuffiness, postnasal drip)
33.3%
3/9 • Number of events 3 • 2 years, 364 days
Investigations
BLOOD/BONE MARROW:: Hemoglobin
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Investigations
BLOOD/BONE MARROW:: Leukocytes (total WBC)
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Investigations
BLOOD/BONE MARROW:: Lymphopenia
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Cardiac disorders
CARDIAC ARRHYTHMIA:: Conduction abnormality/atrioventricular heart block:: AV Block-First degree
11.1%
1/9 • Number of events 5 • 2 years, 364 days
Cardiac disorders
CARDIAC ARRHYTHMIA:: Conduction abnormality/atrioventricular heart block:: AV Block-Second degree Mo
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Congenital, familial and genetic disorders
CARDIAC ARRHYTHMIA:: Palpitations
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Cardiac disorders
CARDIAC ARRHYTHMIA:: Supraventricular and nodal arrhythmia:: Sinus bradycardia
33.3%
3/9 • Number of events 14 • 2 years, 364 days
Cardiac disorders
CARDIAC ARRHYTHMIA:: Supraventricular and nodal arrhythmia:: Sinus tachycardia
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Cardiac disorders
CARDIAC ARRHYTHMIA:: Ventricular arrhythmia:: Ventricular tachycardia
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Cardiac disorders
CARDIAC GENERAL:: Left ventricular diastolic dysfunction
11.1%
1/9 • Number of events 1 • 2 years, 364 days
General disorders
CONSTITUTIONAL SYMPTOMS:: Fatigue (asthenia, lethargy, malaise)
55.6%
5/9 • Number of events 14 • 2 years, 364 days
General disorders
CONSTITUTIONAL SYMPTOMS:: Insomnia
22.2%
2/9 • Number of events 2 • 2 years, 364 days
General disorders
CONSTITUTIONAL SYMPTOMS:: Odor (patient odor)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
General disorders
CONSTITUTIONAL SYMPTOMS:: Weight gain
11.1%
1/9 • Number of events 1 • 2 years, 364 days
General disorders
CONSTITUTIONAL SYMPTOMS:: Weight loss
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Skin and subcutaneous tissue disorders
DERMATOLOGY/SKIN:: Rash/desquamation
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Skin and subcutaneous tissue disorders
DERMATOLOGY/SKIN:: Rash: acne/acneiform
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Anorexia
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Constipation
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Diarrhea
22.2%
2/9 • Number of events 5 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Dysphagia (difficulty swallowing)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Heartburn/dyspepsia
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Nausea
77.8%
7/9 • Number of events 25 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Salivary gland changes/saliva
11.1%
1/9 • Number of events 7 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Taste alteration (dysgeusia)
55.6%
5/9 • Number of events 16 • 2 years, 364 days
Gastrointestinal disorders
GASTROINTESTINAL:: Vomiting
22.2%
2/9 • Number of events 2 • 2 years, 364 days
Blood and lymphatic system disorders
HEMORRHAGE/BLEEDING:: Hemorrhage, GI:: Oral cavity
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Blood and lymphatic system disorders
HEMORRHAGE/BLEEDING:: Hemorrhage, pulmonary/upper respiratory:: Nose
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: ALT, SGPT (serum glutamic pyruvic transaminase)
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: AST, SGOT(serum glutamic oxaloacetic transaminase)
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Albumin, serum-low (hypoalbuminemia)
33.3%
3/9 • Number of events 4 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Bilirubin (hyperbilirubinemia)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: CPK (creatine phosphokinase)
22.2%
2/9 • Number of events 2 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Calcium, serum-high (hypercalcemia)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Calcium, serum-low (hypocalcemia)
22.2%
2/9 • Number of events 3 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Glucose, serum-high (hyperglycemia)
44.4%
4/9 • Number of events 7 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Glucose, serum-low (hypoglycemia)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Magnesium, serum-high (hypermagnesemia)
22.2%
2/9 • Number of events 5 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Metabolic/Laboratory - Other (Specify, __)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Phosphate, serum-low (hypophosphatemia)
22.2%
2/9 • Number of events 2 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Potassium, serum-high (hyperkalemia)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Potassium, serum-low (hypokalemia)
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Sodium, serum-low (hyponatremia)
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Metabolism and nutrition disorders
METABOLIC/LABORATORY:: Uric acid, serum-high (hyperuricemia)
33.3%
3/9 • Number of events 4 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
MUSCULOSKELETAL/SOFT TISSUE:: Extremity-upper (function)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Nervous system disorders
NEUROLOGY:: Ataxia (incoordination)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Nervous system disorders
NEUROLOGY:: Cognitive disturbance
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Nervous system disorders
NEUROLOGY:: Dizziness
55.6%
5/9 • Number of events 5 • 2 years, 364 days
Nervous system disorders
NEUROLOGY:: Neurology - Other (Specify, __)
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Abdomen NOS
22.2%
2/9 • Number of events 8 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Back
11.1%
1/9 • Number of events 5 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Bone
11.1%
1/9 • Number of events 21 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Chest wall
11.1%
1/9 • Number of events 2 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Extremity-limb
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Nervous system disorders
PAIN:: Pain:: Head/headache
55.6%
5/9 • Number of events 8 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Muscle
33.3%
3/9 • Number of events 4 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Neck
11.1%
1/9 • Number of events 5 • 2 years, 364 days
Nervous system disorders
PAIN:: Pain:: Pain NOS
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Musculoskeletal and connective tissue disorders
PAIN:: Pain:: Pelvis
11.1%
1/9 • Number of events 4 • 2 years, 364 days
Respiratory, thoracic and mediastinal disorders
PULMONARY/UPPER RESPIRATORY:: Cough
33.3%
3/9 • Number of events 4 • 2 years, 364 days
Respiratory, thoracic and mediastinal disorders
PULMONARY/UPPER RESPIRATORY:: Fistula, pulmonary/upper respiratory:: Lung
11.1%
1/9 • Number of events 1 • 2 years, 364 days
Respiratory, thoracic and mediastinal disorders
PULMONARY/UPPER RESPIRATORY:: Pulmonary/Upper Respiratory - Other (Specify, __)
11.1%
1/9 • Number of events 1 • 2 years, 364 days

Additional Information

William M. Linehan, M.D.

National Cancer Institute, National Institutes of Health

Phone: 301-496-6353

Results disclosure agreements

  • Principal investigator is a sponsor employee
  • Publication restrictions are in place